Specific code 2014 ICD-9-CM Diagnosis Code 746.5
Congenital mitral stenosis
  • Billable Code
  • Short description: Congen mitral stenosis.
  • ICD-9-CM 746.5 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 746.5 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Congenital stenosis of mitral valve
  • Congenital supravalvular mitral stenosis
  • Mitral valve stenosis, congenital
  • Stenosis (narrowing) of mitral valve, congenital
  • Supravalvular mitral stenosis, congenital
  • Supravalvular stenosis (narrowing) of mitral valve
Applies To
  • Fused commissure of mitral valve
  • Parachute deformity of mitral valve
  • Supernumerary cusps of mitral valve
Convert to ICD-10-CM: 746.5 converts directly to:
  • 2014 ICD-10-CM Q23.2 Congenital mitral stenosis
ICD-9-CM Volume 2 Index entries containing back-references to 746.5:
  • Anomaly, anomalous (congenital) (unspecified type) 759.9
  • Deformity 738.9
    • mitral (leaflets) (valve) (congenital) 746.9
      • acquired - see Endocarditis, mitral
      • Ebstein's 746.89
      • parachute 746.5
      • specified type NEC 746.89
      • stenosis, congenital 746.5
    • parachute, mitral valve 746.5
  • Disease, diseased - see also Syndrome
    • Duroziez's (congenital mitral stenosis) 746.5
  • Duroziez's disease (congenital mitral stenosis) 746.5
  • Fusion, fused (congenital)
    • commissure, mitral valve 746.5
  • Parachute mitral valve 746.5
  • Stenosis (cicatricial) - see also Stricture
    • heart valve (acquired) - see also Endocarditis
    • mitral (valve) (chronic) (inactive) 394.0
      • with
        • aortic (valve)
          • disease (insufficiency) 396.1
          • insufficiency or incompetence 396.1
          • stenosis or obstruction 396.0
        • incompetency, insufficiency or regurgitation 394.2
          • with aortic valve disease 396.8
      • active or acute 391.1
        • with chorea (acute) (rheumatic) (Sydenham's) 392.0
      • congenital 746.5
      • specified cause, except rheumatic 424.0
      • syphilitic 093.21
  • Stricture (see also Stenosis) 799.89
    • heart - see also Disease, heart
    • mitral (valve) (see also Stenosis, mitral) 394.0
      • congenital 746.5
      • specified cause, except rheumatic 424.0
  • Supernumerary (congenital)
    • mitral cusps 746.5
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 746.5 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.