Specific code 2014 ICD-9-CM Diagnosis Code 277.86
Peroxisomal disorders
  • Billable Code
  • ICD-9-CM 277.86 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 277.86 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Adolescent X linked adrenoleukodystrophy
  • Adolescent X-linked adrenoleukodystrophy
  • Adrenoleukodystrophy
  • Adrenomyeloneuropathy
  • Childhood cerebral X linked adrenoleukodystrophy
  • Childhood cerebral X-linked adrenoleukodystrophy
  • Disorder of peroxisomal function
  • Disorder, peroxisomal
  • Neonatal adrenoleucodystrophy
  • Neonatal adrenoleukodystrophy
  • Peroxisomal disorder
  • Rhizomelic chondrodysplasia punctata syndrome
  • X linked adrenoleukodystrophy, unspecified type
  • Zellweger like syndrome
  • Zellweger syndrome
  • Zellweger's-like syndrome
Clinical Information
  • A group of congenital disorders of lipid metabolism, caused by loss of the normal peroxisomes. Signs and symptoms include developmental delays, mental retardation, facial abnormalities, hepatomegaly, and hypotonia.
  • A heterogeneous group of inherited metabolic disorders marked by absent or dysfunctional peroxisomes. Peroxisomal enzymatic abnormalities may be single or multiple. Biosynthetic peroxisomal pathways are compromised, including the ability to synthesize ether lipids and to oxidize long-chain fatty acid precursors. Diseases in this category include zellweger syndrome; infantile refsum disease; rhizomelic chondrodysplasia (chondrodysplasia punctata, rhizomelic); hyperpipecolic acidemia; neonatal adrenoleukodystrophy; and adrenoleukodystrophy (x-linked). Neurologic dysfunction is a prominent feature of most peroxisomal disorders.
  • A syndrome combining the characteristics of adrenocortical insufficiency (addison disease) with those of cerebral sclerosis (schilder disease). Skin bronzing and sclerosis of the brain and demyelination are the principal manifestations.
  • Autosomal recessive peroxisomal disorder, also known as zellweger syndrome, that typically presents in the neonatal period and is usually fatal; clinical features include hypotonia, dysmorphic skull and facial bones, visual compromise, multifocal seizures, hepatomegaly, biliary dysgenesis, and swallowing difficulties; pathologically, there are migration deficits of the neocortex and degeneration of white matter tracts; zellweger-like syndrome refers to conditions that phenotypically resemble neonatal zellweger syndrome, but occur in childhood or adulthood.
  • Childhood genetic disease, transmitted as an x-linked recessive trait, characterized by diffuse abnormality of cerebral white matter and adrenal atrophy; mental deterioration progresses to dementia, aphasia, apraxia, dysarthria, and loss of vision.
Applies To
  • Adrenomyeloneuropathy
  • Neonatal adrenoleukodystrophy
  • Rhizomelic chrondrodysplasia punctata
  • X-linked adrenoleukodystrophy
  • Zellweger syndrome
Convert to ICD-10-CM: 277.86 converts approximately to:
  • 2014 ICD-10-CM E71.50 Peroxisomal disorder, unspecified
    Or:
  • 2014 ICD-10-CM E71.510 Zellweger syndrome
    Or:
  • 2014 ICD-10-CM E71.511 Neonatal adrenoleukodystrophy
    Or:
  • 2014 ICD-10-CM E71.522 Adrenomyeloneuropathy
    Or:
  • 2014 ICD-10-CM E71.529 X-linked adrenoleukodystrophy, unspecified type
    Or:
  • 2014 ICD-10-CM E71.548 Other peroxisomal disorders
ICD-9-CM Volume 2 Index entries containing back-references to 277.86:
  • Aciduria 791.9
    • glutaric
      • type I 270.7
      • type II (type IIA, IIB, IIC) 277.85
      • type III 277.86
  • Adrenoleukodystrophy 277.86
    • neonatal 277.86
    • x-linked 277.86
  • Adrenomyeloneuropathy 277.86
  • Chondrodysplasia 756.4
    • rhizomelic punctata 277.86
  • Disorder - see also Disease
    • peroxisomal 277.86
  • Neonatal - see also condition
    • adrenoleukodystrophy 277.86
  • Rhizomelic chrondrodysplasia punctata 277.86
  • Syndrome - see also Disease
    • Zellweger 277.86
  • Zellweger syndrome 277.86
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 277.86 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.