Specific code 2012 ICD-9-CM Diagnosis Code 282.3
Other hemolytic anemias due to enzyme deficiency
  • Short description: Enzyme defic anemia NEC.
  • ICD-9-CM 282.3 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 282.3 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
  • You are viewing the 2012 version of ICD-9-CM 282.3.
  • More recent version(s) of ICD-9-CM 282.3: 2013 2014.
Disease Synonyms
  • Anemia due to disorders of glycolytic enzymes
  • Anemia due to disorders of nucleotide metabolism
  • Anemia due to enzyme deficiency
  • Anemia due to enzyme disorder
  • Chronic non-spherocytic hemolytic anemia
  • Deficiency of pyruvate kinase
  • Fumarase deficiency
  • Hemolytic anemia due to enzyme deficiency
  • Hemolytic anemia due to hexokinase deficiency
  • Hemolytic anemia due to pyruvate kinase deficiency
  • Hemolytic anemia due to triose phosphate isomerase deficiency
  • Hereditary nonspherocytic hemolytic anemia
  • Hereditary nonspherocytic hemolytic anemia due to aldolase A deficiency
  • Hereditary nonspherocytic hemolytic anemia due to decreased adenosine deaminase activity
  • Hereditary nonspherocytic hemolytic anemia due to diphosphoglycerate mutase deficiency
  • Hereditary nonspherocytic hemolytic anemia due to gamma glutamyl cysteine synthetase deficiency
  • Hereditary nonspherocytic hemolytic anemia due to glucose phosphate isomerase deficiency
  • Hereditary nonspherocytic hemolytic anemia due to hexokinase deficiency
  • Hereditary nonspherocytic hemolytic anemia due to increased adenosine deaminase activity
  • Hereditary nonspherocytic hemolytic anemia due to phosphofructokinase deficiency
  • Hereditary nonspherocytic hemolytic anemia due to phosphoglycerate kinase deficiency
  • Hereditary nonspherocytic hemolytic anemia due to pyrimidine-5'-nucleotidase deficiency
  • Hereditary nonspherocytic hemolytic anemia due to pyruvate kinase deficiency
  • Hereditary nonspherocytic hemolytic anemia due to reduced nicotinamide adenine dinucleotide diaphorase deficiency
  • Hereditary nonspherocytic hemolytic anemia due to triosephosphate isomerase deficiency
  • Triose phosphate isomerase deficiency
Applies To
  • Anemia:
    • hemolytic nonspherocytic (hereditary), type II
    • hexokinase deficiency
    • pyruvate kinase [PK] deficiency
    • triosephosphate isomerase deficiency
Convert to ICD-10-CM: 282.3 converts approximately to:
  • 2014 ICD-10-CM D55.8 Other anemias due to enzyme disorders
ICD-9-CM Volume 2 Index entries containing back-references to 282.3:
  • Anemia 285.9
    • with
      • disorder of
        • anaerobic glycolysis 282.3
        • pentose phosphate pathway 282.2
      • koilonychia 280.9
    • congenital (following fetal blood loss) 776.5
      • aplastic 284.01
      • due to isoimmunization NEC 773.2
      • Heinz-body 282.7
      • hereditary hemolytic NEC 282.9
      • nonspherocytic
        • type I 282.2
        • type II 282.3
      • pernicious 281.0
      • spherocytic (see also Spherocytosis) 282.0
    • Dacie's (nonspherocytic)
      • type I 282.2
      • type II 282.3
    • deficiency 281.9
      • 2, 3 diphosphoglycurate mutase 282.3
      • 2, 3 PG 282.3
      • 6-PGD 282.2
      • 6-phosphogluronic dehydrogenase 282.2
      • amino acid 281.4
      • combined B12 and folate 281.3
      • enzyme, drug-induced (hemolytic) 282.2
      • erythrocytic glutathione 282.2
      • folate 281.2
      • folic acid 281.2
      • G-6-PD 282.2
      • GGS-R 282.2
      • glucose-6-phosphate dehydrogenase (G-6-PD) 282.2
      • glucose-phosphate isomerase 282.3
      • glutathione peroxidase 282.2
      • glutathione reductase 282.2
      • glyceraldehyde phosphate dehydrogenase 282.3
      • GPI 282.3
      • G SH 282.2
      • hexokinase 282.3
      • iron (Fe) 280.9
      • nutritional 281.9
        • with
          • poor iron absorption 280.9
          • specified deficiency NEC 281.8
