Specific code 2014 ICD-9-CM Diagnosis Code 286.2
Congenital factor XI deficiency
  • Billable Code
  • Short description: Cong factor xi disorder.
  • ICD-9-CM 286.2 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 286.2 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Factor XI deficiency, type I
  • Hemophilia C
  • Hemophilia C, type 1
  • Hereditary factor XI deficiency disease
Clinical Information
  • A hereditary deficiency of blood coagulation factor xi (also known as plasma thromboplastin antecedent or pta or antihemophilic factor c) resulting in a systemic blood-clotting defect called hemophilia c or rosenthal's syndrome, that may resemble classical hemophilia.
  • A rare inherited bleeding disorder caused by deficiency of coagulation factor xi. It may be asymptomatic or manifest with bleeding.
Applies To
  • Hemophilia C
  • Plasma thromboplastin antecedent [PTA] deficiency
  • Rosenthal's disease
Convert to ICD-10-CM: 286.2 converts directly to:
  • 2014 ICD-10-CM D68.1 Hereditary factor XI deficiency
ICD-9-CM Volume 2 Index entries containing back-references to 286.2:
  • Deficiency, deficient
    • factor (see also Defect, coagulation) 286.9
      • I (congenital) (fibrinogen) 286.3
        • antepartum or intrapartum 641.3
          • affecting fetus or newborn 762.1
        • newborn, transient 776.3
        • postpartum 666.3
      • II (congenital) (prothrombin) 286.3
      • V (congenital) (labile) 286.3
      • VII (congenital) (stable) 286.3
      • VIII (congenital) (functional) 286.0
      • IX (Christmas) (congenital) (functional) 286.1
      • X (congenital) (Stuart-Prower) 286.3
      • XI (congenital) (plasma thromboplastin antecedent) 286.2
      • XII (congenital) (Hageman) 286.3
      • XIII (congenital) (fibrin stabilizing) 286.3
      • hageman 286.3
      • multiple (congenital) 286.9
    • plasma
      • cell 279.00
      • protein (paraproteinemia) (pyroglobulinemia) 273.8
      • thromboplastin
        • antecedent (PTA) 286.2
        • component (PTC) 286.1
    • PTA 286.2
  • Disease, diseased - see also Syndrome
    • Rosenthal's (factor XI deficiency) 286.2
  • Hemophilia (familial) (hereditary) 286.0
    • C 286.2
  • Rosenthal's disease (factor XI deficiency) 286.2
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 286.2 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.