![Specific code](/images/bullet_triangle_green.png)
2015 ICD-9-CM Diagnosis Code 282.3
Other hemolytic anemias due to enzyme deficiency
- 2015
- Billable Thru Sept 30/2015
- Non-Billable On/After Oct 1/2015
- ICD-9-CM 282.3 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 282.3 should only be used for claims with a date of service on or before September 30, 2015. For claims with a date of service on or after October 1, 2015, use an equivalent ICD-10-CM code (or codes).
Convert to ICD-10-CM:
282.3 converts approximately to:
- 2015/16 ICD-10-CM D55.8 Other anemias due to enzyme disorders
Approximate Synonyms
- Anemia due to disorders of glycolytic enzymes
- Anemia due to disorders of nucleotide metabolism
- Anemia due to enzyme deficiency
- Anemia due to enzyme disorder
- Chronic non-spherocytic hemolytic anemia
- Deficiency of pyruvate kinase
- Fumarase deficiency
- Hemolytic anemia due to enzyme deficiency
- Hemolytic anemia due to hexokinase deficiency
- Hemolytic anemia due to pyruvate kinase deficiency
- Hemolytic anemia due to triose phosphate isomerase deficiency
- Hereditary nonspherocytic hemolytic anemia
- Hereditary nonspherocytic hemolytic anemia due to aldolase A deficiency
- Hereditary nonspherocytic hemolytic anemia due to decreased adenosine deaminase activity
- Hereditary nonspherocytic hemolytic anemia due to diphosphoglycerate mutase deficiency
- Hereditary nonspherocytic hemolytic anemia due to gamma glutamyl cysteine synthetase deficiency
- Hereditary nonspherocytic hemolytic anemia due to glucose phosphate isomerase deficiency
- Hereditary nonspherocytic hemolytic anemia due to hexokinase deficiency
- Hereditary nonspherocytic hemolytic anemia due to increased adenosine deaminase activity
- Hereditary nonspherocytic hemolytic anemia due to phosphofructokinase deficiency
- Hereditary nonspherocytic hemolytic anemia due to phosphoglycerate kinase deficiency
- Hereditary nonspherocytic hemolytic anemia due to pyrimidine-5'-nucleotidase deficiency
- Hereditary nonspherocytic hemolytic anemia due to pyruvate kinase deficiency
- Hereditary nonspherocytic hemolytic anemia due to reduced nicotinamide adenine dinucleotide diaphorase deficiency
- Hereditary nonspherocytic hemolytic anemia due to triosephosphate isomerase deficiency
- Triose phosphate isomerase deficiency
Applies To
- Anemia:
- hemolytic nonspherocytic (hereditary), type II
- hexokinase deficiency
- pyruvate kinase [PK] deficiency
- triosephosphate isomerase deficiency
ICD-9-CM Volume 2 Index entries containing back-references to
282.3:
- Anemia 285.9
![](/images/note.png)
with![](/images/vertical.gif)
disorder of![](/images/vertical.gif)
![](/images/vertical.gif)
anaerobic glycolysis 282.3![](/images/vertical.gif)
![](/images/vertical.gif)
pentose phosphate pathway 282.2![](/images/note.png)
![](/images/vertical.gif)
koilonychia 280.9![](/images/note.png)
congenital (following fetal blood loss) 776.5![](/images/note.png)
![](/images/vertical.gif)
aplastic 284.01![](/images/note.png)
![](/images/vertical.gif)
due to isoimmunization NEC 773.2![](/images/note.png)
![](/images/vertical.gif)
Heinz-body 282.7![](/images/note.png)
![](/images/vertical.gif)
hereditary hemolytic NEC 282.9![](/images/note.png)
![](/images/vertical.gif)
nonspherocytic![](/images/vertical.gif)
![](/images/vertical.gif)
type I 282.2![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
type II 282.3
![](/images/vertical.gif)
pernicious 281.0![](/images/note.png)
![](/images/vertical.gif)
spherocytic (see also Spherocytosis) 282.0![](/images/note.png)
Dacie's (nonspherocytic)![](/images/vertical.gif)
type I 282.2![](/images/note.png)
![](/images/vertical.gif)
type II 282.3
deficiency 281.9![](/images/note.png)
![](/images/vertical.gif)
2, 3 diphosphoglycurate mutase 282.3![](/images/vertical.gif)
2, 3 PG 282.3![](/images/vertical.gif)
6-PGD 282.2![](/images/note.png)
![](/images/vertical.gif)
6-phosphogluronic dehydrogenase 282.2![](/images/note.png)
![](/images/vertical.gif)
amino acid 281.4![](/images/note.png)
![](/images/vertical.gif)
combined B12 and folate 281.3![](/images/note.png)
![](/images/vertical.gif)
enzyme, drug-induced (hemolytic) 282.2![](/images/note.png)
![](/images/vertical.gif)
