Convert to ICD-10-CM:
759.89 converts approximately to:
- 2015/16 ICD-10-CM E78.71 Barth syndrome
Or:
- 2015/16 ICD-10-CM E78.72 Smith-Lemli-Opitz syndrome
Or:
- 2015/16 ICD-10-CM Q87.2 Congenital malformation syndromes predominantly involving limbs
Or:
- 2015/16 ICD-10-CM Q87.3 Congenital malformation syndromes involving early overgrowth
Or:
- 2015/16 ICD-10-CM Q87.5 Other congenital malformation syndromes with other skeletal changes
Or:
- 2015/16 ICD-10-CM Q87.81 Alport syndrome
Or:
- 2015/16 ICD-10-CM Q87.89 Other specified congenital malformation syndromes, not elsewhere classified
Or:
- 2015/16 ICD-10-CM Q89.8 Other specified congenital malformations
ICD-9-CM Volume 2 Index entries containing back-references to
759.89:
- Abrachiocephalia 759.89
- Abrachiocephalus 759.89
- Absence (organ or part) (complete or partial)
heart (congenital) 759.89![](/images/vertical.gif)
acquired - see Status, organ replacement
organ![](/images/16x16.gif)
of Corti (congenital) 744.05![](/images/note.png)
![](/images/16x16.gif)
or site![](/images/16x16.gif)
![](/images/16x16.gif)
acquired V45.79![](/images/note.png)
![](/images/16x16.gif)
![](/images/16x16.gif)
congenital NEC 759.89
- Acardia 759.89
- Arcadiacus amorphus 759.89
- Acardius 759.89
- Acephalobrachia 759.89
- Acephalocardia 759.89
- Acephalocardius 759.89
- Acephalochiria 759.89
- Acephalochirus 759.89
- Acephalogaster 759.89
- Acephalostomus 759.89
- Acephalothorax 759.89
- Alagille syndrome 759.89
- Alport's syndrome (hereditary hematurianephropathy-deafness) 759.89
- Anomaly, anomalous (congenital) (unspecified type) 759.9
![](/images/note.png)
multiple NEC 759.7![](/images/note.png)
![](/images/vertical.gif)
specified type NEC 759.89
organ![](/images/vertical.gif)
of Corti (causing impairment of hearing) 744.05![](/images/note.png)
![](/images/vertical.gif)
or site 759.9![](/images/note.png)
![](/images/vertical.gif)
![](/images/16x16.gif)
specified type NEC 759.89
specified type NEC![](/images/16x16.gif)
adrenal (gland) 759.1![](/images/note.png)
![](/images/16x16.gif)
alimentary tract (complete) (partial) 751.8![](/images/note.png)
![](/images/16x16.gif)
ankle 755.69![](/images/note.png)
![](/images/16x16.gif)
anus, anal (canal) 751.5![](/images/note.png)
![](/images/16x16.gif)
aorta, aortic 747.29![](/images/note.png)
![](/images/16x16.gif)
appendix 751.5![](/images/note.png)
![](/images/16x16.gif)
arm 755.59![](/images/note.png)
![](/images/16x16.gif)
artery (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60![](/images/note.png)
![](/images/16x16.gif)
auditory canal 744.29![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
causing impairment of hearing 744.02![](/images/note.png)
![](/images/16x16.gif)
bile duct or passage 751.69![](/images/note.png)
![](/images/16x16.gif)
bladder 753.8![](/images/note.png)
![](/images/16x16.gif)
bone(s) 756.9![](/images/note.png)
![](/images/16x16.gif)
brain 742.4![](/images/note.png)
![](/images/16x16.gif)
breast 757.6![](/images/note.png)
![](/images/16x16.gif)
broad ligament 752.19![](/images/note.png)
![](/images/16x16.gif)
bronchus 748.3![](/images/note.png)
![](/images/16x16.gif)
canal of Nuck 752.89![](/images/note.png)
![](/images/16x16.gif)
cardiac septal closure 745.8![](/images/note.png)
![](/images/16x16.gif)
carpus 755.59![](/images/note.png)
![](/images/16x16.gif)
cartilaginous 756.9![](/images/note.png)
![](/images/16x16.gif)
cecum 751.5![](/images/note.png)
![](/images/16x16.gif)
cervix 752.49![](/images/note.png)
![](/images/16x16.gif)
chest (wall) 756.3![](/images/note.png)
![](/images/16x16.gif)
chin 744.89![](/images/note.png)
