Specific code 2014 ICD-9-CM Diagnosis Code 746.89
Other specified congenital anomalies of heart
  • Billable Code
  • Short description: Cong heart anomaly NEC.
  • ICD-9-CM 746.89 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 746.89 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Abnormal atrioventricular connection
  • Abnormal atrioventricular connection - biventricular
  • Abnormal atrioventricular connection - univentricular
  • Abnormal number of leaflets
  • Abnormal position of cardiac valve
  • Abnormality of atrioventricular valve
  • Abnormality of common atrioventricular valve papillary muscle
  • Aborted systole
  • Absent atrioventricular connection with straddling valve
  • Absent left sided atrioventricular connection
  • Absent right atrioventricular valve leaflets
  • Accessory tissue on aortic valve cusp
  • Accessory tissue on common atrioventricular valve leaflet
  • Accessory tissue on left atrioventricular valve leaflet
  • Accessory tissue on mitral leaflet
  • Accessory tissue on right atrioventricular valve leaflet
  • Accessory tissue on tricuspid leaflet
  • Accessory tissue on truncal valve cusp
  • Anomalous muscle bands of left ventricle
  • Anomalous muscle bands of right ventricle
  • Anomalous valve of coronary sinus
  • Anterior leaflet of mitral valve attached to septum
  • Aortic orifice anterior left with respect to pulmonary orifice
  • Aortic orifice anterior right with respect to pulmonary orifice
  • Aortic orifice anterior with respect to pulmonary orifice
  • Aortic orifice left side by side with respect to pulmonary orifice
  • Aortic orifice posterior left with respect to pulmonary orifice
  • Aortic orifice posterior with respect to pulmonary orifice
  • Aortic valve atresia, congenital
  • Aortic valve dysplasia
  • Aortic valve ring hypoplasia
  • Arrhythmogenic right ventricular dysplasia
  • Arrhythmogenic right ventricular dysplasia, congenital
  • Atresia of common atrioventricular valve
  • Atrioventricular septal defect - ventricular component under inferior bridging leaflet
  • Atrioventricular septal defect - ventricular component under superior bridging leaflet
  • Atrioventricular septal defect with ventricular imbalance consisting of dominant left ventricle and hypoplastic right ventricle
  • Bifid apex of heart
  • Bilateral atria
  • Bilateral isomeric atria
  • Brugada syndrome
  • Cardiomegaly, congenital
  • Cardiomegaly, congenital (enlarged heart, at birth)
  • Chiari's network
  • Cleft leaflet of mitral valve
  • Cleft leaflet of tricuspid valve
  • Commissural fusion of aortic cusp
  • Commissural fusion of aortic valve
  • Common atrioventricular valve stenosis
  • Complex congenital heart defect
  • Congenital (at birth) cleft leaflet of mitral valve
  • Congenital abnormality of atrioventricular valves in atrioventricular septal defect
  • Congenital absence of aortic valve
  • Congenital absence of chordae tendineae
  • Congenital absence of coronary sinus
  • Congenital aneurysm of heart
  • Congenital anomaly of aortic valve
  • Congenital anomaly of heart valve
  • Congenital anomaly of pericardium
  • Congenital arrhythmogenic right ventricular dysplasia
  • Congenital atresia of aortic valve
  • Congenital atresia of cardiac valve
  • Congenital atresia of cardiac vein
  • Congenital atresia of mitral valve
  • Congenital cardiomegaly
  • Congenital cleft of cardiac valve
  • Congenital conduction defect
  • Congenital dilatation of atrium
  • Congenital dilatation of cardiac ventricle
  • Congenital disease and abnormality of heart, thoracic aorta and pericardium
  • Congenital diverticulum of left ventricle
  • Congenital enlargement of coronary sinus
  • Congenital epicardial cyst
  • Congenital heart defect, complex
  • Congenital His bundle tachycardia
  • Congenital hypertrophy of cardiac ventricle
  • Congenital hypoplasia of aortic valve
  • Congenital hypoplasia of cardiac vein
  • Congenital hypoplasia of cardiac ventricle
  • Congenital hypoplasia of heart
  • Congenital hypoplasia of mitral valve
  • Congenital insufficiency of tricuspid valve
  • Congenital left ventricular aneurysm
