Home > 2013 ICD-9-CM Diagnosis Codes > Congenital Anomalies 740-759 > Other congenital anomalies of heart 746-
2013 ICD-9-CM Diagnosis Code 746.89
Other specified congenital anomalies of heart
- ICD-9-CM 746.89 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
746.89 Alternative Terminology
- Abnormal atrioventricular connection
- Abnormal atrioventricular connection - biventricular
- Abnormal atrioventricular connection - univentricular
- Abnormal number of leaflets
- Abnormal position of cardiac valve
- Abnormality of atrioventricular valve
- Abnormality of common atrioventricular valve papillary muscle
- Aborted systole
- Absent atrioventricular connection with straddling valve
- Absent left sided atrioventricular connection
- Absent right atrioventricular valve leaflets
- Accessory tissue on aortic valve cusp
- Accessory tissue on common atrioventricular valve leaflet
- Accessory tissue on left atrioventricular valve leaflet
- Accessory tissue on mitral leaflet
- Accessory tissue on right atrioventricular valve leaflet
- Accessory tissue on tricuspid leaflet
- Accessory tissue on truncal valve cusp
- Anomalous muscle bands of left ventricle
- Anomalous muscle bands of right ventricle
- Anomalous valve of coronary sinus
- Anterior leaflet of mitral valve attached to septum
- Aortic orifice anterior left with respect to pulmonary orifice
- Aortic orifice anterior right with respect to pulmonary orifice
- Aortic orifice anterior with respect to pulmonary orifice
- Aortic orifice left side by side with respect to pulmonary orifice
- Aortic orifice posterior left with respect to pulmonary orifice
- Aortic orifice posterior with respect to pulmonary orifice
- Aortic valve atresia, congenital
- Aortic valve dysplasia
- Aortic valve ring hypoplasia
- Arrhythmogenic right ventricular dysplasia
- Arrhythmogenic right ventricular dysplasia, congenital
- Atresia of common atrioventricular valve
- Atrioventricular septal defect - ventricular component under inferior bridging leaflet
- Atrioventricular septal defect - ventricular component under superior bridging leaflet
- Atrioventricular septal defect with ventricular imbalance consisting of dominant left ventricle and hypoplastic right ventricle
- Bifid apex of heart
- Bilateral atria
- Bilateral isomeric atria
- Brugada syndrome
- Cardiomegaly, congenital
- Cardiomegaly, congenital (enlarged heart, at birth)
- Chiari's network
- Cleft leaflet of mitral valve
- Cleft leaflet of tricuspid valve
- Commissural fusion of aortic cusp
- Commissural fusion of aortic valve
- Common atrioventricular valve stenosis
- Complex congenital heart defect
- Congenital (at birth) cleft leaflet of mitral valve
- Congenital abnormality of atrioventricular valves in atrioventricular septal defect
- Congenital absence of aortic valve
- Congenital absence of chordae tendineae
- Congenital absence of coronary sinus
- Congenital aneurysm of heart
- Congenital anomaly of aortic valve
- Congenital anomaly of heart valve
- Congenital anomaly of pericardium
- Congenital arrhythmogenic right ventricular dysplasia
- Congenital atresia of aortic valve
- Congenital atresia of cardiac valve
- Congenital atresia of cardiac vein
- Congenital atresia of mitral valve
- Congenital cardiomegaly
- Congenital cleft of cardiac valve
- Congenital conduction defect
- Congenital dilatation of atrium
- Congenital dilatation of cardiac ventricle
- Congenital disease and abnormality of heart, thoracic aorta and pericardium
- Congenital diverticulum of left ventricle
- Congenital enlargement of coronary sinus
- Congenital epicardial cyst
- Congenital heart defect, complex
- Congenital his bundle tachycardia
- Congenital hypertrophy of cardiac ventricle
- Congenital hypoplasia of aortic valve
- Congenital hypoplasia of cardiac vein
- Congenital hypoplasia of cardiac ventricle
- Congenital hypoplasia of heart
- Congenital hypoplasia of mitral valve
- Congenital insufficiency of tricuspid valve
- Congenital left ventricular aneurysm
- Congenital pericardial defect
- Congenital right ventricular aneurysm
- Congenital right ventricular diverticulum
- Congenital stenosis of cardiac valve
- Congenital valvular insufficiency
- Coronary sinus abnormality
- Coronary sinus defect in left atrium
- Criss-cross heart
- Defect, heart, complex congenital (at birth)
- Diffuse hypoplasia of left ventricle