![](/images/16x16.gif)
ciliary body 743.46![](/images/note.png)
![](/images/16x16.gif)
circulatory system 747.89![](/images/note.png)
![](/images/16x16.gif)
clavicle 755.51![](/images/note.png)
![](/images/16x16.gif)
clitoris 752.49![](/images/note.png)
![](/images/16x16.gif)
coccyx 756.19![](/images/note.png)
![](/images/16x16.gif)
colon 751.5![](/images/note.png)
![](/images/16x16.gif)
common duct 751.69![](/images/note.png)
![](/images/16x16.gif)
connective tissue 756.89![](/images/note.png)
![](/images/16x16.gif)
cricoid cartilage 748.3![](/images/note.png)
![](/images/16x16.gif)
cystic duct 751.69![](/images/note.png)
![](/images/16x16.gif)
diaphragm 756.6![](/images/note.png)
![](/images/16x16.gif)
digestive organ(s) or tract 751.8![](/images/note.png)
![](/images/16x16.gif)
duodenum 751.5![](/images/note.png)
![](/images/16x16.gif)
ear 744.29![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
auricle 744.29![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
![](/images/vertical.gif)
causing impairment of hearing 744.02![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
causing impairment of hearing 744.09![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
inner (causing impairment of hearing) 744.05![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
middle, except ossicles 744.03![](/images/note.png)
![](/images/16x16.gif)
ejaculatory duct 752.89![](/images/note.png)
![](/images/16x16.gif)
endocrine 759.2![](/images/note.png)
![](/images/16x16.gif)
epiglottis 748.3![](/images/note.png)
![](/images/16x16.gif)
esophagus 750.4![](/images/note.png)
![](/images/16x16.gif)
Eustachian tube 744.24![](/images/note.png)
![](/images/16x16.gif)
eye 743.8![](/images/note.png)
![](/images/16x16.gif)
face 744.89![](/images/note.png)
![](/images/16x16.gif)
fallopian tube 752.19![](/images/note.png)
![](/images/16x16.gif)
fascia 756.89![](/images/note.png)
![](/images/16x16.gif)
femur 755.69![](/images/note.png)
![](/images/16x16.gif)
fibula 755.69![](/images/note.png)
![](/images/16x16.gif)
finger 755.59![](/images/note.png)
![](/images/16x16.gif)
foot 755.67![](/images/note.png)
![](/images/16x16.gif)
fovea centralis 743.55![](/images/note.png)
![](/images/16x16.gif)
gallbladder 751.69![](/images/note.png)
![](/images/16x16.gif)
Gartner's duct 752.89![](/images/note.png)
![](/images/16x16.gif)
gastrointestinal tract 751.8![](/images/note.png)
![](/images/16x16.gif)
genitalia, genital organ(s)![](/images/16x16.gif)
genitourinary tract NEC 752.89![](/images/note.png)
![](/images/16x16.gif)
glottis 748.3![](/images/note.png)
![](/images/16x16.gif)
hair 757.4![](/images/note.png)
![](/images/16x16.gif)
hand 755.59![](/images/note.png)
![](/images/16x16.gif)
heart 746.89![](/images/note.png)
![](/images/16x16.gif)
hepatic duct 751.69![](/images/note.png)
![](/images/16x16.gif)
hydatid of Morgagni 752.89![](/images/note.png)
![](/images/16x16.gif)
hymen 752.49![](/images/note.png)
![](/images/16x16.gif)
integument 757.8![](/images/note.png)
![](/images/16x16.gif)
intestine (large) (small) 751.5![](/images/note.png)
![](/images/16x16.gif)
iris 743.46![](/images/note.png)
![](/images/16x16.gif)
jejunum 751.5![](/images/note.png)
![](/images/16x16.gif)
joint 755.8![](/images/note.png)
![](/images/16x16.gif)
kidney 753.3![](/images/note.png)
![](/images/16x16.gif)
knee 755.64![](/images/note.png)
![](/images/16x16.gif)
labium (majus) (minus) 752.49![](/images/note.png)
![](/images/16x16.gif)
labyrinth, membranous 744.05![](/images/note.png)
![](/images/16x16.gif)
larynx 748.3![](/images/note.png)
![](/images/16x16.gif)
leg 755.69![](/images/note.png)
![](/images/16x16.gif)