  • Congenital pericardial defect
  • Congenital right ventricular aneurysm
  • Congenital right ventricular diverticulum
  • Congenital stenosis of cardiac valve
  • Congenital tricuspid valve regurgitation
  • Congenital tricuspid valve regurgitation (at birth)
  • Congenital valvular insufficiency
  • Coronary sinus abnormality
  • Coronary sinus defect in left atrium
  • Criss-cross heart
  • Defect, heart, complex congenital (at birth)
  • Diffuse hypoplasia of left ventricle
  • Dilatation of common atrioventricular valve annulus
  • Dilatation of left atrioventricular valve annulus
  • Dilatation of mitral annulus
  • Dilatation of right atrioventricular valve annulus
  • Dilatation of tricuspid annulus
  • Discordant atrioventricular connection
  • Discordant ventriculoarterial connection
  • Diverticulum of left ventricle, congenital (at birth)
  • Divided left atrium
  • Divided right atrium
  • Double aortic valve
  • Double inlet left ventricle
  • Double inlet right ventricle
  • Double inlet to ventricle of indeterminate morphology
  • Double inlet ventricle
  • Double mitral valve
  • Double orifice of common atrioventricular valve
  • Double orifice of left atrioventricular valve
  • Double orifice of mitral valve
  • Double orifice of right atrioventricular valve
  • Double orifice of tricuspid valve
  • Double outlet from ventricle of indeterminate morphology
  • Ebstein-like downward displacement of mitral valve
  • Ebstein-like malformation of the mitral valve
  • Eccentric opening of aortic valve
  • Hemicardia
  • Heterotaxy syndrome, heart, congenital
  • Heterotaxy syndrome, heart, congenital (at birth)
  • Holt Oram syndrome
  • Holt-Oram syndrome
  • Hypoplasia of aortic valve cusp
  • Hypoplasia of cardiac vein
  • Hypoplasia of cardiac vein, congenital
  • Hypoplasia of left ventricular outflow tract
  • Hypoplasia of left ventricular outflow tract and trabecular area
  • Hypoplasia of right heart
  • Hypoplastic (abnormally small) right heart syndrome
  • Hypoplastic common atrioventricular valve papillary muscle
  • Hypoplastic mitral papillary muscle
  • Hypoplastic right atrioventricular valve papillary muscle
  • Hypoplastic right heart syndrome
  • Hypoplastic tricuspid papillary muscle
  • Imperforate common atrioventricular valve
  • Imperforate left atrioventricular valve
  • Imperforate right atrioventricular valve
  • Insufficiency of tricuspid valve congenital (at birth)
  • Leakage of conduit from right atrium to pulmonary artery
  • Left atrial appendage - right - juxtaposition
  • Left atrial appendage aneurysm
  • Left atrial dilatation
  • Left atrial hypoplasia
  • Left atrioventricular valve atresia
  • Left atrioventricular valve dysplasia
  • Left atrioventricular valve hypoplasia
  • Left atrioventricular valve leaflet abnormality
  • Left atrioventricular valve leaflet dysplasia
  • Left atrioventricular valve prolapse
  • Left atrioventricular valve stenosis
  • Left ventricle diverticulum, congenital
  • Left ventricular diverticulum
  • Left ventricular hypoplasia
  • Left ventricular outflow tract abnormality
  • Left ventricular outflow tract atresia
  • Left ventricular outflow tract obstruction
  • Levoatrial cardinal vein
  • Mitral valve atresia, congenital
  • Mitral valve atresia, congenital (present at birth)
  • Mitral valve cleft leaflet, congenital
  • Mitral valve dysplasia
  • Monocuspid cardiac valve
  • Myxomatosis of cardiac valve
  • Overriding left atrioventricular valve
  • Overriding mitral valve
  • Overriding right atrioventricular valve
  • Overriding tricuspid valve
  • Partial agenesis of pericardium
  • Pericardial anomaly
  • Pericardial cyst, congenital
  • Pericardial defect
  • Pericardial diverticulum
  • Pleuropericardial cyst
  • Prolapse of Eustachian valve
  • Quadricuspid aortic valve
  • Quadricuspid cardiac valve
  • Quadricuspid pulmonary valve
  • Regurgitation of common atrioventricular valve
  • Right atrial appendage aneurysm
  • Right atrial endocardial fibroelastosis
  • Right atrioventricular valve atresia
  • Right atrioventricular valve chordae too long
  • Right atrioventricular valve chordae too short
