2013 ICD-9-CM Diagnosis Code 742.3 : Congenital hydrocephalus

Hydrocephalus, absence of the cerebellar vermis, and posterior fossa cyst continuous with the fourth ventricle are the main characteristics of this syndrome. About 4% of all cases of hydrocephalus are complicated by DWS. Associated disorders may include Aase-Smith syndrome 1, Aicardi, Coffin-Siris, cryptophthalmos, Ehlers-Danlos, Ellis-van Creveld, Jones syndrome, Joubert, Ruvalcaba-Myhre-Smith, Walker-Warburg, Meckel, Ritscher-Schinzel, and Veradi syndromes. Dandy-Walker syndrome associated with macrocephaly, facial anomalies, developmental delay, and brain stem dysgenesis inherited as an X-linked recessive trait was reported as a separate syndrome.
ICD-9-CM 742.3 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.

742.3 Excludes

Applies To

Convert 742.3 to ICD-10-CM

ICD-9-CM Volume 2 Index entries containing back-references to 742.3:

Absence (organ or part) (complete or partial)
- skull bone 756.0
  - with
    - anencephalus 740.0
    - encephalocele 742.0
    - hydrocephalus 742.3
      - with spina bifida (see also Spina bifida) 741.0
    - microcephalus 742.1
Agenesis - see also Absence, by site, congenital
- skull (bone) 756.0
  - with
    - anencephalus 740.0
    - encephalocele 742.0
    - hydrocephalus 742.3
      - with spina bifida (see also Spina bifida) 741.0
    - microcephalus 742.1
Anomaly, anomalous (congenital) (unspecified type) 759.9
- aqueduct of Sylvius 742.3
  - with spina bifida (see also Spina bifida) 741.0
- bone NEC 756.9
  - ankle 755.69
  - arm 755.50
  - chest 756.3
  - cranium 756.0
  - face 756.0
  - finger 755.50
  - foot 755.67
  - forearm 755.50
  - frontal 756.0
  - head 756.0
  - hip 755.63
  - leg 755.60
  - lumbosacral 756.10
  - nose 748.1
  - pelvic girdle 755.60
  - rachitic 756.4
  - rib 756.3
  - shoulder girdle 755.50
  - skull 756.0
    - with
      - anencephalus 740.0
      - encephalocele 742.0
      - hydrocephalus 742.3
        with spina bifida (see also Spina bifida) 741.0
      - microcephalus 742.1
  - toe 755.66
- skull (bone) 756.0
  - with
    - anencephalus 740.0
    - encephalocele 742.0
    - hydrocephalus 742.3
      - with spina bifida (see also Spina bifida) 741.0
    - microcephalus 742.1
- specified type NEC
  - adrenal (gland) 759.1
  - alimentary tract (complete) (partial) 751.8
    - lower 751.5
    - upper 750.8
  - ankle 755.69
  - anus, anal (canal) 751.5
  - aorta, aortic 747.29
    - arch 747.21
  - appendix 751.5
  - arm 755.59
  - artery (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60
    - brain 747.81
    - coronary 746.85
    - eye 743.58
    - pulmonary 747.39
    - retinal 743.58
    - umbilical 747.5
  - auditory canal 744.29
    - causing impairment of hearing 744.02
  - bile duct or passage 751.69
  - bladder 753.8
    - neck 753.8
  - bone(s) 756.9
    - arm 755.59
    - face 756.0
    - leg 755.69
    - pelvic girdle 755.69
    - shoulder girdle 755.59
    - skull 756.0
      - with
        anencephalus 740.0
        encephalocele 742.0
        hydrocephalus 742.3
        with spina bifida (see also Spina bifida) 741.0
        microcephalus 742.1
  - brain 742.4
  - breast 757.6
  - broad ligament 752.19
  - bronchus 748.3
  - canal of Nuck 752.89
  - cardiac septal closure 745.8
  - carpus 755.59
  - cartilaginous 756.9
  - cecum 751.5
  - cervix 752.49
  - chest (wall) 756.3
  - chin 744.89
  - ciliary body 743.46
  - circulatory system 747.89