lens 743.39![](/images/note.png)
![](/images/16x16.gif)
limb, except reduction deformity 755.8![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
lower 755.69![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
![](/images/vertical.gif)
reduction deformity (see also Deformity, reduction, lower limb) 755.30![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
upper 755.59![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
![](/images/16x16.gif)
reduction deformity (see also Deformity, reduction, upper limb) 755.20![](/images/note.png)
![](/images/16x16.gif)
lip 750.26![](/images/note.png)
![](/images/16x16.gif)
liver 751.69![](/images/note.png)
![](/images/16x16.gif)
lung (fissure) (lobe) 748.69![](/images/note.png)
![](/images/16x16.gif)
meatus urinarius 753.8![](/images/note.png)
![](/images/16x16.gif)
metacarpus 755.59![](/images/note.png)
![](/images/16x16.gif)
mouth 750.26![](/images/note.png)
![](/images/16x16.gif)
Müllerian![](/images/16x16.gif)
muscle 756.89![](/images/note.png)
![](/images/16x16.gif)
musculoskeletal system, except limbs 756.9![](/images/note.png)
![](/images/16x16.gif)
nail 757.5![](/images/note.png)
![](/images/16x16.gif)
neck 744.89![](/images/note.png)
![](/images/16x16.gif)
nerve 742.8![](/images/note.png)
![](/images/16x16.gif)
nervous system 742.8![](/images/note.png)
![](/images/16x16.gif)
nipple 757.6![](/images/note.png)
![](/images/16x16.gif)
nose 748.1![](/images/note.png)
![](/images/16x16.gif)
organ NEC 759.89![](/images/16x16.gif)
osseous meatus (ear) 744.03![](/images/note.png)
![](/images/16x16.gif)
ovary 752.0![](/images/note.png)
![](/images/16x16.gif)
oviduct 752.19![](/images/note.png)
![](/images/16x16.gif)
pancreas 751.7![](/images/note.png)
![](/images/16x16.gif)
parathyroid 759.2![](/images/note.png)
![](/images/16x16.gif)
patella 755.64![](/images/note.png)
![](/images/16x16.gif)
pelvic girdle 755.69![](/images/note.png)
![](/images/16x16.gif)
penis 752.69![](/images/note.png)
![](/images/16x16.gif)
pericardium 746.89![](/images/note.png)
![](/images/16x16.gif)
peripheral vascular system NEC (see also Anomaly, peripheral vascular system) 747.60![](/images/note.png)
![](/images/16x16.gif)
pharynx 750.29![](/images/note.png)
![](/images/16x16.gif)
pituitary 759.2![](/images/note.png)
![](/images/16x16.gif)
prostate 752.89![](/images/note.png)
![](/images/16x16.gif)
radius 755.59![](/images/note.png)
![](/images/16x16.gif)
rectum 751.5![](/images/note.png)
![](/images/16x16.gif)
respiratory system 748.8![](/images/note.png)
![](/images/16x16.gif)
rib 756.3![](/images/note.png)
![](/images/16x16.gif)
round ligament 752.89![](/images/note.png)
![](/images/16x16.gif)
sacrum 756.19![](/images/note.png)
![](/images/16x16.gif)
salivary duct or gland 750.26![](/images/note.png)
![](/images/16x16.gif)
scapula 755.59![](/images/note.png)
![](/images/16x16.gif)
sclera 743.47![](/images/note.png)
![](/images/16x16.gif)
scrotum 752.89![](/images/note.png)
![](/images/16x16.gif)
seminal duct or tract 752.89![](/images/note.png)
![](/images/16x16.gif)
shoulder girdle 755.59![](/images/note.png)
![](/images/16x16.gif)
site NEC 759.89![](/images/16x16.gif)
skin 757.39![](/images/note.png)
![](/images/16x16.gif)
skull (bone(s)) 756.0![](/images/note.png)
![](/images/16x16.gif)
specified organ or site NEC 759.89![](/images/16x16.gif)
spermatic cord 752.89![](/images/note.png)
![](/images/16x16.gif)
spinal cord 742.59![](/images/note.png)
![](/images/16x16.gif)
spine 756.19![](/images/note.png)
![](/images/16x16.gif)
spleen 759.0![](/images/note.png)
![](/images/16x16.gif)
sternum 756.3![](/images/note.png)