  • Right atrioventricular valve leaflets absent in double inlet ventricle
  • Right hypoplastic heart syndrome
  • Right to left cardiac shunt
  • Right ventricular diverticulum
  • Right ventricular outflow obstruction - localized
  • Rudimentary left ventricle
  • Septoparietal trabeculations
  • Situs ambiguus
  • Solitary aortic trunk with pulmonary atresia
  • Solitary pulmonary trunk with aortic atresia
  • Straddling left atrioventricular valve
  • Straddling mitral valve
  • Straddling right atrioventricular valve
  • Straddling tricuspid valve
  • Totally absent pericardium
  • Tricuspid annulus hypoplasia
  • Tricuspid valve regurgitation, congenital
  • Unicuspid aortic valve
Applies To
  • Atresia of cardiac vein
  • Hypoplasia of cardiac vein
  • Congenital:
    • cardiomegaly
    • diverticulum, left ventricle
    • pericardial defect
Convert to ICD-10-CM: 746.89 converts approximately to:
  • 2014 ICD-10-CM Q23.8 Other congenital malformations of aortic and mitral valves
    Or:
  • 2014 ICD-10-CM Q24.8 Other specified congenital malformations of heart
ICD-9-CM Volume 2 Index entries containing back-references to 746.89:
  • Absence (organ or part) (complete or partial)
    • aortic valve (congenital) 746.89
    • pericardium (congenital) 746.89
  • Accessory (congenital)
    • cusp(s), heart valve NEC 746.89
    • heart 746.89
      • valve NEC 746.89
    • leaflet, heart valve NEC 746.89
    • valve, heart NEC 746.89
  • Agenesis - see also Absence, by site, congenital
    • heart 746.89
      • valve NEC 746.89
        • aortic 746.89
        • mitral 746.89
        • pulmonary 746.01
    • pericardium 746.89
  • Aneurysm (anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (ruptured) (saccular) (varicose) 442.9
    • heart (chronic or with a stated duration of over 8 weeks) (infectional) (wall) 414.10
      • acute or with a stated duration of 8 weeks or less (see also Infarct, myocardium) 410.9
      • congenital 746.89
      • valve - see Endocarditis
  • Anomaly, anomalous (congenital) (unspecified type) 759.9
    • coronary
    • mitral (leaflets) (valve) 746.9
      • atresia 746.89
      • insufficiency 746.6
      • specified type NEC 746.89
      • stenosis 746.5
    • pericardium 746.89
    • tricuspid (leaflet) (valve) 746.9
    • valve (heart) NEC 746.9
      • formation, ureter 753.29
      • pulmonary 746.00
      • specified type NEC 746.89
  • Aplasia - see also Agenesis
    • aortic valve (congenital) 746.89
  • Atresia, atretic (congenital) 759.89
    • aortic (orifice) (valve) 746.89
    • cardiac
      • valve 746.89
        • aortic 746.89
        • mitral 746.89
        • pulmonary 746.01
        • tricuspid 746.1
    • heart
      • valve NEC 746.89
        • aortic 746.89
        • mitral 746.89
        • pulmonary 746.01
        • tricuspid 746.1
    • mitral valve 746.89
      • with atresia or hypoplasia of aortic orifice or valve, with hypoplasia of ascending aorta and defective development of left ventricle 746.7
  • Bifid (congenital) - see also Imperfect, closure
    • apex, heart 746.89
  • Brugada syndrome 746.89
  • Cardiomegaly (see also Hypertrophy, cardiac) 429.3
    • congenital 746.89
  • Chiari's
    • network 746.89
  • Cyst (mucus) (retention) (serous) (simple)
    • celomic (pericardium) 746.89
    • pericardial (congenital) 746.89
      • acquired (secondary) 423.8
    • spring water (pericardium) 746.89
  • Defect, defective 759.9
    • pericardium 746.89
  • Deformity 738.9
    • heart (congenital) 746.9
      • auricle (congenital) 746.9
      • septum 745.9
      • valve (congenital) NEC 746.9
        • acquired - see Endocarditis
        • pulmonary (congenital) 746.00
        • specified type NEC 746.89
      • ventricle (congenital) 746.9
    • mitral (leaflets) (valve) (congenital) 746.9
      • acquired - see Endocarditis, mitral
      • Ebstein's 746.89
      • parachute 746.5
      • specified type NEC 746.89
      • stenosis, congenital 746.5
    • tricuspid (leaflets) (valve) (congenital) 746.9
      • acquired - see Endocarditis, tricuspid
      • atresia or stenosis 746.1
      • specified type NEC 746.89