- Dilatation of common atrioventricular valve annulus
- Dilatation of left atrioventricular valve annulus
- Dilatation of mitral annulus
- Dilatation of right atrioventricular valve annulus
- Dilatation of tricuspid annulus
- Discordant atrioventricular connection
- Discordant ventriculoarterial connection
- Diverticulum of left ventricle, congenital (at birth)
- Divided left atrium
- Divided right atrium
- Double aortic valve
- Double inlet left ventricle
- Double inlet right ventricle
- Double inlet to ventricle of indeterminate morphology
- Double inlet ventricle
- Double mitral valve
- Double orifice of common atrioventricular valve
- Double orifice of left atrioventricular valve
- Double orifice of mitral valve
- Double orifice of right atrioventricular valve
- Double orifice of tricuspid valve
- Double outlet from ventricle of indeterminate morphology
- Ebstein-like downward displacement of mitral valve
- Ebstein-like malformation of the mitral valve
- Eccentric opening of aortic valve
- Hemicardia
- Heterotaxy syndrome, heart, congenital
- Heterotaxy syndrome, heart, congenital (at birth)
- Holt oram syndrome
- Holt-oram syndrome
- Hypoplasia of aortic valve cusp
- Hypoplasia of cardiac vein
- Hypoplasia of cardiac vein, congenital
- Hypoplasia of left ventricular outflow tract
- Hypoplasia of left ventricular outflow tract and trabecular area
- Hypoplasia of right heart
- Hypoplastic (abnormally small) right heart syndrome
- Hypoplastic common atrioventricular valve papillary muscle
- Hypoplastic mitral papillary muscle
- Hypoplastic right atrioventricular valve papillary muscle
- Hypoplastic right heart syndrome
- Hypoplastic tricuspid papillary muscle
- Imperforate common atrioventricular valve
- Imperforate left atrioventricular valve
- Imperforate right atrioventricular valve
- Insufficiency of tricuspid valve congenital (at birth)
- Leakage of conduit from right atrium to pulmonary artery
- Left atrial appendage - right - juxtaposition
- Left atrial appendage aneurysm
- Left atrial dilatation
- Left atrial hypoplasia
- Left atrioventricular valve atresia
- Left atrioventricular valve dysplasia
- Left atrioventricular valve hypoplasia
- Left atrioventricular valve leaflet abnormality
- Left atrioventricular valve leaflet dysplasia
- Left atrioventricular valve prolapse
- Left atrioventricular valve stenosis
- Left ventricle diverticulum, congenital
- Left ventricular diverticulum
- Left ventricular hypoplasia
- Left ventricular outflow tract abnormality
- Left ventricular outflow tract atresia
- Left ventricular outflow tract obstruction
- Levoatrial cardinal vein
- Mitral valve atresia, congenital
- Mitral valve atresia, congenital (present at birth)
- Mitral valve cleft leaflet, congenital
- Mitral valve dysplasia
- Monocuspid cardiac valve
- Myxomatosis of cardiac valve
- Overriding left atrioventricular valve
- Overriding mitral valve
- Overriding right atrioventricular valve
- Overriding tricuspid valve
- Partial agenesis of pericardium
- Pericardial anomaly
- Pericardial cyst, congenital
- Pericardial defect
- Pericardial diverticulum
- Pleuropericardial cyst
- Prolapse of eustachian valve
- Quadricuspid aortic valve
- Quadricuspid cardiac valve
- Quadricuspid pulmonary valve
- Regurgitation of common atrioventricular valve
- Right atrial appendage aneurysm
- Right atrial endocardial fibroelastosis
- Right atrioventricular valve atresia
- Right atrioventricular valve chordae too long
- Right atrioventricular valve chordae too short
- Right atrioventricular valve leaflets absent in double inlet ventricle
- Right hypoplastic heart syndrome
- Right to left cardiac shunt
- Right ventricular diverticulum
- Right ventricular outflow obstruction - localized
- Rudimentary left ventricle
- Septoparietal trabeculations
- Situs ambiguus
- Solitary aortic trunk with pulmonary atresia
- Solitary pulmonary trunk with aortic atresia
- Straddling left atrioventricular valve
- Straddling mitral valve
- Straddling right atrioventricular valve
- Straddling tricuspid valve
- Totally absent pericardium
- Tricuspid annulus hypoplasia
- Tricuspid valve regurgitation, congenital
- Unicuspid aortic valve
Applies To
- Atresia of cardiac vein
- Hypoplasia of cardiac vein
- Congenital:
- cardiomegaly
- diverticulum, left ventricle
- pericardial defect
Convert 746.89 to ICD-10-CM 