erythrocytic glutathione 282.2![](/images/note.png)
![](/images/vertical.gif)
folate 281.2![](/images/note.png)
![](/images/vertical.gif)
folic acid 281.2![](/images/note.png)
![](/images/vertical.gif)
G-6-PD 282.2![](/images/note.png)
![](/images/vertical.gif)
GGS-R 282.2![](/images/note.png)
![](/images/vertical.gif)
glucose-6-phosphate dehydrogenase (G-6-PD) 282.2![](/images/note.png)
![](/images/vertical.gif)
glucose-phosphate isomerase 282.3![](/images/vertical.gif)
glutathione peroxidase 282.2![](/images/note.png)
![](/images/vertical.gif)
glutathione reductase 282.2![](/images/note.png)
![](/images/vertical.gif)
glyceraldehyde phosphate dehydrogenase 282.3![](/images/vertical.gif)
GPI 282.3![](/images/vertical.gif)
G SH 282.2![](/images/note.png)
![](/images/vertical.gif)
hexokinase 282.3![](/images/vertical.gif)
iron (Fe) 280.9![](/images/note.png)
![](/images/vertical.gif)
nutritional 281.9![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
with![](/images/vertical.gif)
![](/images/vertical.gif)
![](/images/vertical.gif)
poor iron absorption 280.9![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
![](/images/vertical.gif)
specified deficiency NEC 281.8![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
due to inadequate dietary iron intake 280.1![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
specified type NEC 281.8![](/images/note.png)
![](/images/vertical.gif)
of or complicating pregnancy 648.2![](/images/note.png)
![](/images/vertical.gif)
pentose phosphate pathway 282.2![](/images/note.png)
![](/images/vertical.gif)
PFK 282.3![](/images/vertical.gif)
phosphofructo-aldolase 282.3![](/images/vertical.gif)
phosphofructokinase 282.3![](/images/vertical.gif)
phosphoglycerate kinase 282.3![](/images/vertical.gif)
PK 282.3![](/images/vertical.gif)
protein 281.4![](/images/note.png)
![](/images/vertical.gif)
pyruvate kinase (PK) 282.3![](/images/vertical.gif)
TPI 282.3![](/images/vertical.gif)
triosephosphate isomerase 282.3![](/images/vertical.gif)
vitamin B12 NEC 281.1![](/images/note.png)
due to![](/images/vertical.gif)
antineoplastic chemotherapy 285.3![](/images/note.png)
![](/images/vertical.gif)
blood loss (chronic) 280.0![](/images/note.png)
![](/images/vertical.gif)
chemotherapy, antineoplastic 285.3![](/images/note.png)
![](/images/vertical.gif)
defect of Embden-Meyerhof pathway glycolysis 282.3![](/images/vertical.gif)
disorder of glutathione metabolism 282.2![](/images/note.png)
![](/images/vertical.gif)
drug - see Anemia, by type (see also Table of Drugs and Chemicals)![](/images/vertical.gif)
![](/images/vertical.gif)
chemotherapy, antineoplastic 285.3![](/images/note.png)
![](/images/vertical.gif)
fetal blood loss 776.5![](/images/note.png)
![](/images/vertical.gif)
fish tapeworm (D. latum) infestation 123.4![](/images/note.png)
![](/images/vertical.gif)
glutathione metabolism disorder 282.2![](/images/note.png)
![](/images/vertical.gif)
hemorrhage (chronic) 280.0![](/images/note.png)
![](/images/vertical.gif)
hexose monophosphate (HMP) shunt deficiency 282.2![](/images/note.png)
![](/images/vertical.gif)
impaired absorption 280.9![](/images/note.png)
![](/images/vertical.gif)
loss of blood (chronic) 280.0![](/images/note.png)
![](/images/vertical.gif)
myxedema 244.9![](/images/note.png)
![](/images/vertical.gif)
Necator americanus 126.1![](/images/note.png)
![](/images/vertical.gif)
prematurity 776.6![](/images/note.png)
![](/images/vertical.gif)
selective vitamin B12 malabsorption with proteinuria 281.1![](/images/note.png)
hemolytic 283.9![](/images/note.png)
![](/images/vertical.gif)
acquired 283.9![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
with hemoglobinuria NEC 283.2![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
autoimmune (cold type) (idiopathic) (primary) (secondary) (symptomatic) (warm type) 283.0![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
due to![](/images/vertical.gif)
![](/images/vertical.gif)
![](/images/vertical.gif)
cold reactive antibodies 283.0![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
![](/images/vertical.gif)
drug exposure 283.0![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
![](/images/vertical.gif)
warm reactive antibodies 283.0![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