  - clavicle 755.51
  - clitoris 752.49
  - coccyx 756.19
  - colon 751.5
  - common duct 751.69
  - connective tissue 756.89
  - cricoid cartilage 748.3
  - cystic duct 751.69
  - diaphragm 756.6
  - digestive organ(s) or tract 751.8
    - lower 751.5
    - upper 750.8
  - duodenum 751.5
  - ear 744.29
    - auricle 744.29
      - causing impairment of hearing 744.02
    - causing impairment of hearing 744.09
    - inner (causing impairment of hearing) 744.05
    - middle, except ossicles 744.03
      - ossicles 744.04
  - ejaculatory duct 752.89
  - endocrine 759.2
  - epiglottis 748.3
  - esophagus 750.4
  - Eustachian tube 744.24
  - eye 743.8
    - lid 743.63
    - muscle 743.69
  - face 744.89
    - bone(s) 756.0
  - fallopian tube 752.19
  - fascia 756.89
  - femur 755.69
  - fibula 755.69
  - finger 755.59
  - foot 755.67
  - fovea centralis 743.55
  - gallbladder 751.69
  - Gartner's duct 752.89
  - gastrointestinal tract 751.8
  - genitalia, genital organ(s)
    - female 752.89
      - external 752.49
      - internal NEC 752.89
    - male 752.89
      - penis 752.69
      - scrotal transposition 752.81
  - genitourinary tract NEC 752.89
  - glottis 748.3
  - hair 757.4
  - hand 755.59
  - heart 746.89
    - valve NEC 746.89
      - pulmonary 746.09
  - hepatic duct 751.69
  - hydatid of Morgagni 752.89
  - hymen 752.49
  - integument 757.8
  - intestine (large) (small) 751.5
    - fixational type 751.4
  - iris 743.46
  - jejunum 751.5
  - joint 755.8
  - kidney 753.3
  - knee 755.64
  - labium (majus) (minus) 752.49
  - labyrinth, membranous 744.05
  - larynx 748.3
  - leg 755.69
  - lens 743.39
  - limb, except reduction deformity 755.8
    - lower 755.69
      - reduction deformity (see also Deformity, reduction, lower limb) 755.30
    - upper 755.59
      - reduction deformity (see also Deformity, reduction, upper limb) 755.20
  - lip 750.26
  - liver 751.69
  - lung (fissure) (lobe) 748.69
  - meatus urinarius 753.8
  - metacarpus 755.59
  - mouth 750.26
  - Müllerian
    - cervix 752.49
    - uterus 752.39
    - vagina 752.49
  - muscle 756.89
    - eye 743.69
  - musculoskeletal system, except limbs 756.9
  - nail 757.5
  - neck 744.89
  - nerve 742.8
    - acoustic 742.8
    - optic 742.8
  - nervous system 742.8
  - nipple 757.6
  - nose 748.1
  - organ NEC 759.89
    - of Corti 744.05
  - osseous meatus (ear) 744.03
  - ovary 752.0
  - oviduct 752.19
  - pancreas 751.7
  - parathyroid 759.2
  - patella 755.64
  - pelvic girdle 755.69
  - penis 752.69
  - pericardium 746.89
  - peripheral vascular system NEC (see also Anomaly, peripheral vascular system) 747.60
  - pharynx 750.29
  - pituitary 759.2
  - prostate 752.89
  - radius 755.59
  - rectum 751.5
  - respiratory system 748.8
  - rib 756.3
  - round ligament 752.89
  - sacrum 756.19
  - salivary duct or gland 750.26
  - scapula 755.59
  - sclera 743.47
  - scrotum 752.89
    - transposition 752.81
  - seminal duct or tract 752.89
  - shoulder girdle 755.59
  - site NEC 759.89
  - skin 757.39
  - skull (bone(s)) 756.0
    - with
      - anencephalus 740.0
      - encephalocele 742.0
      - hydrocephalus 742.3
        with spina bifida (see also Spina bifida) 741.0
      - microcephalus 742.1
  - specified organ or site NEC 759.89
  - spermatic cord 752.89
  - spinal cord 742.59
  - spine 756.19
  - spleen 759.0
  - sternum 756.3
  - stomach 750.7
  - tarsus 755.67
  - tendon 756.89
  - testis 752.89
  - thorax (wall) 756.3
  - thymus 759.2
