Home > 2012 ICD-9-CM Diagnosis Codes > Endocrine, Nutritional And Metabolic Diseases, And Immunity Disorders 240-279 > Other Metabolic Disorders And Immunity Disorders 270-279 > Other and unspecified disorders of metabolism 277-
2012 ICD-9-CM Diagnosis Code 277.89
Other specified disorders of metabolism
- group of disorders of histiocyte proliferation which includes Letterer-Siwe disease; Hand-Schueller-Christian syndrome; and eosinophilic granuloma; Langerhans cells are components of the lesions.
- A neoplastic proliferation of Langerhans cells which contain Birbeck granules by ultrastructural examination. Three major overlapping syndromes are recognized: eosinophilic granuloma, Letterer-Siwe disease, and Hand-Schuller-Christian disease. The clinical course is generally related to the number of organs affected at presentation. (WHO, 2001)
- A multifocal, unisystem form of Langerhans-cell histiocytosis. There is involvement of multiple sites in one organ system, most frequently the bone. Patients are usually young children presenting with multiple destructive bone lesions.
- Short description: Metabolism disorder NEC.
- ICD-9-CM 277.89 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
- You are viewing the 2012 version of ICD-9-CM 277.89.
- More recent version(s) of ICD-9-CM 277.89: 2013.
277.89 Alternative Terminology
- Acatalasemia
- Acatalasia
- Adenosine deaminase overproduction
- Alpha-n-acetylgalactosaminidase deficiency
- Anemia due to disorders of nucleotide metabolism
- Autosomal variant form of transthyretin
- Combined complex deficiencies
- Combined deficiency of long chain 3-hydroxyacyl-coa dehydrogenase and enoyl-coa hydratase
- Defect in post-translational modification of lysosomal enzymes
- Defective biosynthesis
- Defective osmoregulation
- Deficiency in enzyme complexes of mitochondrial respiratory chain
- Deficiency of amylopectin 6-glucanohydrolase
- Deficiency of glycosidase
- Deficiency of halogenase
- Deficiency of isobutyryl-coa dehydrogenase
- Deficiency of limit dextrinase
- Deficiency of protease
- Deletion and duplication of mitochondrial dna
- Depletion of mitochondrial dna
- Disorder of beta alanine, carnosine and/or homocarnosine metabolism
- Disorder of chromium metabolism
- Disorder of glucose regulation
- Disorder of glycoprotein metabolism
- Disorder of glycosaminoglycan metabolism
- Disorder of iodine metabolism
- Disorder of mitochondrial respiratory chain complexes
- Disorder of organic acid metabolism
- Disorder of osmoregulation
- Disorder of oxygen transport
- Disorder of peroxisomal function
- Disorder of protein metabolism
- Disorder of pyruvate metabolism and mitochondrial respiratory chain
- Disorder of sialic acid metabolism
- Disorder of steroid metabolism
- Disorder of strontium metabolism
- Disorder with defective osteoid mineralization
- Disorders of pyruvate metabolism and gluconeogenesis
- Drug resistance to insulin
- Enterokinase deficiency
- Eosinophilic granuloma of bone
- Extensive metabolizer due to cytochrome p450 cyp2d6 variant
- Familial sea-blue histiocytosis
- Fast acetylator due to n-acetyltransferase enzyme variant
- Fat overload syndrome
- Glutaric aciduria, type 1
- Glutathione s-transferase deficiency
- Hand-sch�ller-christian disease
- Histiocytosis x syndrome
- Homocarnosinase deficiency
- Hyper-beta-carnosinemia
- Hyperimidodipeptiduria due to proline dipeptidase deficiency
- Impaired oxygen extraction
- Inborn error of pyruvate metabolism
- Increased auto-oxidation
- Increased fluid pressure
- Increased oxygen demand
- Inherited metabolic disorder of nervous system
- Intermediate metabolizer due to cytochrome p450 cyp2d6 variant
- Langerhans cell histiocytosis
- Langerhans cell histiocytosis - hashimoto-pritzker type
- Langerhans cell histiocytosis of lung
- Langerhans cell histiocytosis, unifocal
- Macroamylasemia
- Methylene thf reductase deficiency and homocystinuria
- Mucinous histiocytosis of the colon
- Pancreatic colipase deficiency
- Pancreatic triacylglycerol lipase deficiency
- Phosphoenolpyruvate carboxykinase deficiency
- Poor metabolizer due to cytochrome p450 cyp2c19 variant
- Poor metabolizer due to cytochrome p450 cyp2c9 variant
- Poor metabolizer due to cytochrome p450 cyp2d6 variant
- Pseudoinfantile refsum's disease
- Pyruvate carboxylase deficiency
