Specific code 2014 ICD-9-CM Diagnosis Code 742.3
Congenital hydrocephalus
  • Billable Code
  • ICD-9-CM 742.3 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 742.3 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Aqueduct of Sylvius anomaly
  • Dandy-Walker syndrome
  • Hydranencephaly
  • Hydrocephalus, congenital
Clinical Information
  • Hydrocephalus that is present at birth.
  • Hydrocephalus, absence of the cerebellar vermis, and posterior fossa cyst continuous with the fourth ventricle are the main characteristics of this syndrome. About 4% of all cases of hydrocephalus are complicated by dws. Associated disorders may include aase-smith syndrome 1, aicardi, coffin-siris, cryptophthalmos, ehlers-danlos, ellis-van creveld, jones syndrome, joubert, ruvalcaba-myhre-smith, walker-warburg, meckel, ritscher-schinzel, and veradi syndromes. Dandy-walker syndrome associated with macrocephaly, facial anomalies, developmental delay, and brain stem dysgenesis inherited as an x-linked recessive trait was reported as a separate syndrome.
742.3 Excludes
Applies To
  • Aqueduct of Sylvius:
    • anomaly
    • obstruction, congenital
    • stenosis
  • Atresia of foramina of Magendie and Luschka
  • Hydrocephalus in newborn
Convert to ICD-10-CM: 742.3 converts approximately to:
  • 2014 ICD-10-CM Q03.0 Malformations of aqueduct of Sylvius
    Or:
  • 2014 ICD-10-CM Q03.1 Atresia of foramina of Magendie and Luschka
    Or:
  • 2014 ICD-10-CM Q03.8 Other congenital hydrocephalus
ICD-9-CM Volume 2 Index entries containing back-references to 742.3:
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 742.3 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.