2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Diseases Of Blood And Blood-Forming Organs 280-289 > Coagulation Defects 286.* > 2006 ICD-9-CM Diagnosis 286.4 Von willebrand's disease View the most recent version of ICD-9-CM 286.4 Group of hemorrhagic disorders in which the von Willebrand factor (Factor VIII-related antigen) is either quantitatively or qualitatively abnormal. They are usually inherited as an autosomal dominant trait though rare kindreds are autosomal recessive. Symptoms vary depending on severity and disease type but may include prolonged bleeding time, deficiency of factor VIII, and impaired platelet adhesion. 286.4 is a specific code that can be used to specify a diagnosis 286.4 contains 16 index entries View the ICD-9-CM Volume 1 286.* hierarchy Alternate Terminology Angiohemophilia (A) (B) Constitutional thrombopathy Factor VIII deficiency with vascular defect Pseudohemophilia type B Vascular hemophilia von Willebrand's (-Jürgens') disease 286.4 Excludes factor VIII deficiency: NOS (286.0) with functional defect (286.0) hereditary capillary fragility (287.8)  Index entries containing 286.4: Angiohemophilia (A) (B) 286.4 Defect, defective 759.9 platelet (qualitative) 287.1 constitutional 286.4 Deficiency, deficient factor (see also Defect, coagulation) 286.9 VIII (congenital) (functional) 286.0 with vascular defect 286.4 platelet NEC 287.1 constitutional 286.4 Disease, diseased - see also Syndrome Minot-von Willebrand-Jürgens (angiohemophilia) 286.4 von Willebrand (-Jürgens) (angiohemophilia) 286.4 Hemophilia (familial) (hereditary) 286.0 vascular 286.4 Minot-von Willebrand (-Jürgens) disease or syndrome (angiohemophilia) 286.4 Prolonged, prolongation "idiopathic" (in von Willebrand's disease) 286.4 Pseudohemophilia (Bernuth's) (hereditary) (type B) 286.4 type A 287.8 vascular 287.8 Syndrome - see also Disease von Willebrand (-Jürgens) (angiohemophilia) 286.4 Willebrand (-Jürgens) (angiohemophilia) 286.4 Thrombopathy (Bernard-Soulier) 287.1 constitutional 286.4 Willebrand-Jürgens (angiohemophilia) 286.4 von Willebrand (-Jürgens) (-Minot) disease or syndrome (angiohemophilia) 286.4 Willebrand (-Jürgens) syndrome or thrombopathy (angiohemophilia) 286.4