ICD-9-CM Volume 2 Index entries containing back-references to 746.89:
- Absence (organ or part) (complete or partial)
aortic valve (congenital) 746.89
pericardium (congenital) 746.89
- Accessory (congenital)
cusp(s), heart valve NEC 746.89
pulmonary 746.09
heart 746.89
valve NEC 746.89

pulmonary 746.09
leaflet, heart valve NEC 746.89
pulmonary 746.09
valve, heart NEC 746.89
pulmonary 746.09
- Agenesis - see also Absence, by site, congenital
heart 746.89
valve NEC 746.89

aortic 746.89

mitral 746.89

pulmonary 746.01
pericardium 746.89
- Aneurysm (anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (ruptured) (saccular) (varicose) 442.9

- Anomaly, anomalous (congenital) (unspecified type) 759.9

cardiac 746.9
coronary
artery 746.85

vein 746.89
heart 746.9

auricle 746.9

bands 746.9

fibroelastosis cordis 425.3

folds 746.9

malposition 746.87

maternal, affecting fetus or newborn 760.3

obstructive NEC 746.84

patent ductus arteriosus (Botalli) 747.0

septum 745.9

specified type NEC 746.89
tetralogy of Fallot 745.2

valve NEC 746.9

ventricle 746.9
mitral (leaflets) (valve) 746.9
pericardium 746.89
specified type NEC
adrenal (gland) 759.1

alimentary tract (complete) (partial) 751.8

ankle 755.69

anus, anal (canal) 751.5

aorta, aortic 747.29


arch 747.21

appendix 751.5

arm 755.59

artery (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60

auditory canal 744.29


causing impairment of hearing 744.02

bile duct or passage 751.69

bladder 753.8


neck 753.8

bone(s) 756.9

brain 742.4

breast 757.6

broad ligament 752.19

bronchus 748.3

canal of Nuck 752.89

cardiac septal closure 745.8

carpus 755.59

cartilaginous 756.9

cecum 751.5

cervix 752.49

chest (wall) 756.3

chin 744.89

ciliary body 743.46

circulatory system 747.89

clavicle 755.51

clitoris 752.49

coccyx 756.19

colon 751.5

common duct 751.69

connective tissue 756.89

cricoid cartilage 748.3

cystic duct 751.69

diaphragm 756.6

digestive organ(s) or tract 751.8

duodenum 751.5

ear 744.29

ejaculatory duct 752.89

endocrine 759.2

epiglottis 748.3

esophagus 750.4

Eustachian tube 744.24

eye 743.8

face 744.89


bone(s) 756.0

fallopian tube 752.19

fascia 756.89

femur 755.69

fibula 755.69

finger 755.59

foot 755.67

fovea centralis 743.55

gallbladder 751.69

Gartner's duct 752.89

gastrointestinal tract 751.8

genitalia, genital organ(s)
genitourinary tract NEC 752.89

glottis 748.3

hair 757.4

hand 755.59

heart 746.89

valve NEC 746.89


pulmonary 746.09

hepatic duct 751.69

hydatid of Morgagni 752.89

hymen 752.49

integument 757.8

intestine (large) (small) 751.5


fixational type 751.4

iris 743.46

jejunum 751.5

joint 755.8

kidney 753.3

knee 755.64

labium (majus) (minus) 752.49

labyrinth, membranous 744.05

larynx 748.3

leg 755.69

lens 743.39

limb, except reduction deformity 755.8

lip 750.26

liver 751.69

lung (fissure) (lobe) 748.69

meatus urinarius 753.8

metacarpus 755.59

mouth 750.26

Müllerian
muscle 756.89


eye 743.69

musculoskeletal system, except limbs 756.9

nail 757.5

neck 744.89

nerve 742.8

nervous system 742.8

nipple 757.6

nose 748.1

organ NEC 759.89


of Corti 744.05

osseous meatus (ear) 744.03

ovary 752.0

oviduct 752.19

pancreas 751.7

parathyroid 759.2

patella 755.64

pelvic girdle 755.69

penis 752.69

pericardium 746.89
peripheral vascular system NEC (see also Anomaly, peripheral vascular system) 747.60