  - thyroid (gland) 759.2
    - cartilage 748.3
  - tibia 755.69
  - toe 755.66
  - tongue 750.19
  - trachea (cartilage) 748.3
  - ulna 755.59
  - urachus 753.7
  - ureter 753.4
    - obstructive 753.29
  - urethra 753.8
    - obstructive 753.6
  - urinary tract 753.8
  - uterus (Müllerian) 752.39
  - uvula 750.26
  - vagina 752.49
  - vascular NEC (see also Anomaly, peripheral vascular system) 747.60
    - brain 747.81
  - vas deferens 752.89
  - vein(s) (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60
    - brain 747.81
    - great 747.49
    - portal 747.49
    - pulmonary 747.49
  - vena cava (inferior) (superior) 747.49
  - vertebra 756.19
  - vulva 752.49
Atresia, atretic (congenital) 759.89
- aqueduct of Sylvius 742.3
  - with spina bifida (see also Spina bifida) 741.0
- foramen of
  - Luschka 742.3
    - with spina bifida (see also Spina bifida) 741.0
  - Magendie 742.3
    - with spina bifida (see also Spina bifida) 741.0
Block
- foramen Magendie (acquired) 331.3
  - congenital 742.3
    - with spina bifida (see also Spina bifida) 741.0
Cyst (mucus) (retention) (serous) (simple)
- Dandy-Walker 742.3
  - with spina bifida (see also Spina bifida) 741.0
Dandy-Walker deformity or syndrome (atresia, foramen of Magendie) 742.3
- with spina bifida (see also Spina bifida) 741.0
Deformity 738.9
- Dandy-Walker 742.3
  - with spina bifida (see also Spina bifida) 741.0
- skull (acquired) 738.19
  - congenital 756.0
    - with
      - anencephalus 740.0
      - encephalocele 742.0
      - hydrocephalus 742.3
        with spina bifida (see also Spina bifida) 741.0
      - microcephalus 742.1
    - due to intrauterine malposition and pressure 754.0
Distortion (congenital)
- skull bone(s) 756.0
  - with
    - anencephalus 740.0
    - encephalocele 742.0
    - hydrocephalus 742.3
      - with spina bifida (see also Spina bifida) 741.0
    - microcephalus 742.1
Forking, aqueduct of Sylvius 742.3
- with spina bifida (see also Spina bifida) 741.0
Hydrancephaly 742.3
- with spina bifida (see also Spina bifida) 741.0
Hydranencephaly 742.3
- with spina bifida (see also Spina bifida) 741.0
Hydrocephalus (acquired) (external) (internal) (malignant) (noncommunicating) (obstructive) (recurrent) 331.4
- aqueduct of Sylvius stricture 742.3
  - with spina bifida (see also Spina bifida) 741.0
- chronic 742.3
  - with spina bifida (see also Spina bifida) 741.0
- congenital (external) (internal) 742.3
  - with spina bifida (see also Spina bifida) 741.0
- due to
  - stricture of aqueduct of Sylvius 742.3
    - with spina bifida (see also Spina bifida) 741.0
  - toxoplasmosis (congenital) 771.2
- foramen Magendie block (acquired) 331.3
  - congenital 742.3
    - with spina bifida (see also Spina bifida) 741.0
- newborn 742.3
  - with spina bifida (see also Spina bifida) 741.0
Hypoplasia, hypoplasis 759.89
- skull (bone) 756.0
  - with
    - anencephalus 740.0
    - encephalocele 742.0
    - hydrocephalus 742.3
      - with spina bifida (see also Spina bifida) 741.0
    - microcephalus 742.1
Imperfect
- closure (congenital)
  - alimentary tract NEC 751.8
    - lower 751.5
    - upper 750.8
  - atrioventricular ostium 745.69
  - atrium (secundum) 745.5
    - primum 745.61
  - branchial cleft or sinus 744.41
  - choroid 743.59
  - cricoid cartilage 748.3
  - cusps, heart valve NEC 746.89
    - pulmonary 746.09
  - ductus
    - arteriosus 747.0
    - Botalli 747.0
  - ear drum 744.29
    - causing impairment of hearing 744.03
  - endocardial cushion 745.60
