Specific code 2014 ICD-9-CM Diagnosis Code 286.3
Congenital deficiency of other clotting factors
  • Billable Code
  • Short description: Cong def clot factor NEC.
  • ICD-9-CM 286.3 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 286.3 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Alpha chain defect dysfibrinogenemia
  • Beta chain defect dysfibrinogenemia
  • Clotting factor deficiency, congenital
  • Congenital afibrinogenemia
  • Congenital clotting factor deficiency
  • Congenital coagulation factor deficiency
  • Congenital dysfibrinogenemia
  • Congenital fibrinogen abnormality
  • Congenital hypofibrinogenemia
  • Contact factor deficiency
  • Dysfibrinogenemia
  • Dysfibrinogenemia, congenital
  • Factor 10 deficiency
  • Factor 12 deficiency
  • Factor 2 mutation
  • Factor 5 deficiency
  • Factor 7 deficiency
  • Factor I deficiency
  • Factor I deficiency disease
  • Factor II deficiency
  • Factor V deficiency
  • Factor V deficiency, Quebec
  • Factor V Quebec
  • Factor VII deficiency
  • Factor X deficiency
  • Factor XII deficiency
  • Factor XII deficiency disease
  • Factor XIII deficiency disease
  • Factor XIII inhibitor disorder
  • Fibrinogen abnormality
  • Fibrinogen deficiency
  • Gamma chain defect dysfibrinogenemia
  • Hemorrhagic disease of the newborn due to factor II deficiency
  • Heparin cofactor II deficiency
  • Hereditary dysfibrinogenemia
  • Hereditary factor I deficiency disease
  • Hereditary factor II deficiency disease
  • Hereditary factor V deficiency disease
  • Hereditary factor VII deficiency disease
  • Hereditary factor X deficiency disease
  • Hereditary factor XII deficiency disease
  • Hereditary factor XIII A subunit and B subunit deficiency
  • Hereditary factor XIII A subunit deficiency
  • Hereditary factor XIII deficiency disease
  • Hyperfibrinogenemia
  • Hypodysfibrinogenemia
  • Hypofibrinogenemia
  • Passovoy factor deficiency
  • Placental abruption W afibrinogenemia
  • Placental abruption with afibrinogenemia
  • Platelet factor V deficiency
  • Platelet factor V deficiency (factor V Quebec)
  • Prothrombin complex deficiency
Clinical Information
  • Absence or reduced levels of prothrombin in the blood.
  • Deficiency or absence of fibrinogen (coagulation factor i) in the blood.
Applies To
  • Congenital afibrinogenemia
  • Deficiency:
    • AC globulin
    • factor:
      • I [fibrinogen]
      • II [prothrombin]
      • V [labile]
      • VII [stable]
      • X [Stuart-Prower]
      • XII [Hageman]
      • XIII [fibrin stabilizing]
    • Laki-Lorand factor
    • proaccelerin
  • Disease:
    • Owren's
    • Stuart-Prower
  • Dysfibrinogenemia (congenital)
  • Dysprothrombinemia (constitutional)
  • Hypoproconvertinemia
  • Hypoprothrombinemia (hereditary)
  • Parahemophilia
Convert to ICD-10-CM: 286.3 converts directly to:
  • 2014 ICD-10-CM D68.2 Hereditary deficiency of other clotting factors
ICD-9-CM Volume 2 Index entries containing back-references to 286.3:
  • Absence (organ or part) (complete or partial)
    • fibrinogen (congenital) 286.3
  • Afibrinogenemia 286.3
    • congenital 286.3
  • Defect, defective 759.9
    • fibrin polymerization (see also Defect, coagulation) 286.3
    • Hageman (factor) (see also Defect, coagulation) 286.3
  • Deficiency, deficient
    • accelerator globulin (Ac G) (blood) (see also Defect, coagulation) 286.3
    • AC globulin (congenital) (see also Defect, coagulation) 286.3
    • activating factor (blood) (see also Defect, coagulation) 286.3
    • autoprothrombin
      • I (see also Defect, coagulation) 286.3
      • II 286.1
      • C (see also Defect, coagulation) 286.3
    • coagulation factor NEC 286.9
      • with
        • abortion - see Abortion, by type, with hemorrhage