fragmentation 283.19![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
idiopathic (chronic) 283.9![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
infectious 283.19![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
non-autoimmune 283.10![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
toxic 283.19![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
traumatic cardiac 283.19![](/images/note.png)
![](/images/vertical.gif)
acute 283.9![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
due to enzyme deficiency NEC 282.3![](/images/vertical.gif)
![](/images/vertical.gif)
fetus or newborn (see also Disease, hemolytic) 773.2![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
Lederer's (acquired infectious hemolytic anemia) 283.19![](/images/note.png)
![](/images/vertical.gif)
autoimmune (acquired) 283.0![](/images/note.png)
![](/images/vertical.gif)
chronic 282.9![](/images/note.png)
![](/images/vertical.gif)
cold type (secondary) (symptomatic) 283.0![](/images/note.png)
![](/images/vertical.gif)
congenital (spherocytic) (see also Spherocytosis) 282.0![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
nonspherocytic - see Anemia, hemolytic, nonspherocytic, congenital
![](/images/vertical.gif)
drug-induced 283.0![](/images/note.png)
![](/images/vertical.gif)
due to![](/images/vertical.gif)
![](/images/vertical.gif)
cardiac conditions 283.19![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
drugs 283.0![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
enzyme deficiency NEC 282.3![](/images/vertical.gif)
![](/images/vertical.gif)
presence of shunt or other internal prosthetic device 283.19![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
thrombotic thrombocytopenic purpura 446.6![](/images/note.png)
![](/images/vertical.gif)
elliptocytotic (see also Elliptocytosis) 282.1![](/images/note.png)
![](/images/vertical.gif)
familial 282.9![](/images/note.png)
![](/images/vertical.gif)
hereditary 282.9![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
due to enzyme deficiency NEC 282.3![](/images/vertical.gif)
![](/images/vertical.gif)
specified NEC 282.8![](/images/note.png)
![](/images/vertical.gif)
idiopathic (chronic) 283.9![](/images/note.png)
![](/images/vertical.gif)
infectious (acquired) 283.19![](/images/note.png)
![](/images/vertical.gif)
mechanical 283.19![](/images/note.png)
![](/images/vertical.gif)
microangiopathic 283.19![](/images/note.png)
![](/images/vertical.gif)
nonautoimmune 283.10![](/images/note.png)
![](/images/vertical.gif)
nonspherocytic![](/images/vertical.gif)
![](/images/vertical.gif)
congenital or hereditary NEC 282.3![](/images/vertical.gif)
![](/images/vertical.gif)
![](/images/vertical.gif)
glucose-6-phosphate dehydrogenase deficiency 282.2![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
![](/images/vertical.gif)
pyruvate kinase (PK) deficiency 282.3![](/images/vertical.gif)
![](/images/vertical.gif)
![](/images/vertical.gif)
type I 282.2![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
![](/images/vertical.gif)
type II 282.3
![](/images/vertical.gif)
![](/images/vertical.gif)
type I 282.2![](/images/note.png)
![](/images/vertical.gif)
![](/images/vertical.gif)
type II 282.3
![](/images/vertical.gif)
of or complicating pregnancy 648.2![](/images/note.png)
![](/images/vertical.gif)
resulting from presence of shunt or other internal prosthetic device 283.19![](/images/note.png)
![](/images/vertical.gif)
secondary 283.19![](/images/note.png)
![](/images/vertical.gif)
sickle-cell - see Disease, sickle-cell![](/images/vertical.gif)
Stransky-Regala type (Hb-E) (see also Disease, hemoglobin) 282.7![](/images/note.png)
![](/images/vertical.gif)
symptomatic 283.19![](/images/note.png)
![](/images/vertical.gif)
toxic (acquired) 283.19![](/images/note.png)
![](/images/vertical.gif)
uremic (adult) (child) 283.11![](/images/note.png)
![](/images/vertical.gif)
warm type (secondary) (symptomatic) 283.0![](/images/note.png)
hexokinase deficiency 282.3
pyruvate kinase (PK) deficiency 282.3
triosephosphate isomerase deficiency 282.3
- Deficiency, deficient
pyruvate kinase (PK) 282.3
- Disorder - see also Disease
anaerobic glycolysis with anemia 282.3