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2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Congenital Anomalies 740-759 > Congenital Anomalies Of The Integument 757.* >

2006 ICD-9-CM Diagnosis 757.39

Other specified congenital anomalies of skin

View the most recent version of ICD-9-CM 757.39

  • Group of genetically determined disorders characterized by the blistering of skin and mucosae. There are four major forms: acquired, simple, junctional, and dystrophic. Each of the latter three has several varieties.
  • 757.39 is a specific code that can be used to specify a diagnosis
  • 757.39 contains 119 index entries
  • View the ICD-9-CM Volume 1 757.* hierarchy

Alternate Terminology

  • Accessory skin tags, congenital
  • Congenital scar
  • Epidermolysis bullosa
  • Keratoderma (congenital)

757.39 Excludes


 Index entries containing 757.39:

Absence (organ or part) (complete or partial)
  • skin (congenital) 757.39
    Acantholysis 701.8
    • bullosa 757.39
      Acanthosis (acquired) (nigricans) 701.2
      • benign (congenital) 757.39
        • congenital 757.39
          Accessory (congenital)
          • skin tags 757.39
            Acrokeratosis verruciformis 757.39
              Acropachyderma 757.39
                Anomaly, anomalous (congenital) (unspecified type) 759.9
                • skin (appendage) 757.9
                  • specified type NEC 757.39
                  • specified type NEC
                    • skin 757.39
                    Aplasia - see also Agenesis
                    • skin (congenital) 757.39
                      Audry's syndrome (acropachyderma) 757.39
                        Bloom (-Machacek) (-Torre) syndrome 757.39
                          Brugsch's syndrome (acropachyderma) 757.39
                            Chalazoderma 757.39
                              Cicatrix (adherent) (contracted) (painful) (vicious) 709.2
                              • congenital 757.39
                                Cockayne-Weber syndrome (epidermolysis bullosa) 757.39
                                  Cutis - see also condition
                                  • verticis gyrata 757.39
                                  Darier's disease (congenital) (keratosis follicularis) 757.39
                                  • due to vitamin A deficiency 264.8
                                    • meaning erythema annulare centrifugum 695.0
                                      Dermatolysis (congenital) (exfoliativa) 757.39Disease, diseased - see also Syndrome
                                      • Darier's (congenital) (keratosis follicularis) 757.39
                                        • erythema annulare centrifugum 695.0
                                          • vitamin A deficiency 264.8
                                          • Goldscheider's (epidermolysis bullosa) 757.39
                                            • Gougerot-Hailey-Hailey (benign familial chronic pemphigus) 757.39
                                              • Hailey-Hailey (benign familial chronic pemphigus) 757.39
                                                • Köbner's (epidermolysis bullosa) 757.39
                                                  • Marie-Bamberger (hypertrophic pulmonary osteoarthropathy) (secondary) 731.2
                                                    • primary or idiopathic (acropachyderma) 757.39
                                                    • Meleda 757.39
                                                      • Mibelli's 757.39
                                                        • Mljet (mal de Meleda) 757.39
                                                          • White's (congenital) (keratosis follicularis) 757.39
                                                            Dyskeratosis (see also Keratosis) 701.1
                                                            • bullosa hereditaria 757.39
                                                              • congenital 757.39
                                                                • follicularis 757.39
                                                                  • vitamin A deficiency 264.8
                                                                  Elastoma 757.39
                                                                  • juvenile 757.39
                                                                    • Miescher's (elastosis perforans serpiginosa) 701.1
                                                                      Epidermolysis
                                                                      • bullosa 757.39
                                                                        Friedrich-Erb-Arnold syndrome (acropachyderma) 757.39
                                                                          Goldscheider's disease (epidermolysis bullosa) 757.39
                                                                            Goltz-Gorlin syndrome (dermal hypoplasia) 757.39
                                                                              Gougerot-Hailey-Hailey disease (benign familial chronic pemphigus) 757.39
                                                                                Gyrate scalp 757.39
                                                                                  Hailey-Hailey disease (benign familial chronic pemphigus) 757.39
                                                                                    Hydromphalus (congenital) (since birth) 757.39
                                                                                      Hyperkeratosis (see also Keratosis) 701.1
                                                                                      • congenital 757.39
                                                                                        • eccentrica 757.39
                                                                                          • figurata centrifuga atrophica 757.39
                                                                                            • follicularis 757.39
                                                                                            Hypoplasia, hypoplasis 759.89
                                                                                            • dermal, focal (Goltz) 757.39
                                                                                              • focal dermal 757.39
                                                                                                • skin 757.39
                                                                                                  Ichthyosis (congenita) 757.1
                                                                                                  • hystrix 757.39
                                                                                                    • palmaris and plantaris 757.39
                                                                                                      Keratoderma, keratodermia (congenital) (palmaris et plantaris) (symmetrical) 757.39Keratolysis exfoliativa (congenital) 757.39
                                                                                                      • acquired 695.89
                                                                                                        • neonatorum 757.39
                                                                                                          Keratoma 701.1
                                                                                                          • congenital 757.39
                                                                                                            • palmaris et plantaris hereditarium 757.39
                                                                                                              Keratosis 701.1
                                                                                                              • congenital (any type) 757.39
                                                                                                                • follicularis 757.39
                                                                                                                  • acquired 701.1
                                                                                                                    • congenital (acneiformis) (Siemens') 757.39
                                                                                                                      • spinulosa (decalvans) 757.39
                                                                                                                        • vitamin A deficiency 264.8
                                                                                                                        • nigricans 701.2
                                                                                                                          • congenital 757.39
                                                                                                                          • palmaris et plantaris (symmetrical) 757.39
                                                                                                                            • pilaris 757.39
                                                                                                                            • suprafollicularis 757.39
                                                                                                                              • vegetans 757.39
                                                                                                                                Köbner's disease (epidermolysis bullosa) 757.39
                                                                                                                                  Lichen 697.9
                                                                                                                                  • pilaris 757.39
                                                                                                                                  • spinulosus 757.39
                                                                                                                                  Mal
                                                                                                                                  • de Meleda 757.39
                                                                                                                                    Marie-Bamberger disease or syndrome (hypertrophic) (pulmonary) (secondary) 731.2
                                                                                                                                    • idiopathic (acropachyderma) 757.39
                                                                                                                                      • primary (acropachyderma) 757.39
                                                                                                                                        Megalia, cutis et ossium 757.39
                                                                                                                                          Mibelli's disease 757.39
                                                                                                                                            Mljet disease (mal de Meleda) 757.39
                                                                                                                                              Osteoarthropathy (see also Osteoarthrosis) 715.9
                                                                                                                                              • chronic idiopathic hypertrophic 757.39
                                                                                                                                                • familial idiopathic 757.39
                                                                                                                                                  • idiopathic hypertrophic 757.39
