Specific code 2014 ICD-9-CM Diagnosis Code 425.3
Endocardial fibroelastosis
  • Billable Code
  • Short description: Endocard fibroelastosis.
  • ICD-9-CM 425.3 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 425.3 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Cardiomyopathy restrictive, endocardial fibroelastosis
  • Cardiomyopathy, restrictive, due to endocardial fibroelastosis
  • Endocardial fibroelastosis, congenital
  • Primary endocardial fibroelastosis
  • Primary endocardial fibroelastosis (heart condition)
  • Restrictive cardiomyopathy secondary to endocardial fibroelastosis
Clinical Information
  • A condition characterized by the thickening of endocardium due to proliferation of fibrous and elastic tissue, usually in the left ventricle leading to impaired cardiac function (cardiomyopathy, restrictive). It is most commonly seen in young children and rarely in adults. It is often associated with congenital heart anomalies (heart defects congenital;) infection; or gene mutation. Defects in the tafazzin protein, encoded by taz gene, result in a form of autosomal dominant familial endocardial fibroelastosis.
  • A rare disorder characterized by diffuse thickening of the endocardium. It presents with unexplained heart failure.
  • Condition characterized by hypertrophy of the wall of the left ventricle and conversion of the endocardium into a thick fibroelastic coat, with the capacity of the ventricle sometimes reduced, but often increased.
Applies To
  • Elastomyofibrosis
Convert to ICD-10-CM: 425.3 converts directly to:
  • 2014 ICD-10-CM I42.4 Endocardial fibroelastosis
ICD-9-CM Volume 2 Index entries containing back-references to 425.3:
  • Anomaly, anomalous (congenital) (unspecified type) 759.9
  • Cardiomyopathy (congestive) (constrictive) (familial) (infiltrative) (obstructive) (restrictive) (sporadic) 425.4
    • congenital 425.3
    • newborn 425.4
      • congenital 425.3
  • Elastomyofibrosis 425.3
  • Endocarditis (chronic) (indeterminate) (interstitial) (marantic) (nonbacterial thrombotic) (residual) (sclerotic) (sclerous) (senile) (valvular) 424.90
    • congenital 425.3
    • fetal 425.3
  • Fibroelastosis (cordis) (endocardial) (endomyocardial) 425.3
  • Newborn (infant) (liveborn)
    • cardiomyopathy 425.4
      • congenital 425.3
  • Sclerosis, sclerotic
    • subendocardial, congenital 425.3
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 425.3 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.