Home > 2013 ICD-9-CM Diagnosis Codes > Congenital Anomalies 740-759 > Other congenital anomalies of circulatory system 747-
2013 ICD-9-CM Diagnosis Code 747.49
Other anomalies of great veins
- ICD-9-CM 747.49 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
747.49 Alternative Terminology
- Abnormal connection of hepatic vein to atrium
- Abnormal inferior vena caval connection
- Abnormality of right superior vena cava
- Absence of inferior vena cava
- Absence of inferior vena cava, congenital
- Absence of superior vena cava
- Absent right superior vena cava
- Anomalous insertion of right superior vena cava to left atrium
- Anomalous portal vein termination
- Atresia of superior vena cava, congenital
- Atresia of superior vena cava, congenital (at birth)
- Atretic right superior vena cava
- Bilateral superior vena cava
- Congenital (at birth) absence of inferior vena cava
- Congenital abnormality of great veins and coronary sinus
- Congenital absence of inferior vena cava
- Congenital absence of portal vein
- Congenital absence of superior vena cava
- Congenital absence of vena cava
- Congenital anomaly of inferior vena cava
- Congenital anomaly of superior vena cava
- Congenital atresia of inferior vena cava
- Congenital atresia of superior vena cava
- Congenital coronary sinus stenosis
- Congenital dilatation of inferior vena cava
- Congenital extrahepatic portal-systemic shunt
- Congenital malposition of inferior vena cava
- Congenital malposition of superior vena cava
- Congenital partial portal-systemic shunt
- Congenital portal-systemic shunt
- Congenital pulmonary vein confluence
- Congenital pulmonary venous atrium
- Congenital splenorenal shunt
- Congenital stenosis of inferior vena cava
- Congenital stenosis of pulmonary veins
- Congenital stenosis of superior vena cava
- Congenital stenosis of vena cava
- Congenital systemic venous atrium
- Congenital transposition of azygos vein
- Ductus venosus abnormality
- Hepatoportal microvascular dysplasia
- Inferior cava to left of spine with right descending aorta
- Inferior vena cava connecting to coronary sinus
- Inferior vena cava connecting to morphological left atrium
- Inferior vena cava interruption with bilateral azygos continuation
- Inferior vena cava interruption with left sided hemiazygos continuation
- Inferior vena cava interruption with right sided azygos continuation
- Inferior vena cava to left of spine
- Left superior caval vein persisting to coronary sinus
- Left superior caval vein persisting to left sided atrium
- Obstructive eustachian valve
- Patent ductus venosus
- Persistent left posterior cardinal vein
- Persistent left superior vena cava
- Persistent vertical vein
- Prominent valve of inferior vena cava
- Pulmonary vein atresia
- Pulmonary vein stenosis
- Pulmonary vein stenosis, congenital
- Pulmonary vein stenosis, congenital (present at birth)
- Saccular dilatation of right superior vena cava
- Scimitar syndrome
- Splenoportal vascular anomaly
- Stenosis (narrowing) of inferior vena cava, congenital
- Stenosis (narrowing) of superior vena cava, congenital
- Stenosis (narrowing) of vena cava, congenital
- Stenosis of inferior vena cava, congenital
- Stenosis of superior vena cava, congenital
- Stenosis of vena cava, congenital
- Subclavian vein stenosis
- Transposition of pulmonary veins
Applies To
- Absence of vena cava (inferior) (superior)
- Congenital stenosis of vena cava (inferior) (superior)
- Persistent:
- left posterior cardinal vein
- left superior vena cava
- Scimitar syndrome
- Transposition of pulmonary veins NOS
Convert 747.49 to ICD-10-CM 