  - epiglottis 748.3
  - esophagus with communication to bronchus or trachea 750.3
  - Eustachian valve 746.89
  - eyelid 743.62
  - face, facial (see also Cleft, lip) 749.10
  - foramen
    - Botalli 745.5
    - ovale 745.5
  - genitalia, genital organ(s) or system
    - female 752.89
      - external 752.49
      - internal NEC 752.89
      - uterus 752.39
    - male 752.89
      - penis 752.69
  - glottis 748.3
  - heart valve (cusps) NEC 746.89
  - interatrial ostium or septum 745.5
  - interauricular ostium or septum 745.5
  - interventricular ostium or septum 745.4
  - iris 743.46
  - kidney 753.3
  - larynx 748.3
  - lens 743.36
  - lip (see also Cleft, lip) 749.10
  - nasal septum or sinus 748.1
  - nose 748.1
  - omphalomesenteric duct 751.0
  - optic nerve entry 743.57
  - organ or site NEC - see Anomaly, specified type, by site
  - ostium
    - interatrial 745.5
    - interauricular 745.5
    - interventricular 745.4
  - palate (see also Cleft, palate) 749.00
  - preauricular sinus 744.46
  - retina 743.56
  - roof of orbit 742.0
  - sclera 743.47
  - septum
    - aortic 745.0
    - aorticopulmonary 745.0
    - atrial (secundum) 745.5
      - primum 745.61
    - between aorta and pulmonary artery 745.0
    - heart 745.9
    - interatrial (secundum) 745.5
      - primum 745.61
    - interauricular (secundum) 745.5
      - primum 745.61
    - interventricular 745.4
      - with pulmonary stenosis or atresia, dextraposition of aorta, and hypertrophy of right ventricle 745.2
      - in tetralogy of Fallot 745.2
    - nasal 748.1
    - ventricular 745.4
      - with pulmonary stenosis or atresia, dextraposition of aorta, and hypertrophy of right ventricle 745.2
      - in tetralogy of Fallot 745.2
  - skull 756.0
    - with
      - anencephalus 740.0
      - encephalocele 742.0
      - hydrocephalus 742.3
        with spina bifida (see also Spina bifida) 741.0
      - microcephalus 742.1
  - spine (with meningocele) (see also Spina bifida) 741.90
  - thyroid cartilage 748.3
  - trachea 748.3
  - tympanic membrane 744.29
    - causing impairment of hearing 744.03
  - uterus (with communication to bladder, intestine, or rectum) 752.39
  - uvula 749.02
    - with cleft lip (see also Cleft, palate, with cleft lip) 749.20
  - vitelline duct 751.0
Obstruction, obstructed, obstructive
- aqueduct of Sylvius 331.4
  - congenital 742.3
    - with spina bifida (see also Spina bifida) 741.0
- foramen of Monro (congenital) 742.3
  - with spina bifida (see also Spina bifida) 741.0
Occlusion
- aqueduct of Sylvius 331.4
  - congenital 742.3
    - with spina bifida (see also Spina bifida) 741.0
Septum, septate (congenital) - see also Anomaly, specified type NEC
- aqueduct of Sylvius 742.3
  - with spina bifida (see also Spina bifida) 741.0
Stenosis (cicatricial) - see also Stricture
- aqueduct of Sylvius (congenital) 742.3
  - with spina bifida (see also Spina bifida) 741.0
  - acquired 331.4
Stricture (see also Stenosis) 799.89
- aqueduct of Sylvius (congenital) 742.3
  - with spina bifida (see also Spina bifida) 741.0
  - acquired 331.4
Syndrome - see also Disease
- Dandy-Walker (atresia, foramen of Magendie) 742.3
  - with spina bifida (see also Spina bifida) 741.0

742.2

ICD9Data.com

742.4

ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 742.3 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2013 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.

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