Specific code 2014 ICD-9-CM Diagnosis Code 270.7
Other disturbances of straight-chain amino-acid metabolism
  • Billable Code
  • Short description: Straig amin-acid met NEC.
  • ICD-9-CM 270.7 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 270.7 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • 3-Phosphoglycerate dehydrogenase deficiency
  • Adenosylcobalamin and methylcobalamin synthesis defect
  • Complete deficiency of methylmalonyl-CoA mutase
  • Disorder of glutamine metabolism
  • Disorder of glycine metabolism
  • Disorder of lysine and hydroxylysine metabolism
  • Disorder of lysine AND/OR hydroxylysine metabolism
  • Disorder of serine metabolism
  • Disorder of threonine metabolism
  • Glucoglycinuria
  • Glutaric acidemia type 1
  • Glutaric acidemia, type 1
  • Glutaric aciduria, type 1
  • Glutaryl-CoA dehydrogenase deficiency
  • Glycine dehydrogenase deficiency
  • Glycine metabolism disorder
  • Hyperglycinemia
  • Hyperglycinemia, non ketotic
  • Hyperlysinemia
  • Impaired fasting glycaemia
  • Intolerance, lysinuric protein
  • Lysine and hydroxylysine metabolism disorder
  • Lysine intolerance
  • Lysinuric protein intolerance
  • Lysinuric protein intolerance, type 1
  • Lysinuric protein intolerance, type 2
  • Methylmalonic acidemia
  • Non ketotic hyperglycinemia
  • Non-ketotic hyperglycinemia
  • Non-ketotic hyperglycinemia H protein deficiency
  • Non-ketotic hyperglycinemia L protein deficiency
  • Periodic hyperlysinemia
  • Periodic hyperlysinemia with hyperammonemia
  • Persistent hyperlysinemia
  • Pipecolic acidemia
  • Saccharopinuria
  • Transient neonatal hyperglycinemia
Clinical Information
  • Autosomal recessive metabolic disorder caused by deficiencies in the mitochondrial glycine cleavage system; an enzyme system with four components: p-, t-, h-, and l-proteins; deficiency of the p-protein is the most prevalent form; clinical features include seizures, hypotonia, apnea, and coma; when the illness presents in childhood there tends to be an associated progressive dementia accompanied by extrapyramidal signs.
Applies To
  • Glucoglycinuria
  • Glycinemia (with methylmalonic acidemia)
  • Hyperglycinemia
  • Hyperlysinemia
  • Pipecolic acidemia
  • Saccharopinuria
  • Other disturbances of metabolism of glycine, threonine, serine, glutamine, and lysine
Convert to ICD-10-CM: 270.7 converts approximately to:
  • 2014 ICD-10-CM E72.3 Disorders of lysine and hydroxylysine metabolism
    Or:
  • 2014 ICD-10-CM E72.8 Other specified disorders of amino-acid metabolism
ICD-9-CM Volume 2 Index entries containing back-references to 270.7:
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 270.7 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.