ICD-9-CM Volume 2 Index entries containing back-references to 747.49:
- Absence (organ or part) (complete or partial)
superior vena cava (congenital) 747.49
vein (congenital) (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60

brain 747.81

great 747.49
portal 747.49
pulmonary 747.49
vena cava (congenital) (inferior) (superior) 747.49
- Agenesis - see also Absence, by site, congenital
vein(s) (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60

brain 747.81

great 747.49
portal 747.49
pulmonary 747.49
vena cava (inferior) (superior) 747.49
- Anomaly, anomalous (congenital) (unspecified type) 759.9

opening, pulmonary veins 747.49
pulmonary 748.60
specified type NEC
adrenal (gland) 759.1

alimentary tract (complete) (partial) 751.8

ankle 755.69

anus, anal (canal) 751.5

aorta, aortic 747.29


arch 747.21

appendix 751.5

arm 755.59

artery (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60

auditory canal 744.29


causing impairment of hearing 744.02

bile duct or passage 751.69

bladder 753.8


neck 753.8

bone(s) 756.9

brain 742.4

breast 757.6

broad ligament 752.19

bronchus 748.3

canal of Nuck 752.89

cardiac septal closure 745.8

carpus 755.59

cartilaginous 756.9

cecum 751.5

cervix 752.49

chest (wall) 756.3

chin 744.89

ciliary body 743.46

circulatory system 747.89

clavicle 755.51

clitoris 752.49

coccyx 756.19

colon 751.5

common duct 751.69

connective tissue 756.89

cricoid cartilage 748.3

cystic duct 751.69

diaphragm 756.6

digestive organ(s) or tract 751.8

duodenum 751.5

ear 744.29

ejaculatory duct 752.89

endocrine 759.2

epiglottis 748.3

esophagus 750.4

Eustachian tube 744.24

eye 743.8

face 744.89


bone(s) 756.0

fallopian tube 752.19

fascia 756.89

femur 755.69

fibula 755.69

finger 755.59

foot 755.67

fovea centralis 743.55

gallbladder 751.69

Gartner's duct 752.89

gastrointestinal tract 751.8

genitalia, genital organ(s)
genitourinary tract NEC 752.89

glottis 748.3

hair 757.4

hand 755.59

heart 746.89

hepatic duct 751.69

hydatid of Morgagni 752.89

hymen 752.49

integument 757.8

intestine (large) (small) 751.5


fixational type 751.4

iris 743.46

jejunum 751.5

joint 755.8

kidney 753.3

knee 755.64

labium (majus) (minus) 752.49

labyrinth, membranous 744.05

larynx 748.3

leg 755.69

lens 743.39

limb, except reduction deformity 755.8

lip 750.26

liver 751.69

lung (fissure) (lobe) 748.69

meatus urinarius 753.8

metacarpus 755.59

mouth 750.26

Müllerian
muscle 756.89


eye 743.69

musculoskeletal system, except limbs 756.9

nail 757.5

neck 744.89

nerve 742.8

nervous system 742.8

nipple 757.6

nose 748.1

organ NEC 759.89


of Corti 744.05

osseous meatus (ear) 744.03

ovary 752.0

oviduct 752.19

pancreas 751.7

parathyroid 759.2

patella 755.64

pelvic girdle 755.69

penis 752.69

pericardium 746.89

peripheral vascular system NEC (see also Anomaly, peripheral vascular system) 747.60

pharynx 750.29

pituitary 759.2

prostate 752.89

radius 755.59

rectum 751.5

respiratory system 748.8

rib 756.3

round ligament 752.89

sacrum 756.19

salivary duct or gland 750.26

scapula 755.59

sclera 743.47

scrotum 752.89


transposition 752.81

seminal duct or tract 752.89

shoulder girdle 755.59

site NEC 759.89

skin 757.39

skull (bone(s)) 756.0

specified organ or site NEC 759.89

spermatic cord 752.89

spinal cord 742.59

spine 756.19

spleen 759.0

sternum 756.3

stomach 750.7

tarsus 755.67

tendon 756.89

testis 752.89

thorax (wall) 756.3

thymus 759.2

thyroid (gland) 759.2


cartilage 748.3

tibia 755.69

toe 755.66

tongue 750.19

trachea (cartilage) 748.3

ulna 755.59

urachus 753.7

ureter 753.4


obstructive 753.29

urethra 753.8


obstructive 753.6

urinary tract 753.8

uterus (Müllerian) 752.39

uvula 750.26

vagina 752.49

vascular NEC (see also Anomaly, peripheral vascular system) 747.60


brain 747.81

vas deferens 752.89

vein(s) (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60


brain 747.81


great 747.49

portal 747.49

pulmonary 747.49

vena cava (inferior) (superior) 747.49
vertebra 756.19

vulva 752.49
vein(s) (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60
- Atresia, atretic (congenital) 759.89

