2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Congenital Anomalies 740-759 > Other Congenital Musculoskeletal Anomalies 756.* > 2006 ICD-9-CM Diagnosis 756.0 Congenital anomalies of skull and face bones View the most recent version of ICD-9-CM 756.0 Premature closure of one or more sutures of the skull. An autosomal dominant disorder characterized by acrocephaly, exophthalmos, hypertelorism, strabismus, parrot-beaked nose, and hypoplastic maxilla with relative mandibular prognathism. Abnormal increase in the interorbital distance due to overdevelopment of the lesser wings of the sphenoid. A developmental deformity of the occipital bone and upper end of the cervical spine, in which the latter appears to have pushed the floor of the occipital bone upward. 756.0 is a specific code that can be used to specify a diagnosis 756.0 contains 116 index entries View the ICD-9-CM Volume 1 756.* hierarchy Alternate Terminology Absence of skull bones Acrocephaly Congenital deformity of forehead Craniosynostosis Crouzon's disease Hypertelorism Imperfect fusion of skull Oxycephaly Platybasia Premature closure of cranial sutures Tower skull Trigonocephaly 756.0 Excludes acrocephalosyndactyly [Apert's syndrome] (755.55) dentofacial anomalies (524.0-524.9) skull defects associated with brain anomalies, such as: anencephalus (740.0) encephalocele (742.0) hydrocephalus (742.3) microcephalus (742.1)  Index entries containing 756.0: Abnormal, abnormality, abnormalities - see also Anomaly shape head (see also Anomaly, skull) 756.0 size head (see also Anomaly, skull) 756.0 Absence (organ or part) (complete or partial) bone (congenital) NEC 756.9 skull 756.0 calvarium, calvaria (skull) 756.0 face bones NEC 756.0 skull bone 756.0 with anencephalus 740.0 encephalocele 742.0 hydrocephalus 742.3 with spina bifida (see also Spina bifida) 741.0 microcephalus 742.1 Accessory (congenital) face bone(s) 756.0 frontonasal process 756.0 Acrobrachycephaly 756.0 Acrocephaly 756.0 Agenesis - see also Absence, by site, congenital face bones NEC 756.0 skull (bone) 756.0 with anencephalus 740.0 encephalocele 742.0 hydrocephalus 742.3 with spina bifida (see also Spina bifida) 741.0 microcephalus 742.1 Anomaly, anomalous (congenital) (unspecified type) 759.9 bone NEC 756.9 cranium 756.0 face 756.0 frontal 756.0 head 756.0 skull 756.0 with anencephalus 740.0 encephalocele 742.0 hydrocephalus 742.3 with spina bifida (see also Spina bifida) 741.0 microcephalus 742.1 face (any part) 744.9 bone(s) 756.0 forehead (see also Anomaly, skull) 756.0 frontal bone (see also Anomaly, skull) 756.0 head (see also Anomaly, skull) 756.0 Pierre Robin 756.0 skull (bone) 756.0 with anencephalus 740.0 encephalocele 742.0 hydrocephalus 742.3 with spina bifida (see also Spina bifida) 741.0 microcephalus 742.1 specified type NEC bone(s) 756.9 face 756.0 skull 756.0 with anencephalus 740.0 encephalocele 742.0 hydrocephalus 742.3 with spina bifida (see also Spina bifida) 741.0 microcephalus 742.1 face 744.89 bone(s) 756.0 skull (bone(s)) 756.0 with anencephalus 740.0 encephalocele 742.0 hydrocephalus 742.3 with spina bifida (see also Spina bifida) 741.0 microcephalus 742.1 Bird face 756.0 Brachycephaly 756.0 Bulging fontanels (congenital) 756.0 Caput crepitus 756.0 Closure cranial sutures, premature 756.0 fontanelle, delayed 756.0 Craniofenestria (skull) 756.0 Craniolacunia (skull) 756.0 Cranioschisis 756.0 Craniostenosis 756.0 Craniosynostosis 756.0 Crepitus caput 756.0 Crouzon's disease (craniofacial dysostosis) 756.0 Deficiency, deficient craniofacial axis 756.0 Deficient - see also Deficiency