![](/images/16x16.gif)
stomach 750.7![](/images/note.png)
![](/images/16x16.gif)
tarsus 755.67![](/images/note.png)
![](/images/16x16.gif)
tendon 756.89![](/images/note.png)
![](/images/16x16.gif)
testis 752.89![](/images/note.png)
![](/images/16x16.gif)
thorax (wall) 756.3![](/images/note.png)
![](/images/16x16.gif)
thymus 759.2![](/images/note.png)
![](/images/16x16.gif)
thyroid (gland) 759.2![](/images/note.png)
![](/images/16x16.gif)
tibia 755.69![](/images/note.png)
![](/images/16x16.gif)
toe 755.66![](/images/note.png)
![](/images/16x16.gif)
tongue 750.19![](/images/note.png)
![](/images/16x16.gif)
trachea (cartilage) 748.3![](/images/note.png)
![](/images/16x16.gif)
ulna 755.59![](/images/note.png)
![](/images/16x16.gif)
urachus 753.7![](/images/note.png)
![](/images/16x16.gif)
ureter 753.4![](/images/note.png)
![](/images/16x16.gif)
urethra 753.8![](/images/note.png)
![](/images/16x16.gif)
urinary tract 753.8![](/images/note.png)
![](/images/16x16.gif)
uterus (Müllerian) 752.39![](/images/note.png)
![](/images/16x16.gif)
uvula 750.26![](/images/note.png)
![](/images/16x16.gif)
vagina 752.49![](/images/note.png)
![](/images/16x16.gif)
vascular NEC (see also Anomaly, peripheral vascular system) 747.60![](/images/note.png)
![](/images/16x16.gif)
vas deferens 752.89![](/images/note.png)
![](/images/16x16.gif)
vein(s) (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60![](/images/note.png)
![](/images/16x16.gif)
vena cava (inferior) (superior) 747.49![](/images/note.png)
![](/images/16x16.gif)
vertebra 756.19![](/images/note.png)
![](/images/16x16.gif)
vulva 752.49![](/images/note.png)
- Atresia, atretic (congenital) 759.89
alimentary organ or tract NEC 751.8![](/images/note.png)
ani, anus, anal (canal) 751.2![](/images/note.png)
aorta 747.22![](/images/note.png)
![](/images/vertical.gif)
with hypoplasia of ascending aorta and defective development of left ventricle (with mitral valve atresia) 746.7![](/images/note.png)
![](/images/vertical.gif)
arch 747.11![](/images/note.png)
![](/images/vertical.gif)
ring 747.21![](/images/note.png)
aortic (orifice) (valve) 746.89![](/images/note.png)
aqueduct of Sylvius 742.3![](/images/note.png)
![](/images/vertical.gif)
with spina bifida (see also Spina bifida) 741.0![](/images/note.png)
artery NEC (see also Atresia, blood vessel) 747.60![](/images/note.png)
auditory canal (external) 744.02![](/images/note.png)
bile, biliary duct (common) or passage 751.61![](/images/note.png)
![](/images/vertical.gif)
acquired (see also Obstruction, biliary) 576.2![](/images/note.png)
blood vessel (peripheral) NEC 747.60![](/images/note.png)
cardiac
cervix (acquired) 622.4![](/images/note.png)
![](/images/vertical.gif)
congenital 752.43![](/images/note.png)
![](/images/vertical.gif)
in pregnancy or childbirth 654.6![](/images/note.png)
![](/images/vertical.gif)
![](/images/16x16.gif)
affecting fetus or newborn 763.89![](/images/note.png)
![](/images/vertical.gif)
![](/images/16x16.gif)
causing obstructed labor 660.2![](/images/note.png)
![](/images/vertical.gif)
![](/images/16x16.gif)
![](/images/16x16.gif)
affecting fetus or newborn 763.1![](/images/note.png)
cystic duct 751.61![](/images/note.png)
![](/images/vertical.gif)
acquired 575.8![](/images/note.png)
![](/images/vertical.gif)
![](/images/16x16.gif)
with obstruction (see also Obstruction, gallbladder) 575.2![](/images/note.png)
digestive organs NEC 751.8![](/images/note.png)
fallopian tube (acquired) 628.2![](/images/note.png)
foramen of![](/images/vertical.gif)
Luschka 742.3![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
with spina bifida (see also Spina bifida) 741.0![](/images/note.png)