vein NEC (see also Atresia, blood vessel) 747.60

cardiac 746.89

great 747.49
portal 747.49
pulmonary 747.49
vena cava (inferior) (superior) 747.49
- Distortion (congenital)
vein (peripheral) NEC (see also Distortion, peripheral vascular system) 747.60

great 747.49
portal 747.49
pulmonary 747.49
vena cava (inferior) (superior) 747.49
- Hypoplasia, hypoplasis 759.89

vein(s) (peripheral) NEC (see also Hypoplasia, peripheral vascular system) 747.60
vena cava (inferior) (superior) 747.49
- Malposition
congenital
adrenal (gland) 759.1

alimentary tract 751.8

aorta 747.21

appendix 751.5

arterial trunk 747.29

artery (peripheral) NEC (see also Malposition, congenital, peripheral vascular system) 747.60

auditory canal 744.29


causing impairment of hearing 744.02

auricle (ear) 744.29

biliary duct or passage 751.69

bladder (mucosa) 753.8


exteriorized or extroverted 753.5

brachial plexus 742.8

brain tissue 742.4

breast 757.6

bronchus 748.3

cardiac apex 746.87

cecum 751.5

clavicle 755.51

colon 751.5

digestive organ or tract NEC 751.8

ear (auricle) (external) 744.29


ossicles 744.04

endocrine (gland) NEC 759.2

epiglottis 748.3

Eustachian tube 744.24

eye 743.8

facial features 744.89

fallopian tube 752.19

finger(s) 755.59


supernumerary 755.01

foot 755.67

gallbladder 751.69

gastrointestinal tract 751.8

genitalia, genital organ(s) or tract
glottis 748.3

hand 755.59

heart 746.87

hepatic duct 751.69

hip (joint) (see also Dislocation, hip, congenital) 754.30

intestine (large) (small) 751.5


with anomalous adhesions, fixation, or malrotation 751.4

joint NEC 755.8

kidney 753.3

larynx 748.3

limb 755.8

liver 751.69

lung (lobe) 748.69

nail(s) 757.5

nerve 742.8

nervous system NEC 742.8

nose, nasal (septum) 748.1

organ or site NEC - see Anomaly, specified type NEC, by site
ovary 752.0

pancreas 751.7

parathyroid (gland) 759.2

patella 755.64

peripheral vascular system 747.60

pituitary (gland) 759.2

respiratory organ or system NEC 748.9

rib (cage) 756.3


supernumerary in cervical region 756.2

scapula 755.59

shoulder 755.59

spinal cord 742.59

spine 756.19

spleen 759.0

sternum 756.3

stomach 750.7

symphysis pubis 755.69

testis (undescended)752.51

thymus (gland) 759.2

thyroid (gland) (tissue) 759.2


cartilage 748.3

toe(s) 755.66


supernumerary 755.02

tongue 750.19

trachea 748.3

uterus 752.39

vein(s) (peripheral) NEC (see also Malposition, congenital, peripheral vascular system) 747.60


great 747.49

portal 747.49

pulmonary 747.49

vena cava (inferior) (superior) 747.49
- Obstruction, obstructed, obstructive
pulmonary
valve (heart) (see also Endocarditis, pulmonary) 424.3

vein, isolated 747.49
- Persistence, persistent (congenital) 759.89

left
posterior cardinal vein 747.49
root with right arch of aorta 747.21

superior vena cava 747.49
sinus
urogenitalis 752.89

venosus with imperfect incorporation in right auricle 747.49
- Scimitar syndrome (anomalous venous drainage, right lung to inferior vena cava) 747.49
- Stenosis (cicatricial) - see also Stricture
pulmonary (artery) (congenital) 747.31
vena cava (inferior) (superior) 459.2

congenital 747.49
- Stricture (see also Stenosis) 799.89

pulmonary, pulmonic
vena cava (inferior) (superior) NEC 459.2

congenital 747.49
- Syndrome - see also Disease
Scimitar (anomalous venous drainage, right lung to inferior vena cava) 747.49
- Termination
anomalous - see also Malposition, congenital
portal vein 747.49
right pulmonary vein 747.42
- Transposition (congenital) - see also Malposition, congenital
pulmonary veins 747.49
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 747.49 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2013 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.
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