Specific code 2014 ICD-9-CM Diagnosis Code 283.2
Hemoglobinuria due to hemolysis from external causes
  • Billable Code
  • Short description: Hemolytic hemoglobinuria.
  • ICD-9-CM 283.2 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 283.2 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Extrinsic hemoglobinuria
  • Hemoglobinuria - external causation
  • Hemoglobinuria, extrinsic
  • Paroxsymal nocturia hemoglobinuria
  • Paroxysmal nocturnal hemoglobinuria
Clinical Information
  • Disorder characterized by intravascular hemolysis and hemoglobinuria; some cases occur on exposure to cold and are due to the presence of an autohemolysin in the serum; other cases are more marked during or immediately after sleep and are considered to be due to an acquired intracorpuscular defect.
Applies To
  • Acute intravascular hemolysis
  • Hemoglobinuria:
    • from exertion
    • march
    • paroxysmal (cold) (nocturnal)
    • due to other hemolysis
  • Marchiafava-Micheli syndrome
Use Additional
  • Use additional E code to identify cause
Convert to ICD-10-CM: 283.2 converts approximately to:
  • 2014 ICD-10-CM D59.5 Paroxysmal nocturnal hemoglobinuria [Marchiafava-Micheli]
    Or:
  • 2014 ICD-10-CM D59.6 Hemoglobinuria due to hemolysis from other external causes
    Or:
  • 2014 ICD-10-CM D59.8 Other acquired hemolytic anemias
ICD-9-CM Volume 2 Index entries containing back-references to 283.2:
  • Anemia 285.9
    • hemolytic 283.9
      • acquired 283.9
        • with hemoglobinuria NEC 283.2
        • autoimmune (cold type) (idiopathic) (primary) (secondary) (symptomatic) (warm type) 283.0
        • due to
          • cold reactive antibodies 283.0
          • drug exposure 283.0
          • warm reactive antibodies 283.0
        • fragmentation 283.19
        • idiopathic (chronic) 283.9
        • infectious 283.19
        • non-autoimmune 283.10
        • toxic 283.19
        • traumatic cardiac 283.19
      • acute 283.9
        • due to enzyme deficiency NEC 282.3
        • fetus or newborn (see also Disease, hemolytic) 773.2
        • Lederer's (acquired infectious hemolytic anemia) 283.19
      • autoimmune (acquired) 283.0
      • chronic 282.9
      • cold type (secondary) (symptomatic) 283.0
      • congenital (spherocytic) (see also Spherocytosis) 282.0
        • nonspherocytic - see Anemia, hemolytic, nonspherocytic, congenital
      • drug-induced 283.0
      • due to
        • cardiac conditions 283.19
        • drugs 283.0
        • enzyme deficiency NEC 282.3
        • presence of shunt or other internal prosthetic device 283.19
        • thrombotic thrombocytopenic purpura 446.6
      • elliptocytotic (see also Elliptocytosis) 282.1
      • familial 282.9
      • hereditary 282.9
        • due to enzyme deficiency NEC 282.3
        • specified NEC 282.8
      • idiopathic (chronic) 283.9
      • infectious (acquired) 283.19
      • mechanical 283.19
      • microangiopathic 283.19
      • nonautoimmune 283.10
      • nonspherocytic
      • of or complicating pregnancy 648.2
      • resulting from presence of shunt or other internal prosthetic device 283.19
      • secondary 283.19
      • sickle-cell - see Disease, sickle-cell
      • Stransky-Regala type (Hb-E) (see also Disease, hemoglobin) 282.7
      • symptomatic 283.19
      • toxic (acquired) 283.19
      • uremic (adult) (child) 283.11
      • warm type (secondary) (symptomatic) 283.0
  • Cold 460
    • agglutinin
      • disease (chronic) or syndrome 283.0
      • hemoglobinuria 283.0
        • paroxysmal (cold) (nocturnal) 283.2
  • Disease, diseased - see also Syndrome
    • cold
      • agglutinin 283.0
        • or hemoglobinuria 283.0
          • paroxysmal (cold) (nocturnal) 283.2
      • hemagglutinin (chronic) 283.0
    • Harley's (intermittent hemoglobinuria) 283.2
    • Murri's (intermittent hemoglobinuria) 283.2
  • Harley's disease (intermittent hemoglobinuria) 283.2
  • Hematinuria (see also Hemoglobinuria) 791.2
    • paroxysmal 283.2
  • Hemoglobinemia 283.2
    • paroxysmal 283.2
  • Hemoglobinuria, hemoglobinuric 791.2
    • with anemia, hemolytic, acquired (chronic) NEC 283.2
    • cold (agglutinin) (paroxysmal) (with Raynaud's syndrome) 283.2
    • due to
      • exertion 283.2
      • hemolysis (from external causes) NEC 283.2
    • exercise 283.2
    • intermittent 283.2
    • march 283.2
    • nocturnal (paroxysmal) 283.2
    • paroxysmal (cold) (nocturnal) 283.2
  • Hemolysis
    • intravascular (disseminated) NEC 286.6
      • with
        • abortion - see Abortion, by type, with hemorrhage, delayed or excessive
        • ectopic pregnancy (see also categories 633.0-633.9) 639.1
        • hemorrhage of pregnancy 641.3
          • affecting fetus or newborn 762.1
        • molar pregnancy (see also categories 630-632) 639.1
      • acute 283.2
      • following
  • March
    • hemoglobinuria 283.2
  • Marchiafava-Micheli syndrome (paroxysmal nocturnal hemoglobinuria) 283.2
  • Murri's disease (intermittent hemoglobinuria) 283.2
  • Syndrome - see also Disease
    • Dressler's (postmyocardial infarction) 411.0
      • hemoglobinuria 283.2
      • postcardiotomy 429.4
    • Marchiafava-Micheli (paroxysmal nocturnal hemoglobinuria) 283.2
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 283.2 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.