2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Congenital Anomalies 740-759 > Other Congenital Anomalies Of Heart 746.* > 2006 ICD-9-CM Diagnosis 746.01 Atresia of pulmonary valve congenital View the most recent version of ICD-9-CM 746.01 Congenital absence of the normal valvular orifice into the pulmonary artery. This condition is characterized by cardiomegaly, reduced pulmonary vascularity, and right ventricular atrophy. 746.01 is a specific code that can be used to specify a diagnosis 746.01 contains 10 index entries View the ICD-9-CM Volume 1 746.* hierarchy Alternate Terminology Congenital absence of pulmonary valve  Index entries containing 746.01: Absence (organ or part) (complete or partial) pulmonary valve (congenital) 746.01 Agenesis - see also Absence, by site, congenital heart 746.89 valve NEC 746.89 pulmonary 746.01 Anomaly, anomalous (congenital) (unspecified type) 759.9 heart 746.9 valve NEC 746.9 pulmonary 746.00 atresia 746.01 pulmonary 748.60 valve 746.00 atresia 746.01 Atresia, atretic (congenital) 759.89 cardiac valve 746.89 pulmonary 746.01 heart valve NEC 746.89 pulmonary 746.01 pulmonary (artery) 747.3 valve 746.01 pulmonic 746.01 Hypoplasia, hypoplasis 759.89 heart 746.89 valve NEC 746.89 pulmonary 746.01 pulmonary 748.5 valve 746.01