pharynx 750.29

pituitary 759.2

prostate 752.89

radius 755.59

rectum 751.5

respiratory system 748.8

rib 756.3

round ligament 752.89

sacrum 756.19

salivary duct or gland 750.26

scapula 755.59

sclera 743.47

scrotum 752.89


transposition 752.81

seminal duct or tract 752.89

shoulder girdle 755.59

site NEC 759.89

skin 757.39

skull (bone(s)) 756.0

specified organ or site NEC 759.89

spermatic cord 752.89

spinal cord 742.59

spine 756.19

spleen 759.0

sternum 756.3

stomach 750.7

tarsus 755.67

tendon 756.89

testis 752.89

thorax (wall) 756.3

thymus 759.2

thyroid (gland) 759.2


cartilage 748.3

tibia 755.69

toe 755.66

tongue 750.19

trachea (cartilage) 748.3

ulna 755.59

urachus 753.7

ureter 753.4


obstructive 753.29

urethra 753.8


obstructive 753.6

urinary tract 753.8

uterus (Müllerian) 752.39

uvula 750.26

vagina 752.49

vascular NEC (see also Anomaly, peripheral vascular system) 747.60


brain 747.81

vas deferens 752.89

vein(s) (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60

vena cava (inferior) (superior) 747.49

vertebra 756.19

vulva 752.49
tricuspid (leaflet) (valve) 746.9
- Aplasia - see also Agenesis
aortic valve (congenital) 746.89
- Atresia, atretic (congenital) 759.89

aortic (orifice) (valve) 746.89
arch 747.11
mitral valve 746.89
with atresia or hypoplasia of aortic orifice or valve, with hypoplasia of ascending aorta and defective development of left ventricle 746.7
- Bifid (congenital) - see also Imperfect, closure
apex, heart 746.89
- Brugada syndrome 746.89
- Cardiomegaly (see also Hypertrophy, cardiac) 429.3

congenital 746.89
- Chiari's
network 746.89
- Cyst (mucus) (retention) (serous) (simple)
celomic (pericardium) 746.89
pericardial (congenital) 746.89
acquired (secondary) 423.8
spring water (pericardium) 746.89
- Defect, defective 759.9

pericardium 746.89
- Deformity 738.9

heart (congenital) 746.9
mitral (leaflets) (valve) (congenital) 746.9
- Degeneration, degenerative
myocardium, myocardial (brown) (calcareous) (fatty) (fibrous) (hyaline) (mural) (muscular) (pigmentary) (senile) (with arteriosclerosis) 429.1
- Dilatation
cardiac (acute) (chronic) (see also Hypertrophy, cardiac) 429.3
- Disease, diseased - see also Syndrome
heart (organic) 429.9

with

acute pulmonary edema (see also Failure, ventricular, left) 428.1

amyloid 277.39
[425.7
]
aortic (valve) (see also Endocarditis, aortic) 424.1

arteriosclerotic or sclerotic (minimal) (senile) - see Arteriosclerosis, coronary
artery, arterial - see Arteriosclerosis, coronary
atherosclerotic - see Arteriosclerosis, coronary
beer drinkers' 425.5

beriberi 265.0
[425.7
]
black 416.0

congenital NEC 746.9

congestive (see also Failure, heart) 428.0

coronary 414.9

cryptogenic 429.9

due to
fetal 746.9


inflammatory 746.89

fibroid (see also Myocarditis) 429.0

functional 427.9

glycogen storage 271.0
[425.7
]
gonococcal NEC 098.85

gouty 274.82

hypertensive (see also Hypertension, heart) 402.90

hyperthyroid (see also Hyperthyroidism) 242.9
[425.7
]
incompletely diagnosed - see Disease, heart
ischemic (chronic) (see also Ischemia, heart) 414.9

kyphoscoliotic 416.1

mitral (see also Endocarditis, mitral) 394.9

muscular (see also Degeneration, myocardial) 429.1

postpartum 674.8

psychogenic (functional) 306.2

pulmonary (chronic) 416.9

rheumatic (chronic) (inactive) (old) (quiescent) (with chorea) 398.90

rheumatoid - see Arthritis, rheumatoid
sclerotic - see Arteriosclerosis, coronary
senile (see also Myocarditis) 429.0

specified type NEC 429.89

syphilitic 093.89

thyroid (gland) (see also Hyperthyroidism) 242.9
[425.7
]
thyrotoxic (see also Thyrotoxicosis) 242.9
[425.7
]
tuberculous (see also Tuberculosis) 017.9
[425.8
]
valve, valvular (obstructive) (regurgitant) - see also Endocarditis
vascular - see Disease, cardiovascular
- Displacement, displaced
ventricular septum 746.89
with rudimentary ventricle 746.89
- Distortion (congenital)
heart (auricle) (ventricle) 746.89
valve (cusp) 746.89
- Diverticula, diverticulosis, diverticulum (acute) (multiple) (perforated) (ruptured) 562.10

