2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Congenital Anomalies 740-759 > ICD-9-CM Diagnosis 756 Other congenital musculoskeletal anomalies 756 is a non-specific code that cannot be used to specify a diagnosis ICD-9-CM Diagnosis 756.0 Congenital anomalies of skull and face bones Premature closure of one or more sutures of the skull. An autosomal dominant disorder characterized by acrocephaly, exophthalmos, hypertelorism, strabismus, parrot-beaked nose, and hypoplastic maxilla with relative mandibular prognathism. Abnormal increase in the interorbital distance due to overdevelopment of the lesser wings of the sphenoid. A developmental deformity of the occipital bone and upper end of the cervical spine, in which the latter appears to have pushed the floor of the occipital bone upward. 756.0 is a specific code that can be used to specify a diagnosis 756.0 contains 116 index entries ICD-9-CM Diagnosis 756.1 Congenital anomalies of spine 756.1 is a non-specific code that cannot be used to specify a diagnosis ICD-9-CM Diagnosis 756.10 Congenital anomaly of spine unspecified 756.10 is a specific code that can be used to specify a diagnosis 756.10 contains 15 index entries ICD-9-CM Diagnosis 756.11 Congenital spondylolysis lumbosacral region 756.11 is a specific code that can be used to specify a diagnosis 756.11 contains 10 index entries ICD-9-CM Diagnosis 756.12 Spondylolisthesis congenital 756.12 is a specific code that can be used to specify a diagnosis 756.12 contains 5 index entries ICD-9-CM Diagnosis 756.13 Absence of vertebra congenital 756.13 is a specific code that can be used to specify a diagnosis 756.13 contains 13 index entries ICD-9-CM Diagnosis 756.14 Hemivertebra 756.14 is a specific code that can be used to specify a diagnosis 756.14 contains 2 index entries ICD-9-CM Diagnosis 756.15 Fusion of spine (vertebra) congenital 756.15 is a specific code that can be used to specify a diagnosis 756.15 contains 11 index entries ICD-9-CM Diagnosis 756.16 Klippel-feil syndrome A condition characterized by shortness of the neck resulting from reduction in the number of vertebrae or the fusion of multiple hemivertebrae into one osseous mass. The hairline is low and the motion of the neck is limited. 756.16 is a specific code that can be used to specify a diagnosis 756.16 contains 9 index entries ICD-9-CM Diagnosis 756.17 Spina bifida occulta A common congenital midline defect of fusion of the vertebral arch without protrusion of the spinal cord or meninges. The lesion is also covered by skin. L5 and S1 are the most common vertebrae involved. The condition may be associated with an overlying area of hyperpigmented skin, a dermal sinus, or an abnormal patch of hair. The majority of individuals with this malformation are asymptomatic although there is an increased incidence of tethered cord syndrome and lumbar SPONDYLOSIS. 756.17 is a specific code that can be used to specify a diagnosis 756.17 contains 1 index entry ICD-9-CM Diagnosis 756.19 Other congenital anomalies of spine 756.19 is a specific code that can be used to specify a diagnosis 756.19 contains 38 index entries ICD-9-CM Diagnosis 756.2 Cervical rib 756.2 is a specific code that can be used to specify a diagnosis 756.2 contains 9 index entries ICD-9-CM Diagnosis 756.3 Other congenital anomalies of ribs and sternum 756.3 is a specific code that can be used to specify a diagnosis 756.3 contains 40 index entries ICD-9-CM Diagnosis 756.4 Chondrodystrophy An autosomal dominant disorder that is the most frequent form of short-limb dwarfism. Affected individuals exhibit short stature caused by rhizomelic shortening of the limbs, characteristic facies with frontal bossing and mid-face hypoplasia, exaggerated lumbar lordosis, limitation of elbow extension, genu varum, and trident hand. Benign growths of cartilage in the metaphyses of several bones. 756.4 is a specific code that can be used to specify a diagnosis 756.4 contains 40 index entries ICD-9-CM Diagnosis 756.5 Congenital osteodystrophies 756.5 is a non-specific code that cannot be used to specify a diagnosis ICD-9-CM Diagnosis 756.50 Congenital osteodystrophy unspecified 756.50 is a specific code that can be used to specify a diagnosis 756.50 contains 6 index entries ICD-9-CM Diagnosis 756.51 Osteogenesis imperfecta Autosomal dominant COLLAGEN DISEASES resulting from defective biosynthesis of COLLAGEN TYPE I and characterized by brittle, osteoporotic, and easily fractured bones. It may also present with blue sclerae, loose joints, and imperfect dentin formation. There are four major types, I-IV. 756.51 is a specific code that can be used to specify a diagnosis 756.51 contains 27 index entries ICD-9-CM Diagnosis 756.52 Osteopetrosis Excessive formation of dense trabecular bone leading to pathological fractures, OSTEITIS, SPLENOMEGALY with infarct, ANEMIA, and extramedullary hemopoiesis (HEMATOPOIESIS, EXTRAMEDULLARY). 756.52 is a specific code that can be used to specify a diagnosis 756.52 contains 7 index entries ICD-9-CM Diagnosis 756.53 Osteopoikilosis An asymptomatic, autosomal dominant trait in which pea-sized sclerotic spots, prominent in the metaphyseal area, are accompanied by unique cutaneous lesions. These are yellowish papules or plaques with increased elastin content. 