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2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Congenital Anomalies 740-759 > Other Congenital Anomalies Of Circulatory System 747.* >

2006 ICD-9-CM Diagnosis 747.49

Other anomalies of great veins

View the most recent version of ICD-9-CM 747.49

  • Anomalous venous drainage of the right lung into the inferior vena cava, with hypoplasia of the right lung. The scimitar-shaped radiographic shadow of the anomalous vein gives the syndrome its name.
  • 747.49 is a specific code that can be used to specify a diagnosis
  • 747.49 contains 49 index entries
  • View the ICD-9-CM Volume 1 747.* hierarchy

Alternate Terminology

  • Absence of vena cava (inferior) (superior)
  • Congenital stenosis of vena cava (inferior) (superior)
  • Persistent:
    • left posterior cardinal vein
    • left superior vena cava
  • Scimitar syndrome
  • Transposition of pulmonary veins NOS


 Index entries containing 747.49:

Absence (organ or part) (complete or partial)
  • pulmonary
    • vein 747.49
    • superior vena cava (congenital) 747.49
      • vein (congenital) (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60
        • great 747.49
          • portal 747.49
            • pulmonary 747.49
            • vena cava (congenital) (inferior) (superior) 747.49
              Agenesis - see also Absence, by site, congenital
              • pulmonary
                • vein 747.49
                • vein(s) (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60
                  • great 747.49
                    • portal 747.49
                      • pulmonary 747.49
                      • vena cava (inferior) (superior) 747.49
                        Anomaly, anomalous (congenital) (unspecified type) 759.9
                        • opening, pulmonary veins 747.49
                          • pulmonary 748.60
                            • venous
                              • connection 747.49
                              • return 747.49
                                • partial 747.42
                                  • total (TAPVR) (complete) (subdiaphragmatic) (supradiaphragmatic) 747.41
                              • specified type NEC
                                • vein(s) (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60
                                  • great 747.49
                                    • portal 747.49
                                      • pulmonary 747.49
                                      • vena cava (inferior) (superior) 747.49
                                      • vein(s) (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60
                                        • great 747.40
                                          • specified type NEC 747.49
                                        • venous return (pulmonary) 747.49
                                        Atresia, atretic (congenital) 759.89
                                        • pulmonary (artery) 747.3
                                          • vein 747.49
                                          • vein NEC (see also Atresia, blood vessel) 747.60
                                            • great 747.49
                                              • portal 747.49
                                                • pulmonary 747.49
                                                • vena cava (inferior) (superior) 747.49
                                                  Distortion (congenital)
                                                  • vein (peripheral) NEC (see also Distortion, peripheral vascular system) 747.60
                                                    • great 747.49
                                                      • portal 747.49
                                                        • pulmonary 747.49
                                                        • vena cava (inferior) (superior) 747.49
                                                          Hypoplasia, hypoplasis 759.89
                                                          • vein(s) (peripheral) NEC (see also Hypoplasia, peripheral vascular system) 747.60
                                                            • great 747.49
                                                              • portal 747.49
                                                                • pulmonary 747.49
                                                                • vena cava (inferior) (superior) 747.49
                                                                  Malposition
                                                                  • congenital
                                                                    • vein(s) (peripheral) NEC (see also Malposition, congenital, peripheral vascular system) 747.60
                                                                      • great 747.49
                                                                        • portal 747.49
                                                                          • pulmonary 747.49
                                                                          • vena cava (inferior) (superior) 747.49
                                                                          Obstruction, obstructed, obstructive
                                                                          • pulmonary
                                                                            • vein, isolated 747.49
                                                                            Persistence, persistent (congenital) 759.89
                                                                            • left
                                                                              • posterior cardinal vein 747.49
                                                                                • superior vena cava 747.49
                                                                                • sinus
                                                                                  • venosus with imperfect incorporation in right auricle 747.49
                                                                                  Scimitar syndrome (anomalous venous drainage, right lung to inferior vena cava) 747.49
                                                                                    Stenosis (cicatricial) - see also Stricture
                                                                                    • pulmonary (artery) (congenital) 747.3
                                                                                      • vein 747.49
                                                                                    • vena cava (inferior) (superior) 459.2
                                                                                      • congenital 747.49
                                                                                      Stricture (see also Stenosis) 799.89
                                                                                      • pulmonary, pulmonic
                                                                                        • vein (congenital) 747.49
                                                                                      • vena cava (inferior) (superior) NEC 459.2
                                                                                        • congenital 747.49
                                                                                        Syndrome - see also Disease
                                                                                        • Scimitar (anomalous venous drainage, right lung to inferior vena cava) 747.49
                                                                                          Termination
                                                                                          • anomalous - see also Malposition, congenital
                                                                                            • portal vein 747.49
                                                                                            Transposition (congenital) - see also Malposition, congenital
                                                                                            • pulmonary veins 747.49