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2015 ICD-9-CM Diagnosis Code 753.14
Polycystic kidney, autosomal recessive
- 2015
- Billable Thru Sept 30/2015
- Non-Billable On/After Oct 1/2015
- ICD-9-CM 753.14 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 753.14 should only be used for claims with a date of service on or before September 30, 2015. For claims with a date of service on or after October 1, 2015, use an equivalent ICD-10-CM code (or codes).
Convert to ICD-10-CM:
753.14 converts approximately to:
- 2015/16 ICD-10-CM Q61.19 Other polycystic kidney, infantile type
Approximate Synonyms
- Autosomal recessive infantile polycystic kidney disease
- Polycystic kidney disease, infantile type
Clinical Information
- A genetic disorder with autosomal recessive inheritance, characterized by multiple cysts in both kidneys and associated liver lesions. Serious manifestations are usually present at birth with high perinatal mortality
- Polycystic kidney disease inherited in an autosomal recessive pattern. Patients present with progressive renal failure early in life. The autosomal recessive trait is associated with abnormalities of chromosome 6
ICD-9-CM Volume 2 Index entries containing back-references to
753.14:
- Degeneration, degenerative
kidney (see also Sclerosis, renal) 587![](/images/note.png)
renal (see also Sclerosis, renal) 587![](/images/note.png)
![](/images/16x16.gif)
fibrocystic 753.19![](/images/note.png)
![](/images/16x16.gif)
polycystic 753.12![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
adult type (APKD) 753.13![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
autosomal dominant 753.13![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
autosomal recessive 753.14
![](/images/16x16.gif)
childhood type (CPKD) 753.14
- Disease, diseased - see also Syndrome
kidney (functional) (pelvis) (see also Disease, renal) 593.9![](/images/note.png)
![](/images/vertical.gif)
chronic 585.9![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
requiring chronic dialysis 585.6![](/images/note.png)
![](/images/vertical.gif)
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stage
![](/images/vertical.gif)
cystic (congenital) 753.10![](/images/note.png)
![](/images/vertical.gif)
fibrocystic (congenital) 753.19![](/images/note.png)
![](/images/vertical.gif)
in gout 274.10![](/images/note.png)
![](/images/vertical.gif)
polycystic (congenital) 753.12![](/images/note.png)
![](/images/vertical.gif)
![](/images/16x16.gif)
adult type (APKD) 753.13![](/images/note.png)
![](/images/vertical.gif)
![](/images/16x16.gif)
autosomal dominant 753.13![](/images/note.png)
![](/images/vertical.gif)
![](/images/16x16.gif)
autosomal recessive 753.14![](/images/vertical.gif)
![](/images/16x16.gif)
childhood type (CPKD) 753.14![](/images/vertical.gif)
![](/images/16x16.gif)
infantile type 753.14
polycystic (congenital) 759.89![](/images/note.png)
![](/images/vertical.gif)
kidney or renal 753.12![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
adult type (APKD) 753.13![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
autosomal dominant 753.13![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
autosomal recessive 753.14![](/images/vertical.gif)
![](/images/vertical.gif)
childhood type (CPKD) 753.14![](/images/vertical.gif)
![](/images/vertical.gif)
infantile type 753.14
![](/images/vertical.gif)
liver or hepatic 751.62![](/images/note.png)
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lung or pulmonary 518.89![](/images/note.png)
![](/images/vertical.gif)
ovary, ovaries 256.4![](/images/note.png)
![](/images/vertical.gif)
spleen 759.0![](/images/note.png)
renal (functional) (pelvis) (see also Disease, kidney) 593.9![](/images/note.png)
![](/images/16x16.gif)
with![](/images/16x16.gif)
![](/images/vertical.gif)
edema (see also Nephrosis) 581.9![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
exudative nephritis 583.89![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
lesion of interstitial nephritis 583.89![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
stated generalized cause - see Nephritis
![](/images/16x16.gif)
acute 593.9![](/images/note.png)
![](/images/16x16.gif)
basement membrane NEC 583.89![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
with pulmonary hemorrhage (Goodpasture's syndrome) 446.21
[583.81
]
![](/images/16x16.gif)
chronic (see also Disease, kidney, chronic) 585.9![](/images/note.png)
![](/images/16x16.gif)
complicating pregnancy or puerperium NEC 646.2![](/images/note.png)
![](/images/16x16.gif)
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with hypertension - see Toxemia, of pregnancy![](/images/16x16.gif)
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affecting fetus or newborn 760.1![](/images/note.png)
![](/images/16x16.gif)
cystic, congenital (see also Cystic, disease, kidney) 753.10![](/images/note.png)
![](/images/16x16.gif)
diabetic 250.4
[583.81
]![](/images/16x16.gif)
due to![](/images/16x16.gif)
end-stage 585.6![](/images/note.png)
![](/images/16x16.gif)
exudative 583.89![](/images/note.png)
![](/images/16x16.gif)
fibrocystic (congenital) 753.19![](/images/note.png)
![](/images/16x16.gif)
gonococcal 098.19
[583.81
]![](/images/16x16.gif)
gouty 274.10![](/images/note.png)
![](/images/16x16.gif)
hypertensive (see also Hypertension, kidney) 403.90![](/images/note.png)
![](/images/16x16.gif)
immune complex NEC 583.89![](/images/note.png)
![](/images/16x16.gif)
interstitial (diffuse) (focal) 583.89![](/images/note.png)
![](/images/16x16.gif)
lupus 710.0
[583.81
]![](/images/16x16.gif)
maternal, affecting fetus or newborn 760.1![](/images/note.png)
![](/images/16x16.gif)
phosphate-losing (tubular) 588.0![](/images/note.png)
![](/images/16x16.gif)
polycystic (congenital) 753.12![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
adult type (APKD) 753.13![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
autosomal dominant 753.13![](/images/note.png)
![](/images/16x16.gif)
![](/images/vertical.gif)
autosomal recessive 753.14![](/images/16x16.gif)
![](/images/vertical.gif)
childhood type (CPKD) 753.14![](/images/16x16.gif)
![](/images/vertical.gif)
infantile type 753.14
![](/images/16x16.gif)
specified lesion or cause NEC (see also Glomerulonephritis) 583.89![](/images/note.png)
![](/images/16x16.gif)
subacute 581.9![](/images/note.png)
![](/images/16x16.gif)
syphilitic 095.4![](/images/note.png)
![](/images/16x16.gif)
tuberculous (see also Tuberculosis) 016.0
[583.81
]![](/images/16x16.gif)
tubular (see also Nephrosis, tubular) 584.5![](/images/note.png)
- Nephritis, nephritic (albuminuric) (azotemic) (congenital) (degenerative) (diffuse) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic) 583.9
![](/images/note.png)
polycystic 753.12![](/images/note.png)
![](/images/16x16.gif)
adult type (APKD) 753.13![](/images/note.png)
![](/images/16x16.gif)
autosomal dominant 753.13![](/images/note.png)
![](/images/16x16.gif)
autosomal recessive 753.14![](/images/16x16.gif)
childhood type (CPKD) 753.14![](/images/16x16.gif)
infantile type 753.14
- Polycystic (congenital) (disease) 759.89
![](/images/note.png)
kidney (congenital) 753.12![](/images/note.png)
![](/images/16x16.gif)
adult type (APKD) 753.13![](/images/note.png)
![](/images/16x16.gif)
autosomal dominant 753.13![](/images/note.png)
![](/images/16x16.gif)
autosomal recessive 753.14![](/images/16x16.gif)
childhood type (CPKD) 753.14![](/images/16x16.gif)
infantile type 753.14