2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Diseases Of The Nervous System And Sense Organs 320-389 > Hereditary And Degenerative Diseases Of The Central Nervous System 330-338 > Other Extrapyramidal Disease And Abnormal Movement Disorders 333.* > 2006 ICD-9-CM Diagnosis 333.2 Myoclonus View the most recent version of ICD-9-CM 333.2 A heterogeneous group of primarily familial disorders characterized by myoclonic seizures, tonic-clonic seizures, ataxia, progressive intellectual deterioration, and neuronal degeneration. These include LAFORA DISEASE; MERRF SYNDROME; NEURONAL CEROID-LIPOFUSCINOSIS; sialidosis (see MUCOLIPIDOSES), and UNVERRICHT-LUNDBORG SYNDROME. An autosomal recessive condition characterized by recurrent myoclonic and generalized seizures, ATAXIA, slowly progressive intellectual deterioration, dysarthria, and intention tremor. Myoclonic seizures are severe and continuous, and tend to be triggered by movement, stress, and sensory stimuli. The age of onset is between 8 and 13 years, and the condition is relatively frequent in the Baltic region, especially Finland. Involuntary shock-like contractions, irregular in rhythm and amplitude, followed by relaxation, of a muscle or a group of muscles. This condition may be a feature of some CENTRAL NERVOUS SYSTEMS DISEASES (e.g., EPILEPSY, MYOCLONIC). Nocturnal myoclonus may represent a normal physiologic event or occur as the principal feature of the NOCTURNAL MYOCLONUS SYNDROME. (From Adams et al., Principles of Neurology, 6th ed, pp102-3). 333.2 is a specific code that can be used to specify a diagnosis 333.2 contains 22 index entries View the ICD-9-CM Volume 1 333.* hierarchy Alternate Terminology Familial essential myoclonus Progressive myoclonic epilepsy Unverricht-Lundborg disease  Index entries containing 333.2: Convulsions (idiopathic) 780.39 myoclonic 333.2 Disease, diseased - see also Syndrome Friedreich's myoclonia 333.2 Lafora's 333.2 Unverricht (-Lundborg) 333.2 Epilepsy, epileptic (idiopathic) 345.9 myoclonus, myoclonic 345.1 progressive (familial) 333.2 progressive myoclonic (familial) 333.2 unverricht (-Lundborg) (familial myoclonic) 333.2 Friedreich's disease 333.2 combined systemic 334.0 myoclonia 333.2 Jerks, myoclonic 333.2 Lafora's disease 333.2 Myoclonia (essential) 333.2 epileptica 333.2 Friedrich's 333.2 massive 333.2 Myoclonic epilepsy, familial (progressive) 333.2 jerks 333.2 Myoclonus (familial essential) (multifocal) (simplex) 333.2 with epilepsy and with ragged red fibers (MERRF syndrome) 277.87 facial 351.8 massive (infantile) 333.2 pharyngeal 478.29 Paramyoclonus multiplex 333.2 Syndrome - see also Disease Unverricht (-Lundborg) 333.2 Unverricht (-Lundborg) disease, syndrome, or epilepsy 333.2