    • valve, valvular (heart) (congenital) 746.9
      • acquired - see Endocarditis
      • pulmonary 746.00
      • specified type NEC 746.89
  • Degeneration, degenerative
    • myocardium, myocardial (brown) (calcareous) (fatty) (fibrous) (hyaline) (mural) (muscular) (pigmentary) (senile) (with arteriosclerosis) 429.1
      • with rheumatic fever (conditions classifiable to 390) 398.0
        • active, acute, or subacute 391.2
        • inactive or quiescent (with chorea) 398.0
      • amyloid 277.39[425.7]
      • congenital 746.89
      • fetus or newborn 779.89
      • gouty 274.82
      • hypertensive (see also Hypertension, heart) 402.90
      • ischemic 414.8
      • rheumatic (see also Degeneration, myocardium, with rheumatic fever) 398.0
      • syphilitic 093.82
  • Dilatation
    • cardiac (acute) (chronic) (see also Hypertrophy, cardiac) 429.3
      • congenital 746.89
        • valve NEC 746.89
      • hypertensive (see also Hypertension, heart) 402.90
    • heart (acute) (chronic) (see also Hypertrophy, cardiac) 429.3
      • congenital 746.89
      • hypertensive (see also Hypertension, heart) 402.90
      • valve - see also Endocarditis
        • congenital 746.89
  • Disease, diseased - see also Syndrome
    • heart (organic) 429.9
      • with
        • acute pulmonary edema (see also Failure, ventricular, left) 428.1
          • hypertensive 402.91
          • kidney disease - see Hypertension, cardiorenal
          • rheumatic fever (conditions classifiable to 390)
      • amyloid 277.39[425.7]
      • aortic (valve) (see also Endocarditis, aortic) 424.1
      • arteriosclerotic or sclerotic (minimal) (senile) - see Arteriosclerosis, coronary
      • artery, arterial - see Arteriosclerosis, coronary
      • atherosclerotic - see Arteriosclerosis, coronary
      • beer drinkers' 425.5
      • beriberi 265.0 [425.7]
      • black 416.0
      • congenital NEC 746.9
        • cyanotic 746.9
        • maternal, affecting fetus or newborn 760.3
        • specified type NEC 746.89
      • congestive (see also Failure, heart) 428.0
      • coronary 414.9
      • cryptogenic 429.9
      • due to
      • fetal 746.9
        • inflammatory 746.89
      • fibroid (see also Myocarditis) 429.0
      • functional 427.9
      • glycogen storage 271.0 [425.7]
      • gonococcal NEC 098.85
      • gouty 274.82
      • hypertensive (see also Hypertension, heart) 402.90
      • hyperthyroid (see also Hyperthyroidism) 242.9 [425.7]
      • incompletely diagnosed - see Disease, heart
      • ischemic (chronic) (see also Ischemia, heart) 414.9
        • acute (see also Infarct, myocardium) 410.9
          • without myocardial infarction 411.89
            • with coronary (artery) occlusion 411.81
        • asymptomatic 412
        • diagnosed on ECG or other special investigation but currently presenting no symptoms 412
      • kyphoscoliotic 416.1
      • mitral (see also Endocarditis, mitral) 394.9
      • muscular (see also Degeneration, myocardial) 429.1
      • postpartum 674.8
      • psychogenic (functional) 306.2
      • pulmonary (chronic) 416.9
      • rheumatic (chronic) (inactive) (old) (quiescent) (with chorea) 398.90
        • active or acute 391.9
          • with chorea (active) (rheumatic) (Sydenham's) 392.0
          • specified type NEC 391.8
        • maternal, affecting fetus or newborn 760.3
      • rheumatoid - see Arthritis, rheumatoid
      • sclerotic - see Arteriosclerosis, coronary
      • senile (see also Myocarditis) 429.0
      • specified type NEC 429.89
      • syphilitic 093.89
      • thyroid (gland) (see also Hyperthyroidism) 242.9 [425.7]
      • thyrotoxic (see also Thyrotoxicosis) 242.9 [425.7]
      • tuberculous (see also Tuberculosis) 017.9 [425.8]
      • valve, valvular (obstructive) (regurgitant) - see also Endocarditis
        • congenital NEC (see also Anomaly, heart, valve) 746.9
          • pulmonary 746.00
          • specified type NEC 746.89
      • vascular - see Disease, cardiovascular
    • valve, valvular - see also Endocarditis
      • congenital NEC (see also Anomaly, heart, valve) 746.9
        • pulmonary 746.00
        • specified type NEC 746.89
