Specific code 2014 ICD-9-CM Diagnosis Code 286.4
Von Willebrand's disease
  • Billable Code
  • ICD-9-CM 286.4 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 286.4 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Von willebrand disease
  • von Willebrand disorder
Clinical Information
  • Group of hemorrhagic disorders in which the von willebrand factor is either quantitatively or qualitatively abnormal. They are usually inherited as an autosomal dominant trait though rare kindreds are autosomal recessive. Symptoms vary depending on severity and disease type but may include prolonged bleeding time, deficiency of factor viii, and impaired platelet adhesion.
  • Hemophilioid disorder due to deficiency of von willebrand factor and thus of factor viii complex.
  • Hereditary or acquired coagulation disorder characterized by a qualitative or quantitative deficiency of the von willebrand factor. The latter plays an important role in platelet adhesion. Signs and symptoms include bruises, nose bleeding, gum bleeding following a dental procedure, heavy menstrual bleeding, and gastrointestinal bleeding.
  • Includes true von willebrand disease with mutation at the vwf locus, as well as mimicking disorders with other mutations (pseudo vwd) and acquired von willebrand syndrome
286.4 Excludes
  • factor VIII deficiency:
  • hereditary capillary fragility (287.8)
Applies To
  • Angiohemophilia (A) (B)
  • Constitutional thrombopathy
  • Factor VIII deficiency with vascular defect
  • Pseudohemophilia type B
  • Vascular hemophilia
  • von Willebrand's (-Jürgens') disease
Convert to ICD-10-CM: 286.4 converts directly to:
  • 2014 ICD-10-CM D68.0 Von Willebrand's disease
ICD-9-CM Volume 2 Index entries containing back-references to 286.4:
  • Angiohemophilia (A) (B) 286.4
  • Defect, defective 759.9
    • platelet (qualitative) 287.1
      • constitutional 286.4
  • Deficiency, deficient
    • factor (see also Defect, coagulation) 286.9
      • I (congenital) (fibrinogen) 286.3
        • antepartum or intrapartum 641.3
          • affecting fetus or newborn 762.1
        • newborn, transient 776.3
        • postpartum 666.3
      • II (congenital) (prothrombin) 286.3
      • V (congenital) (labile) 286.3
      • VII (congenital) (stable) 286.3
      • VIII (congenital) (functional) 286.0
        • with
          • functional defect 286.0
          • vascular defect 286.4
      • IX (Christmas) (congenital) (functional) 286.1
      • X (congenital) (Stuart-Prower) 286.3
      • XI (congenital) (plasma thromboplastin antecedent) 286.2
      • XII (congenital) (Hageman) 286.3
      • XIII (congenital) (fibrin stabilizing) 286.3
      • hageman 286.3
      • multiple (congenital) 286.9
    • platelet NEC 287.1
      • constitutional 286.4
  • Disease, diseased - see also Syndrome
    • Minot-von Willebrand-Jürgens (angiohemophilia) 286.4
    • von Willebrand (-Jürgens) (angiohemophilia) 286.4
  • Hemophilia (familial) (hereditary) 286.0
    • vascular 286.4
  • Minot-von Willebrand (-Jürgens) disease or syndrome (angiohemophilia) 286.4
  • Prolonged, prolongation
    • "idiopathic" (in von Willebrand's disease) 286.4
  • Pseudohemophilia (Bernuth's) (hereditary) (type B) 286.4
  • Syndrome - see also Disease
    • von Willebrand (-Jürgens) (angiohemophilia) 286.4
    • Willebrand (-Jürgens) (angiohemophilia) 286.4
  • Thrombopathy (Bernard-Soulier) 287.1
    • constitutional 286.4
    • Willebrand-Jürgens (angiohemophilia) 286.4
  • von Willebrand (-Jürgens) (-Minot) disease or syndrome (angiohemophilia) 286.4
  • Willebrand (-Jürgens) syndrome or thrombopathy (angiohemophilia) 286.4
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 286.4 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.