heart (congenital) 746.89
pericardium (congenital) (cyst) 746.89
acquired (true) 423.8
ventricle, left (congenital) 746.89
- Double
orifice
heart valve NEC 746.89

pulmonary 746.09
- Endocarditis (chronic) (indeterminate) (interstitial) (marantic) (nonbacterial thrombotic) (residual) (sclerotic) (sclerous) (senile) (valvular) 424.90

aortic (heart) (nonrheumatic) (valve) 424.1
mitral (chronic) (double) (fibroid) (heart) (inactive) (valve) (with chorea) 394.9
tricuspid (chronic) (heart) (inactive) (rheumatic) (valve) (with chorea) 397.0
- Fenestration, fenestrated - see also Imperfect, closure
cusps, heart valve NEC 746.89
pulmonary 746.09
- Folds, anomalous - see also Anomaly, specified type NEC
heart 746.89
- Fusion, fused (congenital)
cusps, heart valve NEC 746.89
mitral 746.5

tricuspid 746.89
- Hemicardia 746.89
- Hypertrophy, hypertrophic
cardiac (chronic) (idiopathic) 429.3
heart (idiopathic) - see also Hypertrophy, cardiac
valve - see also Endocarditis

congenital NEC 746.89
- Hypoplasia, hypoplasis 759.89

cardiac 746.89
valve - see Hypoplasia, heart, valve
vein 746.89
- Imperfect
closure (congenital)
alimentary tract NEC 751.8

atrioventricular ostium 745.69

atrium (secundum) 745.5


primum 745.61

branchial cleft or sinus 744.41

choroid 743.59

cricoid cartilage 748.3

cusps, heart valve NEC 746.89

pulmonary 746.09

ductus
ear drum 744.29


causing impairment of hearing 744.03

endocardial cushion 745.60

epiglottis 748.3

esophagus with communication to bronchus or trachea 750.3

Eustachian valve 746.89
eyelid 743.62

face, facial (see also Cleft, lip) 749.10

foramen
genitalia, genital organ(s) or system
glottis 748.3

heart valve (cusps) NEC 746.89
interatrial ostium or septum 745.5

interauricular ostium or septum 745.5

interventricular ostium or septum 745.4

iris 743.46

kidney 753.3

larynx 748.3

lens 743.36

lip (see also Cleft, lip) 749.10

nasal septum or sinus 748.1

nose 748.1

omphalomesenteric duct 751.0

optic nerve entry 743.57

organ or site NEC - see Anomaly, specified type, by site
ostium
palate (see also Cleft, palate) 749.00

preauricular sinus 744.46

retina 743.56

roof of orbit 742.0

sclera 743.47

septum
skull 756.0

spine (with meningocele) (see also Spina bifida) 741.90

thyroid cartilage 748.3

trachea 748.3

tympanic membrane 744.29


causing impairment of hearing 744.03

uterus (with communication to bladder, intestine, or rectum) 752.39

uvula 749.02


with cleft lip (see also Cleft, palate, with cleft lip) 749.20

vitelline duct 751.0
- Incompetency, incompetence, incompetent
heart valve, congenital 746.89
- Insufficiency, insufficient
heart - see also Insufficiency, myocardial
myocardial, myocardium (with arteriosclerosis) 428.0

with rheumatic fever (conditions classifiable to 390
)
congenital 746.89
due to presence of (cardiac) prosthesis 429.4

fetus or newborn 779.89

following cardiac surgery 429.4

hypertensive (see also Hypertension, heart) 402.91

postoperative 997.1


long-term effect of cardiac surgery 429.4

rheumatic 398.0

syphilitic 093.82
- Malformation (congenital) - see also Anomaly
- Morbus
caeruleus 746.89
- Myocarditis (fibroid) (interstitial) (old) (progressive) (senile) (with arteriosclerosis) 429.0

congenital 746.89
- Nonclosure - see also Imperfect, closure
Eustachian valve 746.89
- Nondevelopment
heart 746.89
- Patent - see also Imperfect closure
Eustachian
tube 381.7

valve 746.89
- Quadricuspid aortic valve 746.89
- Stenosis (cicatricial) - see also Stricture
heart valve (acquired) - see also Endocarditis
valve (cardiac) (heart) (see also Endocarditis) 424.90
- Stricture (see also Stenosis) 799.89

heart - see also Disease, heart
- Supernumerary (congenital)
aortic cusps 746.89
- Syndrome - see also Disease
Brugada 746.89
- Undeveloped, undevelopment - see also Hypoplasia
heart 746.89
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 746.89 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2013 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.
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