- A benign or malignant neoplasm composed of cells of neuroendocrine origin. Representative examples include paraganglioma, carcinoid tumor, and neuroendocrine carcinoma.
- A neoplasm composed of cells of neuroendocrine origin for which the malignancy status has not been established.
- A tumor derived from cells that release a hormone in response to a signal from the nervous system. Some examples of neuroendocrine tumors are carcinoid tumors, islet cell tumors, medullary thyroid carcinoma, and pheochromocytoma. These tumors secrete hormones in excess, causing a variety of symptoms.
- A tumor that forms from cells that release hormones in response to a signal from the nervous system. Some examples of neuroendocrine tumors are carcinoid tumors, islet cell tumors, medullary thyroid carcinomas, pheochromocytomas, and neuroendocrine carcinomas of the skin (merkel cell cancer). These tumors may secrete higher-than-normal amounts of hormones, which can cause many different symptoms.
- Tumors whose cells possess secretory granules and originate from the neuroectoderm, i.e., the cells of the ectoblast or epiblast that program the neuroendocrine system. Common properties across most neuroendocrine tumors include ectopic hormone production (often via apud cells), the presence of tumor-associated antigens, and isozyme composition.
209 Neuroendocrine tumors 
209.0 Malignant carcinoid tumors of the small intestine 
209.00 Malignant carcinoid tumor of the small intestine, unspecified portion convert 209.00 to ICD-10-CM- 209.01 Malignant carcinoid tumor of the duodenum convert 209.01 to ICD-10-CM
- 209.02 Malignant carcinoid tumor of the jejunum convert 209.02 to ICD-10-CM
209.03 Malignant carcinoid tumor of the ileum convert 209.03 to ICD-10-CM- 209.1 Malignant carcinoid tumors of the appendix, large intestine, and rectum
- 209.10 Malignant carcinoid tumor of the large intestine, unspecified portion convert 209.10 to ICD-10-CM
- 209.11 Malignant carcinoid tumor of the appendix convert 209.11 to ICD-10-CM
- 209.12 Malignant carcinoid tumor of the cecum convert 209.12 to ICD-10-CM
- 209.13 Malignant carcinoid tumor of the ascending colon convert 209.13 to ICD-10-CM
- 209.14 Malignant carcinoid tumor of the transverse colon convert 209.14 to ICD-10-CM
- 209.15 Malignant carcinoid tumor of the descending colon convert 209.15 to ICD-10-CM
- 209.16 Malignant carcinoid tumor of the sigmoid colon convert 209.16 to ICD-10-CM
- 209.17 Malignant carcinoid tumor of the rectum convert 209.17 to ICD-10-CM
- 209.2 Malignant carcinoid tumors of other and unspecified sites
- 209.20 Malignant carcinoid tumor of unknown primary site convert 209.20 to ICD-10-CM
- 209.21 Malignant carcinoid tumor of the bronchus and lung convert 209.21 to ICD-10-CM
- 209.22 Malignant carcinoid tumor of the thymus convert 209.22 to ICD-10-CM
- 209.23 Malignant carcinoid tumor of the stomach convert 209.23 to ICD-10-CM
- 209.24 Malignant carcinoid tumor of the kidney convert 209.24 to ICD-10-CM
- 209.25 Malignant carcinoid tumor of foregut, not otherwise specified convert 209.25 to ICD-10-CM
- 209.26 Malignant carcinoid tumor of midgut, not otherwise specified convert 209.26 to ICD-10-CM
- 209.27 Malignant carcinoid tumor of hindgut, not otherwise specified convert 209.27 to ICD-10-CM
- 209.29 Malignant carcinoid tumor of other sites convert 209.29 to ICD-10-CM
- 209.3 Malignant poorly differentiated neuroendocrine tumors
- 209.30 Malignant poorly differentiated neuroendocrine carcinoma, any site convert 209.30 to ICD-10-CM
- 209.31 Merkel cell carcinoma of the face convert 209.31 to ICD-10-CM
- 209.32 Merkel cell carcinoma of the scalp and neck convert 209.32 to ICD-10-CM
- 209.33 Merkel cell carcinoma of the upper limb convert 209.33 to ICD-10-CM
- 209.34 Merkel cell carcinoma of the lower limb convert 209.34 to ICD-10-CM
- 209.35 Merkel cell carcinoma of the trunk convert 209.35 to ICD-10-CM
- 209.36 Merkel cell carcinoma of other sites convert 209.36 to ICD-10-CM
- 209.4 Benign carcinoid tumors of the small intestine
- 209.40 Benign carcinoid tumor of the small intestine, unspecified portion convert 209.40 to ICD-10-CM
- 209.41 Benign carcinoid tumor of the duodenum convert 209.41 to ICD-10-CM
- 209.42 Benign carcinoid tumor of the jejunum convert 209.42 to ICD-10-CM
- 209.43 Benign carcinoid tumor of the ileum convert 209.43 to ICD-10-CM
- 209.5 Benign carcinoid tumors of the appendix, large intestine, and rectum
- 209.50 Benign carcinoid tumor of the large intestine, unspecified portion convert 209.50 to ICD-10-CM
- 209.51 Benign carcinoid tumor of the appendix convert 209.51 to ICD-10-CM
- 209.52 Benign carcinoid tumor of the cecum convert 209.52 to ICD-10-CM
- 209.53 Benign carcinoid tumor of the ascending colon convert 209.53 to ICD-10-CM
- 209.54 Benign carcinoid tumor of the transverse colon convert 209.54 to ICD-10-CM
- 209.55 Benign carcinoid tumor of the descending colon convert 209.55 to ICD-10-CM
- 209.56 Benign carcinoid tumor of the sigmoid colon convert 209.56 to ICD-10-CM
- 209.57 Benign carcinoid tumor of the rectum convert 209.57 to ICD-10-CM
- 209.6 Benign carcinoid tumors of other and unspecified sites
- 209.60 Benign carcinoid tumor of unknown primary site convert 209.60 to ICD-10-CM
- 209.61 Benign carcinoid tumor of the bronchus and lung convert 209.61 to ICD-10-CM
- 209.62 Benign carcinoid tumor of the thymus convert 209.62 to ICD-10-CM
- 209.63 Benign carcinoid tumor of the stomach convert 209.63 to ICD-10-CM
- 209.64 Benign carcinoid tumor of the kidney convert 209.64 to ICD-10-CM
- 209.65 Benign carcinoid tumor of foregut, not otherwise specified convert 209.65 to ICD-10-CM
- 209.66 Benign carcinoid tumor of midgut, not otherwise specified convert 209.66 to ICD-10-CM
- 209.67 Benign carcinoid tumor of hindgut, not otherwise specified convert 209.67 to ICD-10-CM
- 209.69 Benign carcinoid tumor of other sites convert 209.69 to ICD-10-CM
- 209.7 Secondary neuroendocrine tumors
209.70 Secondary neuroendocrine tumor, unspecified site convert 209.70 to ICD-10-CM- 209.71 Secondary neuroendocrine tumor of distant lymph nodes convert 209.71 to ICD-10-CM
- 209.72 Secondary neuroendocrine tumor of liver convert 209.72 to ICD-10-CM
- 209.73 Secondary neuroendocrine tumor of bone convert 209.73 to ICD-10-CM
- 209.74 Secondary neuroendocrine tumor of peritoneum convert 209.74 to ICD-10-CM
- 209.75 Secondary Merkel cell carcinoma convert 209.75 to ICD-10-CM
- 209.79 Secondary neuroendocrine tumor of other sites convert 209.79 to ICD-10-CM