- Pyruvate dehydrogenase complex deficiency
- Refeeding syndrome
- Sepiapterin reductase deficiency
- Sinus histiocytosis with massive lymphadenopathy
- Slow acetylator due to n-acetyltransferase enzyme variant
- Solitary reticulohistiocytoma
- Tetrahydrobiopterin synthesis defect
- Trypsinogen deficiency
- Tumor lysis syndrome
- Ugt1a1*28 polymorphism
- Ultrarapid metabolizer due to cytochrome p450 cyp2d6 variant
- Undetermined cell histiocytosis
277.89 Excludes 
Applies To
- Hand-Schüller-Christian disease
- Histiocytosis (acute) (chronic)
- Histiocytosis X (chronic)
Convert 277.89 to ICD-10-CM
ICD-9-CM 277.89 converts approximately to:
- 2013 ICD-10-CM C96.5 Multifocal and unisystemic Langerhans-cell histiocytosisOr:
- 2013 ICD-10-CM C96.6 Unifocal Langerhans-cell histiocytosisOr:
- 2013 ICD-10-CM E71.39 Other disorders of fatty-acid metabolismOr:
- 2013 ICD-10-CM E80.3 Defects of catalase and peroxidaseOr:
- 2013 ICD-10-CM E88.89 Other specified metabolic disordersOr:
- 2013 ICD-10-CM E88.9 Metabolic disorder, unspecified
ICD-9-CM Volume 2 Index entries containing back-references to 277.89:
- Acatalasemia 277.89
- Acatalasia 277.89
- Christian's syndrome (chronic histiocytosis X) 277.89
- Disease, diseased - see also Syndrome
Christian's (chronic histiocytosis X) 277.89
- Erdheim-Chester (ECD) 277.89
- Hand-Schüller-Christian (chronic histiocytosis X) 277.89
Schüller-Christian (chronic histiocytosis X) 277.89
- Disorder - see also Disease
- metabolism NEC 277.9
with- alkaptonuria 270.2
- amino acid (see also Disorder, amino acid) 270.9
specified type NEC 270.8
- ammonia 270.6
- arginine 270.6
- argininosuccinic acid 270.6
- basal 794.7
- bilirubin 277.4
- calcium 275.40
- carbohydrate 271.9
- specified type NEC 271.8
- cholesterol 272.9
- citrulline 270.6
- copper 275.1
- corticosteroid 255.2
- cystine storage 270.0
- cystinuria 270.0
- fat 272.9
- fatty acid oxidation 277.85
- following
- fructosemia 271.2
- fructosuria 271.2
- fucosidosis 271.8
- galactose-1-phosphate uridyl transferase 271.1
- glutamine 270.7
- glycine 270.7
- glycogen storage NEC 271.0
- hepatorenal 271.0
- hemochromatosis (see also Hemochromatosis) 275.03
- in labor and delivery 669.0
- iron 275.09
- lactose 271.3
- lipid 272.9
- lipoprotein - see also Hyperlipemia
- deficiency (familial) 272.5
- lysine 270.7
- magnesium 275.2
- mannosidosis 271.8
- mineral 275.9
- specified type NEC 275.8
- mitochondrial 277.87
- mucopolysaccharide 277.5
- nitrogen 270.9
- ornithine 270.6
- oxalosis 271.8
- pentosuria 271.8
- phenylketonuria 270.1
- phosphate 275.3
- phosphorus 275.3
- plasma protein 273.9
- specified type NEC 273.8
- porphyrin 277.1
- purine 277.2
- pyrimidine 277.2
- serine 270.7
- sodium 276.9
- specified type NEC 277.89
- steroid 255.2
- threonine 270.7
- urea cycle 270.6
- xylose 271.8
- ECD (Erdheim-Chester disease) 277.89
- Eosinophilic - see also condition
- granuloma (bone) 277.89
- Erdheim-Chester disease (ECD) 277.89
- Granuloma NEC 686.1
- eosinophilic 277.89
- bone 277.89
- lung 277.89
- oral mucosa 528.9
- lipid 277.89
- lipoid 277.89
- reticulohistiocytic 277.89
- Granulomatosis NEC 686.1
- lipoid 277.89
- Hand-Schüller-Christian disease or syndrome (chronic histiocytosis x) 277.89
- Histiocytosis (acute) (chronic) (subacute) 277.89
- acute differentiated progressive (M9722/3) 202.5
- adult pulmonary Langerhans cell (PLCH) 516.5
- cholesterol 277.89
- essential 277.89
- lipid, lipoid (essential) 272.7
- lipochrome (familial) 288.1
- malignant (M9720/3) 202.3
- non-Langerhans cell 277.89
- polyostotic sclerosing 277.89
- X (chronic) 277.89
- acute (progressive) (M9722/3) 202.5
- Metabolism disorder 277.9
- specified type NEC 277.89
- Reticulohistiocytoma (giant cell) 277.89
- Schüller-Christian disease or syndrome (chronic histiocytosis X) 277.89
- Syndrome - see also Disease
- Christian's (chronic histiocytosis X) 277.89
- Erdheim-Chester 277.89
- Hand-Schüller-Christian (chronic histiocytosis X) 277.89
- Schüller-Christian (chronic histiocytosis X) 277.89
- Xanthoma(s), xanthomatosis 272.2
- craniohypophyseal 277.89
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 277.89 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2012 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.
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