craniofacial axis 756.0 Deformity 738.9 cranium (acquired) 738.19 congenital (see also Deformity, skull, congenital) 756.0 forehead (acquired) 738.19 congenital (see also Deformity, skull, congenital) 756.0 frontal bone (acquired) 738.19 congenital (see also Deformity, skull, congenital) 756.0 head (acquired) 738.10 congenital (see also Deformity, skull, congenital) 756.0 Pierre Robin (congenital) 756.0 skull (acquired) 738.19 congenital 756.0 with anencephalus 740.0 encephalocele 742.0 hydrocephalus 742.3 with spina bifida (see also Spina bifida) 741.0 microcephalus 742.1 due to intrauterine malposition and pressure 754.0 Delay, delayed closure - see also Fistula cranial suture 756.0 fontanel 756.0 Diastasis cranial bones 733.99 congenital 756.0 Dilatation fontanel 756.0 Disease, diseased - see also Syndrome Crouzon's (craniofacial dysostosis) 756.0 Friedreich's facial hemihypertrophy 756.0 Distortion (congenital) face bone(s) 756.0 skull bone(s) 756.0 with anencephalus 740.0 encephalocele 742.0 hydrocephalus 742.3 with spina bifida (see also Spina bifida) 741.0 microcephalus 742.1 Duplication - see also Accessory frontonasal process 756.0 Dysostosis craniofacial 756.0 mandibularis 756.0 mandibulofacial, incomplete 756.0 Dysplasia - see also Anomaly oculoauriculovertebral 756.0 Ecchordosis physaliphora 756.0 Franceschetti's syndrome (mandibulofacial dysostosis) 756.0 Fusion, fused (congenital) cranial sutures, premature 756.0 skull, imperfect 756.0 Goldenhar's syndrome (oculoauriculovertebral dysplasia) 756.0 Greig's syndrome (hypertelorism) 756.0 Hallermann-Streiff syndrome 756.0 Hemihypertrophy (congenital) 759.89 cranial 756.0 Hyperostosis 733.99 skull 733.3 congenital 756.0 Hypertelorism 756.0 orbit, orbital 376.41 Hypoplasia, hypoplasis 759.89 bone NEC 756.9 face 756.0 malar 756.0 skull (see also Hypoplasia, skull) 756.0 face 744.89 bone(s) 756.0 skull (bone) 756.0 with anencephalus 740.0 encephalocele 742.0 hydrocephalus 742.3 with spina bifida (see also Spina bifida) 741.0 microcephalus 742.1 Idiot, idiocy (congenital) 318.2 oxycephalic 756.0 Imperfect closure (congenital) skull 756.0 with anencephalus 740.0 encephalocele 742.0 hydrocephalus 742.3 with spina bifida (see also Spina bifida) 741.0 microcephalus 742.1 Impression, basilar 756.0 Invagination basilar 756.0 Lacunar skull 756.0 Macrocephalia, macrocephaly 756.0 Maldevelopment - see also Anomaly, by site mastoid process 756.0 Megalocephalus, megalocephaly NEC 756.0 Nager-de Reynier syndrome (dysostosis mandibularis) 756.0 Oculoauriculovertebral dysplasia 756.0 Ossification fontanel defective or delayed 756.0 premature 756.0 Oxycephaly, oxycephalic 756.0 syphilitic, congenital 090.0 Pierre Robin deformity or syndrome (congenital) 756.0 Platybasia 756.0 Premature - see also condition closure cranial suture 756.0 fontanel 756.0 Robin's syndrome 756.0 Scaphocephaly 756.0 Stenocephaly 756.0 Sunken fontanels 756.0 Syndrome - see also Disease eyelid-malar-mandible 756.0 first arch 756.0 Franceschetti's (mandibulofacial dysostosis) 756.0 Goldenhar's (oculoauriculovertebral dysplasia) 756.0 Greig's (hypertelorism) 756.0 Hallermann-Strieff 756.0 incomplete mandibulofacial 756.0 mandibulofacial dysostosis 756.0 micrognathia-glossoptosis 756.0 Nager-de Reynier (dysostosis mandibularis) 756.0 OAV (oculoauriculovertebral dysplasia) 756.0 Pierre Robin 756.0 Robin's 756.0 Treacher Collins' (incomplete mandibulofacial dysostosis) 756.0 Tower skull 756.0 with exophthalmos 756.0 Treacher Collins' syndrome (incomplete facial dysostosis) 756.0 Trigonocephaly 756.0 Turricephaly 756.0