        • ectopic pregnancy (see also categories 634-638) 639.1
        • molar pregnancy (see also categories 630-632) 639.1
      • acquired (any) 286.7
      • antepartum or intrapartum 641.3
        • affecting fetus or newborn 762.1
      • complicating pregnancy, childbirth, or puerperium 649.3
      • due to
      • newborn, transient 776.3
      • postpartum 666.3
      • specified type NEC 286.3
    • contact factor (see also Defect, coagulation) 286.3
    • factor (see also Defect, coagulation) 286.9
      • I (congenital) (fibrinogen) 286.3
        • antepartum or intrapartum 641.3
          • affecting fetus or newborn 762.1
        • newborn, transient 776.3
        • postpartum 666.3
      • II (congenital) (prothrombin) 286.3
      • V (congenital) (labile) 286.3
      • VII (congenital) (stable) 286.3
      • VIII (congenital) (functional) 286.0
      • IX (Christmas) (congenital) (functional) 286.1
      • X (congenital) (Stuart-Prower) 286.3
      • XI (congenital) (plasma thromboplastin antecedent) 286.2
      • XII (congenital) (Hageman) 286.3
      • XIII (congenital) (fibrin stabilizing) 286.3
      • hageman 286.3
      • multiple (congenital) 286.9
    • fibrinase (see also Defect, coagulation) 286.3
    • fibrinogen (congenital) (see also Defect, coagulation) 286.3
    • fibrin-stabilizing factor (congenital) (see also Defect, coagulation) 286.3
    • glass factor (see also Defect, coagulation) 286.3
    • Hageman factor (congenital) (see also Defect, coagulation) 286.3
    • labile factor (congenital) (see also Defect, coagulation) 286.3
    • laki-Lorand factor (see also Defect, coagulation) 286.3
    • proaccelerin (congenital) (see also Defect, congenital) 286.3
    • proconvertin factor (congenital) (see also Defect, coagulation) 286.3
    • prothrombin (congenital) (see also Defect, coagulation) 286.3
    • Prower factor (see also Defect, coagulation) 286.3
    • SPCA (see also Defect, coagulation) 286.3
    • stable factor (congenital) (see also Defect, coagulation) 286.3
    • Stuart (-Prower) factor (see also Defect, coagulation) 286.3
    • thrombokinase (see also Defect, coagulation) 286.3
  • Disease, diseased - see also Syndrome
    • Hageman (congenital factor XII deficiency) (see also Defect, congenital) 286.3
    • Owren's (congenital) (see also Defect, coagulation) 286.3
    • Stuart's (congenital factor X deficiency) (see also Defect, coagulation) 286.3
    • Stuart-Prower (congenital factor X deficiency) (see also Defect, coagulation) 286.3
  • Dysfibrinogenemia (congenital) (see also Defect, coagulation) 286.3
  • Dysprothrombinemia (constitutional) (see also Defect, coagulation) 286.3
  • Fibrinogenopenia (congenital) (hereditary) (see also Defect, coagulation) 286.3
  • Fibrinopenia (hereditary) (see also Defect, coagulation) 286.3
  • Hageman factor defect, deficiency, or disease (see also Defect, coagulation) 286.3
  • Hypofibrinogenemia 286.3
    • congenital 286.3
  • Hypoproaccelerinemia (see also Defect, coagulation) 286.3
  • Hypoproconvertinemia (congenital) (see also Defect, coagulation) 286.3
  • Hypoprothrombinemia (congenital) (hereditary) (idiopathic) (see also Defect, coagulation) 286.3
  • Laki-Lorand factor deficiency (see also Defect, coagulation) 286.3
  • Owren's disease or syndrome (parahemophilia) (see also Defect, coagulation) 286.3
  • Parahemophilia (see also Defect, coagulation) 286.3
  • Stuart's disease (congenital factor X deficiency) (see also Defect, coagulation) 286.3
  • Stuart-Prower factor deficiency (congenital factor X deficiency) (see also Defect, coagulation) 286.3
  • Syndrome - see also Disease
    • Owren's (see also Defect, coagulation) 286.3
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 286.3 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.