        • due to inadequate dietary iron intake 280.1
        • specified type NEC 281.8
      • of or complicating pregnancy 648.2
      • pentose phosphate pathway 282.2
      • PFK 282.3
      • phosphofructo-aldolase 282.3
      • phosphofructokinase 282.3
      • phosphoglycerate kinase 282.3
      • PK 282.3
      • protein 281.4
      • pyruvate kinase (PK) 282.3
      • TPI 282.3
      • triosephosphate isomerase 282.3
      • vitamin B12 NEC 281.1
    • due to
      • antineoplastic chemotherapy 285.3
      • blood loss (chronic) 280.0
      • chemotherapy, antineoplastic 285.3
      • defect of Embden-Meyerhof pathway glycolysis 282.3
      • disorder of glutathione metabolism 282.2
      • drug - see Anemia, by type (see also Table of Drugs and Chemicals)
        • chemotherapy, antineoplastic 285.3
      • fetal blood loss 776.5
      • fish tapeworm (D. latum) infestation 123.4
      • glutathione metabolism disorder 282.2
      • hemorrhage (chronic) 280.0
      • hexose monophosphate (HMP) shunt deficiency 282.2
      • impaired absorption 280.9
      • loss of blood (chronic) 280.0
      • myxedema 244.9
      • Necator americanus 126.1
      • prematurity 776.6
      • selective vitamin B12 malabsorption with proteinuria 281.1
    • hemolytic 283.9
      • acquired 283.9
        • with hemoglobinuria NEC 283.2
        • autoimmune (cold type) (idiopathic) (primary) (secondary) (symptomatic) (warm type) 283.0
        • due to
          • cold reactive antibodies 283.0
          • drug exposure 283.0
          • warm reactive antibodies 283.0
        • fragmentation 283.19
        • idiopathic (chronic) 283.9
        • infectious 283.19
        • non-autoimmune 283.10
        • toxic 283.19
        • traumatic cardiac 283.19
      • acute 283.9
        • due to enzyme deficiency NEC 282.3
        • fetus or newborn (see also Disease, hemolytic) 773.2
        • Lederer's (acquired infectious hemolytic anemia) 283.19
      • autoimmune (acquired) 283.0
      • chronic 282.9
      • cold type (secondary) (symptomatic) 283.0
      • congenital (spherocytic) (see also Spherocytosis) 282.0
        • nonspherocytic - see Anemia, hemolytic, nonspherocytic, congenital
      • drug-induced 283.0
      • due to
        • cardiac conditions 283.19
        • drugs 283.0
        • enzyme deficiency NEC 282.3
        • presence of shunt or other internal prosthetic device 283.19
        • thrombotic thrombocytopenic purpura 446.6
      • elliptocytotic (see also Elliptocytosis) 282.1
      • familial 282.9
      • hereditary 282.9
        • due to enzyme deficiency NEC 282.3
        • specified NEC 282.8
      • idiopathic (chronic) 283.9
      • infectious (acquired) 283.19
      • mechanical 283.19
      • microangiopathic 283.19
      • nonautoimmune 283.10
      • nonspherocytic
        • congenital or hereditary NEC 282.3
          • glucose-6-phosphate dehydrogenase deficiency 282.2
          • pyruvate kinase (PK) deficiency 282.3
          • type I 282.2
          • type II 282.3
        • type I 282.2
        • type II 282.3
      • of or complicating pregnancy 648.2
      • resulting from presence of shunt or other internal prosthetic device 283.19
      • secondary 283.19
      • sickle-cell - see Disease, sickle-cell
      • Stransky-Regala type (Hb-E) (see also Disease, hemoglobin) 282.7
      • symptomatic 283.19
      • toxic (acquired) 283.19
      • uremic (adult) (child) 283.11
      • warm type (secondary) (symptomatic) 283.0
    • hexokinase deficiency 282.3
    • pyruvate kinase (PK) deficiency 282.3
    • triosephosphate isomerase deficiency 282.3
  • Deficiency, deficient
    • pyruvate kinase (PK) 282.3
  • Disorder - see also Disease
    • anaerobic glycolysis with anemia 282.3
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 282.3 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2012 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.