  • Displacement, displaced
    • ventricular septum 746.89
      • with rudimentary ventricle 746.89
  • Distortion (congenital)
    • heart (auricle) (ventricle) 746.89
      • valve (cusp) 746.89
  • Diverticula, diverticulosis, diverticulum (acute) (multiple) (perforated) (ruptured) 562.10
    • heart (congenital) 746.89
    • pericardium (congenital) (cyst) 746.89
    • ventricle, left (congenital) 746.89
  • Double
    • orifice
      • heart valve NEC 746.89
  • Endocarditis (chronic) (indeterminate) (interstitial) (marantic) (nonbacterial thrombotic) (residual) (sclerotic) (sclerous) (senile) (valvular) 424.90
    • aortic (heart) (nonrheumatic) (valve) 424.1
      • with
        • mitral (valve) disease 396.9
          • active or acute 391.1
            • with chorea (acute) (rheumatic) (Sydenham's) 392.0
            • bacterial 421.0
        • rheumatic fever (conditions classifiable to 390)
          • active - see Endocarditis, acute, rheumatic
          • inactive or quiescent (with chorea) 395.9
            • with mitral disease 396.9
      • acute or subacute 421.9
      • arteriosclerotic 424.1
      • congenital 746.89
      • hypertensive 424.1
      • rheumatic (chronic) (inactive) 395.9
        • with mitral (valve) disease 396.9
          • active or acute 391.1
            • with chorea (acute) (rheumatic) (Sydenham's) 392.0
        • active or acute 391.1
          • with chorea (acute) (rheumatic) (Sydenham's) 392.0
      • specified cause, except rheumatic 424.1
      • syphilitic 093.22
    • mitral (chronic) (double) (fibroid) (heart) (inactive) (valve) (with chorea) 394.9
      • with
        • aortic (valve) disease 396.9
          • active or acute 391.1
            • with chorea (acute) (rheumatic) (Sydenham's) 392.0
        • rheumatic fever (conditions classifiable to 390)
          • active - see Endocarditis, acute, rheumatic
          • inactive or quiescent (with chorea) 394.9
            • with aortic valve disease 396.9
      • active or acute 391.1
        • with chorea (acute) (rheumatic) (Sydenham's) 392.0
        • bacterial 421.0
      • arteriosclerotic 424.0
      • congenital 746.89
      • hypertensive 424.0
      • nonrheumatic 424.0
      • syphilitic 093.21
    • tricuspid (chronic) (heart) (inactive) (rheumatic) (valve) (with chorea) 397.0
      • with
        • rheumatic fever (conditions classifiable to 390)
          • active - see Endocarditis, acute, rheumatic
          • inactive or quiescent (with chorea) 397.0
      • active or acute 391.1
        • with chorea (acute) (rheumatic) (Sydenham's) 392.0
      • arteriosclerotic 424.2
      • congenital 746.89
      • hypertensive 424.2
      • nonrheumatic 424.2
      • specified cause, except rheumatic 424.2
      • syphilitic 093.23
  • Fenestration, fenestrated - see also Imperfect, closure
    • cusps, heart valve NEC 746.89
  • Folds, anomalous - see also Anomaly, specified type NEC
    • heart 746.89
  • Fusion, fused (congenital)
    • cusps, heart valve NEC 746.89
      • mitral 746.5
      • tricuspid 746.89
  • Hemicardia 746.89
  • Hypertrophy, hypertrophic
    • cardiac (chronic) (idiopathic) 429.3
      • with
        • rheumatic fever (conditions classifiable to 390)
      • congenital NEC 746.89
      • fatty (see also Degeneration, myocardial) 429.1
      • hypertensive (see also Hypertension, heart) 402.90
      • rheumatic (with chorea) 398.99
      • valve (see also Endocarditis) 424.90
        • congenital NEC 746.89
    • heart (idiopathic) - see also Hypertrophy, cardiac
      • valve - see also Endocarditis
        • congenital NEC 746.89
    • ventricle, ventricular (heart) (left) (right) - see also Hypertrophy, cardiac
      • congenital 746.89
      • due to hypertension (left) (right) (see also Hypertension, heart) 402.90
      • right with ventricular septal defect, pulmonary stenosis or atresia, and dextraposition of aorta 745.2
  • Hypoplasia, hypoplasis 759.89
    • cardiac 746.89
      • valve - see Hypoplasia, heart, valve
      • vein 746.89
    • heart 746.89
      • left (complex) (syndrome) 746.7
      • valve NEC 746.89
  • Imperfect
    • closure (congenital)