Specific code 2015 ICD-9-CM Diagnosis Code 746.01
Atresia of pulmonary valve, congenital
  • 2015
  • Billable Thru Sept 30/2015
  • Non-Billable On/After Oct 1/2015

  • ICD-9-CM 746.01 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 746.01 should only be used for claims with a date of service on or before September 30, 2015. For claims with a date of service on or after October 1, 2015, use an equivalent ICD-10-CM code (or codes).
Convert to ICD-10-CM: 746.01 converts directly to:
  • 2015/16 ICD-10-CM Q22.0 Pulmonary valve atresia
Approximate Synonyms
  • Absent pulmonary valve
  • Absent pulmonary valve, congenital
  • Absent pulmonary valve, congenital (at birth)
  • Atresia of pulmonary valve
  • Congenital absence of pulmonary valve
  • Congenital atresia of pulmonary valve
  • Congenital atresia of the pulmonary valve (disorder)
  • Congenital hypoplasia of pulmonary valve
  • Congenital pulmonary valve atresia
  • Congenital pulmonary valve atresia (at birth)
  • Congenital pulmonary valve hypoplasia
  • Congenital pulmonary valve hypoplasia (at birth)
  • Pulmonary valve atresia, congenital
  • Pulmonary valve hypoplasia, congenital
  • Pulmonary valve hypoplasia, congenital (at birth)
Clinical Information
  • A congenital heart defect characterized by complete atresia of the pulmonary valve. It is manifested during infancy with cyanosis, dyspnea, and tachypnea
  • A congenital heart defect characterized by the narrowing or complete absence of the opening between the right ventricle and the pulmonary artery. Lacking a normal pulmonary valve, unoxygenated blood in the right ventricle can not be effectively pumped into the lung for oxygenation. Clinical features include rapid breathing, cyanosis, right ventricle atrophy, and abnormal heart sounds (heart murmurs)
  • Atresia of the pulmonary valve and/or the subvalvular region of the pulmonary valve
Applies To
  • Congenital absence of pulmonary valve
ICD-9-CM Volume 2 Index entries containing back-references to 746.01:
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 746.01 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2015 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.