Specific code 2014 ICD-9-CM Diagnosis Code 286.0
Congenital factor VIII disorder
  • Billable Code
  • Short description: Cong factor viii diord.
  • ICD-9-CM 286.0 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 286.0 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Hemophilia
  • Hemophilia A
  • Hemophilic arthropathy
  • Hereditary factor VIII deficiency disease
Clinical Information
  • A deficiency or abnormality of a blood coagulation factor characterized by the tendency to spontaneous or exaggerated post-traumatic hemorrhage, hemophilia is typically a hereditary disorder but, rarely, may be acquired. Inherited coagulation factor-deficient hemophilias include hemophilia a or classic hemophilia (factor viii deficiency) hemophilia b or christmas disease (factor ix deficiency), and hemophilia c (factor xi deficiency). In individuals without hereditary hemophilia a, factor viii inhibitors may occur spontaneously as autoantibodies, resulting in a condition known as 'acquired hemophilia.' approximately 10 % of patients with acquired hemophilia have an underlying malignancy.
  • An inherited deficiency of coagulation factor viii characterized by the tendency to spontaneous or exaggerated post-traumatic hemorrhage. Inherited as an x-linked recessive disease, hemophilia a is the most common hemophilia, occurring in approximately 1 in 10,000 male births.
  • Classic hemophilia resulting from a deficiency of factor viii; an inherited disorder of blood coagulation characterized by a permanent tendency to hemorrhage.
  • Group of hereditary disorders in which affected individuals fail to make enough of certain proteins needed to form blood clots.
286.0 Excludes
  • factor VIII deficiency with vascular defect (286.4)
Applies To
  • Antihemophilic globulin [AHG] deficiency
  • Factor VIII (functional) deficiency
  • Hemophilia:
    • NOS
    • A
    • classical
    • familial
    • hereditary
  • Subhemophilia
Convert to ICD-10-CM: 286.0 converts directly to:
  • 2014 ICD-10-CM D66 Hereditary factor VIII deficiency
ICD-9-CM Volume 2 Index entries containing back-references to 286.0:
  • Deficiency, deficient
    • antihemophilic
      • factor (A) 286.0
      • globulin (AHG) NEC 286.0
    • factor (see also Defect, coagulation) 286.9
      • I (congenital) (fibrinogen) 286.3
        • antepartum or intrapartum 641.3
          • affecting fetus or newborn 762.1
        • newborn, transient 776.3
        • postpartum 666.3
      • II (congenital) (prothrombin) 286.3
      • V (congenital) (labile) 286.3
      • VII (congenital) (stable) 286.3
      • VIII (congenital) (functional) 286.0
        • with
          • functional defect 286.0
          • vascular defect 286.4
      • IX (Christmas) (congenital) (functional) 286.1
      • X (congenital) (Stuart-Prower) 286.3
      • XI (congenital) (plasma thromboplastin antecedent) 286.2
      • XII (congenital) (Hageman) 286.3
      • XIII (congenital) (fibrin stabilizing) 286.3
      • hageman 286.3
      • multiple (congenital) 286.9
  • Disease, diseased - see also Syndrome
    • bleeder's 286.0
  • Disorder - see also Disease
    • coagulation (factor) (see also Defect, coagulation) 286.9
      • factor VIII (congenital) (functional) 286.0
      • factor IX (congenital) (functional) 286.1
      • neonatal, transitory 776.3
    • factor, coagulation (see also Defect, coagulation) 286.9
      • VIII (congenital) (functional) 286.0
      • IX (congenital) (functional) 286.1
  • Hemophilia (familial) (hereditary) 286.0
    • calcipriva (see also Fibrinolysis) 286.7
    • classical 286.0
  • Subhemophilia 286.0
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 286.0 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.