![](/images/vertical.gif)
Magendie 742.3![](/images/note.png)
![](/images/vertical.gif)
![](/images/16x16.gif)
with spina bifida (see also Spina bifida) 741.0![](/images/note.png)
genital organ
heart
iris, filtration angle (see also Buphthalmia) 743.20![](/images/note.png)
lacrimal, apparatus 743.65![](/images/note.png)
![](/images/vertical.gif)
acquired - see Stenosis, lacrimal
mitral valve 746.89![](/images/note.png)
![](/images/vertical.gif)
with atresia or hypoplasia of aortic orifice or valve, with hypoplasia of ascending aorta and defective development of left ventricle 746.7![](/images/note.png)
nares (anterior) (posterior) 748.0![](/images/note.png)
organ or site NEC - see Anomaly, specified type NEC
submaxillary duct or gland 750.23![](/images/note.png)
vascular NEC (see also Atresia, blood vessel) 747.60![](/images/note.png)
vein NEC (see also Atresia, blood vessel) 747.60![](/images/note.png)
vena cava (inferior) (superior) 747.49![](/images/note.png)
vesicourethral orifice 753.6![](/images/note.png)
- Barth syndrome 759.89
- Beckwith (-Wiedemann) syndrome 759.89
- Biedl-Bardet syndrome 759.89
- Biemond's syndrome (obesity, polydactyly, and intellectual disabilities) 759.89
- Birt-Hogg-Dube syndrome 759.89
- Brachman-de Lange syndrome (Amsterdam dwarf, intellectual disabilities, and brachycephaly) 759.89
- Brachymorphism and ectopia lentis 759.89
- Bruck-de Lange disease or syndrome (Amsterdam dwarf, intellectual disabilities, and brachycephaly) 759.89
- Carpenter's syndrome 759.89
- Cerebrohepatorenal syndrome 759.89
- CGF (congenital generalized fibromatosis) 759.89
- CHARGE association (syndrome) 759.89
- Cockayne's disease or syndrome (microcephaly and dwarfism) 759.89
- Congenital - see also condition
generalized fibromatosis (CGF) 759.89
- Cornelia de Lange's syndrome (Amsterdam dwarf, intellectual disabilities, and brachycephaly) 759.89
- Cyclencephaly 759.89
- Cyclopia, cyclops 759.89
- Cyllosoma 759.89
- Cyst (mucus) (retention) (serous) (simple)
congenital NEC 759.89
umbilicus 759.89
- Deformity 738.9
![](/images/note.png)
multiple, congenital NEC 759.7![](/images/note.png)
![](/images/16x16.gif)
specified type NEC 759.89
- de Lange's syndrome (Amsterdam dwarf, intellectual disabilities, and brachycephaly) 759.89
- Disease, diseased - see also Syndrome
Bruck-de Lange (Amsterdam dwarf, intellectual disabilities, and brachycephaly) 759.89
Cockayne's (microcephaly and dwarfism) 759.89
Kok 759.89
lymphoproliferative (chronic) (M9970/1) 238.79![](/images/note.png)
![](/images/vertical.gif)
X linked 759.89
polycystic (congenital) 759.89
Startle 759.89
- Dwarf, dwarfism 259.4
![](/images/note.png)
Amsterdam 759.89
bird-headed 759.89
Russell's (uterine dwarfism and craniofacial dysostosis) 759.89
- Dyscraniopyophalangy 759.89
- Dysostosis
orodigitofacial 759.89
- Dysplasia - see also Anomaly
craniocarpotarsal 759.89
linguofacialis 759.89
oculodentodigital 759.89
- Ectopic, ectopia (congenital) 759.89
abdominal viscera 751.8![](/images/note.png)
![](/images/vertical.gif)
due to defect in anterior abdominal wall 756.79![](/images/note.png)
bone and cartilage in lung 748.69![](/images/note.png)
gestation - see Pregnancy, ectopic
hormone secretion NEC 259.3![](/images/note.png)
hyperparathyroidism 259.3![](/images/note.png)
kidney (crossed) (intrathoracic) (pelvis) 753.3![](/images/note.png)
![](/images/vertical.gif)
in pregnancy or childbirth 654.4![](/images/note.png)
![](/images/vertical.gif)
![](/images/16x16.gif)
causing obstructed labor 660.2![](/images/note.png)
mole - see Pregnancy, ectopic