756.53 is a specific code that can be used to specify a diagnosis 756.53 contains 3 index entries ICD-9-CM Diagnosis 756.54 Polyostotic fibrous dysplasia of bone FIBROUS DYSPLASIA OF BONE affecting several or many bones. When associated with melanotic pigmentation of the skin and endocrine disorders, it is known as Albright's syndrome. 756.54 is a specific code that can be used to specify a diagnosis 756.54 contains 4 index entries ICD-9-CM Diagnosis 756.55 Chondroectodermal dysplasia Dwarfism occurring in association with defective development of skin, hair, and teeth, polydactyly, and defect of the cardiac septum. Chondrodysplasia of long bones affecting mainly the distal ends of extremities and resulting in short-limb dwarfism, hexadactyly of the fingers and less frequently the toes; ectodermal dysplasia with nail and hair abnormalities, and congenital heart defects. Associated abnormalities may include cryptorchidism, epispadias, talipes equinovalgus, and Dandy-Walker syndrome (absence of cerebellar vermis, hydrocephalus, and posterior fossa cyst continuous with the fourth ventricle). Some patients are retarded. The largest pedigree was observed in Old Order Amish in Lancaster County, Pennsylvania and some cases were reported in Australian Aborigines. 756.55 is a specific code that can be used to specify a diagnosis 756.55 contains 6 index entries ICD-9-CM Diagnosis 756.56 Multiple epiphyseal dysplasia 756.56 is a specific code that can be used to specify a diagnosis 756.56 contains 2 index entries ICD-9-CM Diagnosis 756.59 Other congenital osteodystrophies 756.59 is a specific code that can be used to specify a diagnosis 756.59 contains 49 index entries ICD-9-CM Diagnosis 756.6 Congenital anomalies of diaphragm A congenital abnormality characterized by the elevation of the DIAPHRAGM dome. It is the result of a thinned diaphragmatic muscle and injured PHRENIC NERVE, allowing the intra-abdominal viscera to push the diaphragm upward against the LUNG. 756.6 is a specific code that can be used to specify a diagnosis 756.6 contains 23 index entries ICD-9-CM Diagnosis 756.7 Congenital anomalies of abdominal wall 756.7 is a non-specific code that cannot be used to specify a diagnosis ICD-9-CM Diagnosis 756.70 Anomaly of abdominal wall unspecified 756.70 is a specific code that can be used to specify a diagnosis 756.70 contains 3 index entries ICD-9-CM Diagnosis 756.71 Prune belly syndrome A syndrome of hypoplasia or aplasia of the abdominal muscle, presenting a thin, loose, wrinkled and shriveled (prunelike) abdominal wall, with furrowlike umbilicus, and other anomalies, including persistent urachus, pigeon breast deformity, and a variety of gastrointestinal, cardiovascular, urogenital, and skeletal abnormalities. Prune belly syndrome may occur with or without pulmonic stenosis, deafness, and mental retardation. Distention of the bladder and urethra in utero is considered as a possible cause of abdominal overdistention. A syndrome characterized by abdominal wall musculature deficiency, cryptorchism, and urinary tract abnormalities. The syndrome derives its name from its characteristic distended abdomen with wrinkled skin. 756.71 is a specific code that can be used to specify a diagnosis 756.71 contains 7 index entries ICD-9-CM Diagnosis 756.79 Other congenital anomalies of abdominal wall A congenital defect with major fissure in the ABDOMINAL WALL lateral to, but not at, the UMBILICUS. This results in the extrusion of VISCERA. Unlike OMPHALOCELE, herniated structures in gastroschisis are not covered by a sac or PERITONEUM. A congenital defect with major fissure in the ABDOMINAL WALL at the UMBILICUS resulting in the extrusion of VISCERA through the UMBILICUS. Unlike GASTROSCHISIS, omphalocele is covered with PERITONEUM but without overlying SKIN. 756.79 is a specific code that can be used to specify a diagnosis 756.79 contains 13 index entries ICD-9-CM Diagnosis 756.8 Other specified congenital anomalies of muscle tendon fascia and connective tissue 756.8 is a non-specific code that cannot be used to specify a diagnosis ICD-9-CM Diagnosis 756.81 Congenital absence of muscle and tendon 756.81 is a specific code that can be used to specify a diagnosis 756.81 contains 6 index entries ICD-9-CM Diagnosis 756.82 Accessory muscle 756.82 is a specific code that can be used to specify a diagnosis 756.82 contains 2 index entries ICD-9-CM Diagnosis 756.83 Ehlers-danlos syndrome A heterogeneous group of inherited COLLAGEN DISEASES. The most common manifestations of Ehlers-Danlos Syndrome are hyperextensible skin and joints, skin fragility and reduced wound healing capability. 756.83 is a specific code that can be used to specify a diagnosis 756.83 contains 13 index entries ICD-9-CM Diagnosis 756.89 Other specified congenital anomalies of muscle tendon fascia and connective tissue 756.89 is a specific code that can be used to specify a diagnosis 756.89 contains 55 index entries ICD-9-CM Diagnosis 756.9 Other and unspecified congenital anomalies of musculoskeletal system 756.9 is a specific code that can be used to specify a diagnosis 756.9 contains 47 index entries