2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Diseases Of Blood And Blood-Forming Organs 280-289 > Coagulation Defects 286.* > 2006 ICD-9-CM Diagnosis 286.1 Congenital factor ix disorder View the most recent version of ICD-9-CM 286.1 A deficiency of blood coagulation factor IX inherited as an X-linked disorder. (Also known as Christmas Disease, after the first patient studied in detail, not the holy day.) Historical and clinical features resemble those in classic hemophilia (HEMOPHILIA A), but patients present with fewer symptoms. Severity of bleeding is usually similar in members of a single family. Many patients are asymptomatic until the hemostatic system is stressed by surgery or trauma. Treatment is similar to that for hemophilia A. 286.1 is a specific code that can be used to specify a diagnosis 286.1 contains 11 index entries View the ICD-9-CM Volume 1 286.* hierarchy Alternate Terminology Christmas disease Deficiency: factor IX (functional) plasma thromboplastin component [PTC] Hemophilia B  Index entries containing 286.1: Christmas disease 286.1 Deficiency, deficient antihemophilic factor (A) 286.0 B 286.1 autoprothrombin II 286.1 Christmas factor 286.1 factor (see also Defect, coagulation) 286.9 IX (Christmas) (congenital) (functional) 286.1 plasma thromboplastin component (PTC) 286.1 PTC 286.1 Disease, diseased - see also Syndrome Christmas 286.1 Disorder - see also Disease coagulation (factor) (see also Defect, coagulation) 286.9 factor IX (congenital) (functional) 286.1 factor, coagulation (see also Defect, coagulation) 286.9 IX (congenital) (functional) 286.1 Hemophilia (familial) (hereditary) 286.0 B (Leyden) 286.1