organ or site NEC - see Malposition, congenital
pancreas, pancreatic tissue 751.7![](/images/note.png)
pregnancy - see Pregnancy, ectopic
sebaceous glands of mouth 750.26![](/images/note.png)
secretion
- Fibromatosis 728.79
![](/images/note.png)
congenital generalized (CGF) 759.89
- Finnish type nephrosis (congenital) 759.89
- Fistula (sinus) 686.9
![](/images/note.png)
umbilical 759.89
- Fraser's syndrome 759.89
- Freeman-Sheldon syndrome 759.89
- Gillespie's syndrome (dysplasia oculodentodigitalis) 759.89
- Gorlin-Chaudhry-Moss syndrome 759.89
- Hemihypertrophy (congenital) 759.89
- Hyperekplexia 759.89
- Hyperexplexia 759.89
- Hypoplasia, hypoplasis 759.89
angiolymphoid, with eosinophilia (ALHE) 228.01![](/images/note.png)
aortic![](/images/vertical.gif)
arch (tubular) 747.10![](/images/note.png)
![](/images/vertical.gif)
orifice or valve with hypoplasia of ascending aorta and defective development of left ventricle (with mitral valve atresia) 746.7![](/images/note.png)
arm (see also Absence, arm, congenital) 755.20![](/images/note.png)
artery (congenital) (peripheral) 747.60![](/images/note.png)
biliary duct (common) or passage 751.61![](/images/note.png)
cardiac 746.89![](/images/note.png)
![](/images/vertical.gif)
valve - see Hypoplasia, heart, valve![](/images/vertical.gif)
vein 746.89![](/images/note.png)
carpus (see also Absence, carpal, congenital) 755.28![](/images/note.png)
digestive organ(s) or tract NEC 751.8![](/images/note.png)
enamel of teeth (neonatal) (postnatal) (prenatal) 520.4![](/images/note.png)
endocrine (gland) NEC 759.2![](/images/note.png)
erythropoietic, chronic acquired 284.81![](/images/note.png)
eye (see also Microphthalmos) 743.10![](/images/note.png)
femur (see also Absence, femur, congenital) 755.34![](/images/note.png)
fibula (see also Absence, fibula, congenital) 755.37![](/images/note.png)
finger (see also Absence, finger, congenital) 755.29![](/images/note.png)
genitalia, genital organ(s)
humerus (see also Absence, humerus, congenital) 755.24![](/images/note.png)
lacrimal duct (apparatus) 743.65![](/images/note.png)
leg (see also Absence, limb, congenital, lower) 755.30![](/images/note.png)
limb 755.4![](/images/note.png)
![](/images/vertical.gif)
lower (see also Absence, limb, congenital, lower) 755.30![](/images/note.png)
![](/images/vertical.gif)
upper (see also Absence, limb, congenital, upper) 755.20![](/images/note.png)
metacarpus (see also Absence, metacarpal, congenital) 755.28![](/images/note.png)
metatarsus (see also Absence, metatarsal, congenital) 755.38![](/images/note.png)
myocardium (congenital) (Uhl's anomaly) 746.84![](/images/note.png)
ophthalmic (see also Microphthalmos) 743.10![](/images/note.png)
organ![](/images/vertical.gif)
of Corti 744.05![](/images/note.png)
![](/images/vertical.gif)
or site NEC - see Anomaly, by site
parathyroid (gland) 759.2![](/images/note.png)
peripheral vascular system (congenital) NEC 747.60![](/images/note.png)
radioulnar (see also Absence, radius, congenital, with ulna) 755.25![](/images/note.png)
radius (see also Absence, radius, congenital) 755.26![](/images/note.png)
respiratory system NEC 748.9![](/images/note.png)
spinal (cord) (ventral horn cell) 742.59![](/images/note.png)
tarsus (see also Absence, tarsal, congenital) 755.38![](/images/note.png)
thyroid (gland) 243![](/images/note.png)
tibiofibular (see also Absence, tibia, congenital, with fibula) 755.35![](/images/note.png)
toe (see also Absence, toe, congenital) 755.39![](/images/note.png)
trachea (cartilage) (rings) 748.3![](/images/note.png)
ulna (see also Absence, ulna, congenital) 755.27![](/images/note.png)
