Specific code 2012 ICD-9-CM Diagnosis Code 270.6
Disorders of urea cycle metabolism
  • Short description: Dis urea cycle metabol.
  • ICD-9-CM 270.6 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 270.6 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
  • You are viewing the 2012 version of ICD-9-CM 270.6.
  • More recent version(s) of ICD-9-CM 270.6: 2013 2014.
Disease Synonyms
  • Arginase deficiency
  • Argininaemia
  • Argininemia
  • Argininosuccinate lyase deficiency
  • Arginosuccinate lyase deficiency
  • Carbamoyl phosphate synthetase deficiency
  • Citrullinemia
  • Congenital hyperammonemia, type I
  • Deficiency, arginosuccinate lyase
  • Deficiency, carbamyl phosphate synthetase
  • Deficiency, N acetylglutamate synthetase
  • Deficiency, ornithine transcarbamylase
  • Disorder of ornithine metabolism
  • Disorder of the urea cycle metabolism
  • Disorder of urea cycle metabolism
  • Hyperammonemia
  • Hyperammonemia, type III
  • Hyperornithinemia hyperammonemia homocitrullinemia
  • Hyperornithinemia hyperammonemia homocitrullinemia syndrome
  • Hyperornithinemia-hyperammonemia-homocitrullinuria syndrome
  • N-acetylglutamate synthetase deficiency
  • Ornithine carbamoyltransferase deficiency
  • Ornithine metabolism disorder
  • Ornithine transcarbamylase deficiency
  • Urea cycle metabolism disorder
Applies To
  • Argininosuccinic aciduria
  • Citrullinemia
  • Disorders of metabolism of ornithine, citrulline, argininosuccinic acid, arginine, and ammonia
  • Hyperammonemia
  • Hyperornithinemia
Convert to ICD-10-CM: 270.6 converts approximately to:
  • 2014 ICD-10-CM E72.20 Disorder of urea cycle metabolism, unspecified
    Or:
  • 2014 ICD-10-CM E72.22 Arginosuccinic aciduria
    Or:
  • 2014 ICD-10-CM E72.23 Citrullinemia
    Or:
  • 2014 ICD-10-CM E72.29 Other disorders of urea cycle metabolism
ICD-9-CM Volume 2 Index entries containing back-references to 270.6:
  • Acidemia 276.2
    • arginosuccinic 270.6
  • Aciduria 791.9
    • arginosuccinic 270.6
  • Arginosuccinicaciduria 270.6
  • Citrullinemia 270.6
  • Citrullinuria 270.6
  • Deficiency, deficient
    • argininosuccinate synthetase or lyase 270.6
    • carbamyl phosphate synthetase 270.6
    • ornithine transcarbamylase 270.6
  • Disorder - see also Disease
  • Disturbance - see also Disease
  • Hyperaminoaciduria 270.9
    • arginine 270.6
    • citrulline 270.6
    • ornithine 270.6
  • Hyperammonemia (congenital) 270.6
  • Hyperornithinemia 270.6
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 270.6 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2012 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.