                                                                                                                                                    Osteosis
                                                                                                                                                    • acromegaloid 757.39
                                                                                                                                                      Pachydermatocele (congenital) 757.39Pachydermoperiostosis
                                                                                                                                                      • primary idiopathic 757.39
                                                                                                                                                        Pachyperiosteodermia
                                                                                                                                                        • primary or idiopathic 757.39
                                                                                                                                                          Pachyperiostosis
                                                                                                                                                          • primary or idiopathic 757.39
                                                                                                                                                            Particolored infant 757.39
                                                                                                                                                              Pemphigus 694.4
                                                                                                                                                              • benign 694.5
                                                                                                                                                                • chronic familial 757.39
                                                                                                                                                                • congenital, traumatic 757.39
                                                                                                                                                                  Pityriasis 696.5Porokeratosis 757.39
                                                                                                                                                                  • disseminated superficial actinic (DSAP) 692.75
                                                                                                                                                                    Pseudoxanthoma elasticum 757.39
                                                                                                                                                                      Psorospermosis 136.4
                                                                                                                                                                      • follicularis (vegetans) 757.39
                                                                                                                                                                        Roy (-Jutras) syndrome (acropachyderma) 757.39
                                                                                                                                                                          Sauriderma 757.39
                                                                                                                                                                            Scar, scarring (see also Cicatrix) 709.2
                                                                                                                                                                            • congenital 757.39
                                                                                                                                                                              Siemens' syndrome
                                                                                                                                                                              • keratosis follicularis spinulosa (decalvans) 757.39
                                                                                                                                                                                Syndrome - see also Disease
                                                                                                                                                                                • Audry's (acropachyderma) 757.39
                                                                                                                                                                                  • Bloom (-Machacek) (-Torre) 757.39
                                                                                                                                                                                    • Brugsch's (acropachyderma) 757.39
                                                                                                                                                                                      • Cockayne-Weber (epidermolysis bullosa) 757.39
                                                                                                                                                                                        • FDH (focal dermal hypoplasia) 757.39
                                                                                                                                                                                          • Friedrich-Erb-Arnold (acropachyderma) 757.39
                                                                                                                                                                                            • Goltz-Gorlin (dermal hypoplasia) 757.39
                                                                                                                                                                                              • Marie's (acromegaly) 253.0
                                                                                                                                                                                                • primary or idiopathic (acropachyderma) 757.39
                                                                                                                                                                                                • osteodermopathic hyperostosis 757.39
                                                                                                                                                                                                  • Proteus (dermal hypoplasia) 757.39
                                                                                                                                                                                                    • Roy (-Jutras) (acropachyderma) 757.39
                                                                                                                                                                                                      • Siemens'
                                                                                                                                                                                                        • keratosis follicularis spinulosa (decalvans) 757.39
                                                                                                                                                                                                        • Touraine-Solente-Golé (acropachyderma) 757.39
                                                                                                                                                                                                          • Uehlinger's (acropachyderma) 757.39
                                                                                                                                                                                                            • Weber-Cockayne (epidermolysis bullosa) 757.39
                                                                                                                                                                                                              Tag (hypertrophied skin) (infected) 701.9
                                                                                                                                                                                                              • skin 701.9
                                                                                                                                                                                                                • accessory 757.39
                                                                                                                                                                                                                  • congenital 757.39
                                                                                                                                                                                                                  Touraine-Solente-Golé syndrome (acropachyderma) 757.39
                                                                                                                                                                                                                    Tumor (M8000/1) - see also Neoplasm, by site, unspecified nature
                                                                                                                                                                                                                    • White-Darier 757.39
                                                                                                                                                                                                                      Tylosis 700
                                                                                                                                                                                                                      • palmaris et plantaris 757.39
                                                                                                                                                                                                                        Uehlinger's syndrome (acropachyderma) 757.39
                                                                                                                                                                                                                          Urticaria 708.9
                                                                                                                                                                                                                          • perstans hemorrhagica 757.39
                                                                                                                                                                                                                            Weber-Cockayne syndrome (epidermolysis bullosa) 757.39
                                                                                                                                                                                                                              White's disease (congenital) (keratosis follicularis) 757.39
                                                                                                                                                                                                                                Xeroderma (congenital) 757.39