vascular (peripheral) NEC (see also Hypoplasia, peripheral vascular system) 747.60![](/images/note.png)
vein(s) (peripheral) NEC (see also Hypoplasia, peripheral vascular system) 747.60![](/images/note.png)
vena cava (inferior) (superior) 747.49![](/images/note.png)
- Joubert syndrome 759.89
- Kabuki syndrome 759.89
- Klippel-Trenaunay syndrome 759.89
- Laurence-Moon-Biedl syndrome (obesity, polydactyly, and intellectual disabilities) 759.89
- Marchesani (-Weill) syndrome (brachymorphism and ectopia lentis) 759.89
- Meyer-Schwickerath and Weyers syndrome (dysplasia oculodentodigitalis) 759.89
- Microphthalmos (congenital) 743.10
![](/images/note.png)
syndrome 759.89
- Mieten's syndrome 759.89
- Mohr's syndrome (types I and II) 759.89
- Myofibromatosis
infantile 759.89
- Negri bodies 071
![](/images/note.png)
Neill-Dingwall syndrome (microcephaly and dwarfism) 759.89
- Nephritis, nephritic (albuminuric) (azotemic) (congenital) (degenerative) (diffuse) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic) 583.9
![](/images/note.png)
hereditary (Alport's syndrome) 759.89
- Nephrosis, nephrotic (Epstein's) (syndrome) 581.9
![](/images/note.png)
Finnish type (congenital) 759.89
- Nevus (M8720/0) - see also Neoplasm, skin, benign
flammeus 757.32![](/images/note.png)
![](/images/vertical.gif)
osteohypertrophic 759.89
osteohypertrophic, flammeus 759.89
- Orodigitofacial dysostosis 759.89
- Papillon-Léage and Psaume syndrome (orodigitofacial dysostosis) 759.89
- Persistence, persistent (congenital) 759.89
bulbus cordis in left ventricle 745.8![](/images/note.png)
cilioretinal artery or vein 743.51![](/images/note.png)
communication - see Fistula, congenital
convolutions
ductus
fetal![](/images/vertical.gif)
circulation 747.83![](/images/note.png)
![](/images/vertical.gif)
form of cervix (uteri) 752.49![](/images/note.png)
![](/images/vertical.gif)
hemoglobin (hereditary) ("Swiss variety") 282.7![](/images/note.png)
![](/images/vertical.gif)
pulmonary hypertension 747.83![](/images/note.png)
foramen
hemoglobin, fetal (hereditary) (HPFH) 282.7![](/images/note.png)
hyaloid
hymen (tag)![](/images/vertical.gif)
in pregnancy or childbirth 654.8![](/images/note.png)
![](/images/vertical.gif)
![](/images/16x16.gif)
causing obstructed labor 660.2![](/images/note.png)
left![](/images/vertical.gif)
posterior cardinal vein 747.49![](/images/note.png)
![](/images/vertical.gif)
root with right arch of aorta 747.21![](/images/note.png)
![](/images/vertical.gif)
superior vena cava 747.49![](/images/note.png)
Meckel's diverticulum 751.0![](/images/note.png)
mucosal disease (middle ear) (with posterior or superior marginal perforation of ear drum) 382.2![](/images/note.png)
occiput, anterior or posterior 660.3![](/images/note.png)
omphalomesenteric duct 751.0![](/images/note.png)
organ or site NEC - see Anomaly, specified type NEC
ostium
ovarian rests in fallopian tube 752.19![](/images/note.png)
pancreatic tissue in intestinal tract 751.5![](/images/note.png)
primary (deciduous)
Rhesus (Rh) titer (see also Complications, transfusion) 999.70![](/images/note.png)
sinus![](/images/vertical.gif)
urogenitalis 752.89![](/images/note.png)
![](/images/vertical.gif)
venosus with imperfect incorporation in right auricle 747.49![](/images/note.png)
truncus arteriosus or communis 745.0![](/images/note.png)
tunica vasculosa lentis 743.39![](/images/note.png)
- Podencephalus 759.89
- Polycystic (congenital) (disease) 759.89
degeneration, kidney - see Polycystic, kidney
- Pseudo-Turner's syndrome 759.89
- Rubinstein-Taybi's syndrome (brachydactylia, short stature and intellectual disabilities) 759.89
