2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Diseases Of Blood And Blood-Forming Organs 280-289 > Coagulation Defects 286.* > 2006 ICD-9-CM Diagnosis 286.0 Congenital factor viii disorder View the most recent version of ICD-9-CM 286.0 Group of hereditary disorders in which affected individuals fail to make enough of certain proteins needed to form blood clots. The classic hemophilia resulting from a deficiency of factor VIII. It is an inherited disorder of blood coagulation characterized by a permanent tendency to hemorrhage. An inherited deficiency of coagulation Factor VIII characterized by the tendency to spontaneous or exaggerated post-traumatic hemorrhage. Inherited as an x-linked recessive disease, hemophilia A is the most common hemophilia, occurring in approximately 1 in 10,000 male births. --2004 A deficiency or abnormality of a blood coagulation factor characterized by the tendency to spontaneous or exaggerated post-traumatic hemorrhage, Hemophilia is typically a hereditary disorder but, rarely, may be acquired. Inherited coagulation factor-deficient hemophilias include hemophilia A or classic hemophilia (Factor VIII deficiency) hemophilia B or Christmas disease (Factor IX deficiency), and hemophilia C (Factor XI deficiency). In individuals without hereditary hemophilia A, Factor VIII inhibitors may occur spontaneously as autoantibodies, resulting in a condition known as 'acquired hemophilia.' Approximately 10 % of patients with acquired hemophilia have an underlying malignancy. --2004 286.0 is a specific code that can be used to specify a diagnosis 286.0 contains 11 index entries View the ICD-9-CM Volume 1 286.* hierarchy Alternate Terminology Antihemophilic globulin [AHG] deficiency Factor VIII (functional) deficiency Hemophilia: NOS A classical familial hereditary Subhemophilia 286.0 Excludes factor VIII deficiency with vascular defect (286.4)  Index entries containing 286.0: Deficiency, deficient antihemophilic factor (A) 286.0 B 286.1 C 286.2 globulin (AHG) NEC 286.0 factor (see also Defect, coagulation) 286.9 VIII (congenital) (functional) 286.0 with functional defect 286.0 vascular defect 286.4 Disease, diseased - see also Syndrome bleeder's 286.0 Disorder - see also Disease coagulation (factor) (see also Defect, coagulation) 286.9 factor VIII (congenital) (functional) 286.0 factor, coagulation (see also Defect, coagulation) 286.9 VIII (congenital) (functional) 286.0 Hemophilia (familial) (hereditary) 286.0 A 286.0 carrier (asymptomatic) V83.01 symptomatic V83.02 acquired 286.5 B (Leyden) 286.1 C 286.2 calcipriva (see also Fibrinolysis) 286.7 classical 286.0 nonfamilial 286.7 secondary 286.5 vascular 286.4 Subhemophilia 286.0