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2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Congenital Anomalies 740-759 > Other And Unspecified Congenital Anomalies 759.* >

2006 ICD-9-CM Diagnosis 759.3

Situs inversus

View the most recent version of ICD-9-CM 759.3

  • A laterization defect marked by asymmetric position of visceral organs usually occurring as a component of a wide variety of abnormalities. Transposition may be complete, with the heart, lungs and all abdominal organs reversed, or incomplete, manifesting itself as a simple reversal of the stomach or spleen. Associated malformations are variable and may include tetralogy of Fallot, transposition of great vessels, pulmonary valve stenosis, ventricular and atrial septal defects, asplenia-polysplenia. and other defects.
  • Lateral transposition of the viscera of the thorax and abdomen. It has a familial pattern and consanguineous parents have been reported.
  • 759.3 is a specific code that can be used to specify a diagnosis
  • 759.3 contains 16 index entries
  • View the ICD-9-CM Volume 1 759.* hierarchy

Alternate Terminology

  • Situs inversus or transversus:
    • abdominalis
    • thoracis
  • Transposition of viscera:
    • abdominal
    • thoracic

759.3 Excludes

  • dextrocardia without mention of complete transposition (746.87)

 Index entries containing 759.3:

Dextrocardia (corrected) (false) (isolated) (secondary) (true) 746.87
  • with
    • complete transposition of viscera 759.3
      • situs inversus 759.3
      Kartagener's syndrome or triad (sinusitis, bronchiectasis, situs inversus) 759.3
        Levocardia (isolated) 746.87
        • with situs inversus 759.3
          Malposition
          • congenital
            • heart 746.87
              • dextrocardia 746.87
                • with complete transposition of viscera 759.3
            Sinusitis-bronchiectasis-situs inversus (syndrome) (triad) 759.3
              Situs inversus or transversus 759.3
              • abdominalis 759.3
                • thoracis 759.3
                  Syndrome - see also Disease
                  • Kartagener's (sinusitis, bronchiectasis, situs inversus) 759.3
                    • sinusitis-bronchiectasis-situs inversus 759.3
                      Transposition (congenital) - see also Malposition, congenital
                      • abdominal viscera 759.3
                        • heart 746.87
                          • with complete transposition of viscera 759.3
                          • stomach 750.7
                            • with general transposition of viscera 759.3
                            • viscera (abdominal) (thoracic) 759.3
                              Triad
                              • Kartagener's 759.3