- Rud's syndrome (mental deficiency, epilepsy, and infantilism) 759.89
- Russell's dwarf (uterine dwarfism and craniofacial dysostosis) 759.89
- Russell (-Silver) syndrome (congenital hemihypertrophy and short stature) 759.89
- Seborrhea, seborrheic 706.3
![](/images/note.png)
nigricans 759.89
- Seckel's syndrome 759.89
- Sick 799.9
![](/images/note.png)
cilia syndrome 759.89
- Silver's syndrome (congenital hemihypertrophy and short stature 759.89
- Sirenomelia 759.89
- Smith-Lemli-Opitz syndrome (cerebrohepatorenal syndrome) 759.89
- Stickler syndrome 759.89
- Stiff-baby 759.89
- Sympus 759.89
- Syndrome - see also Disease
Alagille 759.89
Alport's (hereditary hematuria-nephropathy-deafness) 759.89
Angelman 759.89
Bardet-Biedl (obesity, polydactyly, and intellectual disabilities) 759.89
Barth 759.89
basal cell nevus 759.89
Beckwith (-Wiedemann) 759.89
Biedl-Bardet (obesity, polydactyly, and intellectual disabilities) 759.89
Biemond's (obesity, polydactyly, and intellectual disabilities) 759.89
Birt-Hogg-Dube 759.89
Borjeson-Forssman-Lehmann 759.89
Brachman-de Lange (Amsterdam dwarf, intellectual disabilities, and brachycephaly) 759.89
cardiofaciocutaneous 759.89
Carpenter's 759.89
cerebrohepatorenal 759.89
CHARGE association 759.89
Cockayne's (microencephaly and dwarfism) 759.89
Coffin-Lowry 759.89
congenital![](/images/vertical.gif)
affecting more than one system 759.7![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
specified type NEC 759.89
![](/images/vertical.gif)
congenital central alveolar hypoventilation 327.25![](/images/note.png)
![](/images/vertical.gif)
facial diplegia 352.6![](/images/note.png)
![](/images/vertical.gif)
muscular hypertrophy-cerebral 759.89
de Lange's (Amsterdam dwarf, intellectual disabilities, and brachycephaly) (Cornelia) 759.89
Fraser's 759.89
Freeman-Sheldon 759.89
Gillespie's (dysplasia oculodentodigitalis) 759.89
Gorlin-Chaudhry-Moss 759.89
Gorlin's 759.89
inverted Marfan's 759.89
Joubert 759.89
Kabuki 759.89
Klippel-Trenaunay 759.89
Laurence-Moon (-Bardet)-Biedl (obesity, polydactyly, and intellectual disabilities) 759.89
Marchesani (-Weill) (brachymorphism and ectopia lentis) 759.89
Menkes' 759.89![](/images/vertical.gif)
glutamic acid 759.89![](/images/vertical.gif)
maple syrup (urine) disease 270.3![](/images/note.png)
Meyer-Schwickerath and Weyers (dysplasia oculodentodigitalis) 759.89
microphthalmos (congenital) 759.89
Mieten's 759.89
Mohr's (types I and II) 759.89
Neill Dingwall (microencephaly and dwarfism) 759.89
Noonan's 759.89
oral-facial-digital 759.89
ordigitofacial 759.89
otopalatodigital 759.89
Papillon-Léage and Psaume (orodigitofacial dysostosis) 759.89
pseudo-Turner's 759.89
Rubinstein-Taybi's (brachydactylia, short stature, and intellectual disabilities) 759.89
Rud's (mental deficiency, epilepsy, and infantilism) 759.89
Russell (-Silver) (congenital hemihypertrophy and short stature) 759.89
Seckel's 759.89
sick
Silver's (congenital hemihypertrophy and short stature) 759.89
Smith-Lemli-Opitz (cerebrohepatorenal syndrome) 759.89
spherophakia-brachymorphia 759.89
Stickler 759.89
stiff-baby 759.89
Taybi's (otopalatodigital) 759.89
Ullrich-Feichtiger 759.89
VATER 759.89
Weill-Marchesani (brachymorphism and ectopia lentis) 759.89
"whistling face" (craniocarpotarsal dystrophy) 759.89
- Synophthalmus 759.89
- Taybi's syndrome (otopalatodigital) 759.89
- Teratencephalus 759.89
- Thoracogastroschisis (congenital) 759.89
- Ullrich-Feichtiger syndrome 759.89
- VATER syndrome 759.89
- Weill-Marchesani syndrome (brachymorphism and ectopia lentis) 759.89
- "Whistling face" syndrome (craniocarpotarsal dystrophy) 759.89