classic hemophilia resulting from a deficiency of factor VIII; an inherited disorder of blood coagulation characterized by a permanent tendency to hemorrhage.
An inherited deficiency of coagulation Factor VIII characterized by the tendency to spontaneous or exaggerated post-traumatic hemorrhage. Inherited as an x-linked recessive disease, hemophilia A is the most common hemophilia, occurring in approximately 1 in 10,000 male births. --2004
Group of hereditary disorders in which affected individuals fail to make enough of certain proteins needed to form blood clots.
A deficiency or abnormality of a blood coagulation factor characterized by the tendency to spontaneous or exaggerated post-traumatic hemorrhage, Hemophilia is typically a hereditary disorder but, rarely, may be acquired. Inherited coagulation factor-deficient hemophilias include hemophilia A or classic hemophilia (Factor VIII deficiency) hemophilia B or Christmas disease (Factor IX deficiency), and hemophilia C (Factor XI deficiency). In individuals without hereditary hemophilia A, Factor VIII inhibitors may occur spontaneously as autoantibodies, resulting in a condition known as 'acquired hemophilia.' Approximately 10 % of patients with acquired hemophilia have an underlying malignancy. --2004
Excludes
factor VIII deficiency with vascular defect (286.4)
Also applicable to/known as
Antihemophilic globulin [AHG] deficiency
Factor VIII (functional) deficiency
Hemophilia:
NOS
A
classical
familial
hereditary
Subhemophilia
ICD-9-CM Volume 2 Index Entries That Refer To 286.0
2009 ICD-9-CM Diagnosis Code 286.0
286.0
