Specific code 2014 ICD-9-CM Diagnosis Code 282.0
Hereditary spherocytosis
  • Billable Code
  • ICD-9-CM 282.0 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 282.0 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Spherocytosis, hereditary
Clinical Information
  • Autosomal dominant trait marked by splenomegaly, jaundice, and fragile, spheroid erythrocytes which are prematurely cleared by the spleen; anemia is usually mild; treatment is splenectomy.
  • Includes hereditary erythrocyte membrane defects, enzyme deficiencies, hemoglobin abnormalities, stem cell defects (paroxysmal nocturnal hemoglobinuria), and alloimmune (rh) disease of newborn.
282.0 Excludes
Applies To
  • Acholuric (familial) jaundice
  • Congenital hemolytic anemia (spherocytic)
  • Congenital spherocytosis
  • Minkowski-Chauffard syndrome
  • Spherocytosis (familial)
Convert to ICD-10-CM: 282.0 converts directly to:
  • 2014 ICD-10-CM D58.0 Hereditary spherocytosis
ICD-9-CM Volume 2 Index entries containing back-references to 282.0:
  • Acholuric jaundice (familial) (splenomegalic) (see also Spherocytosis) 282.0
  • Anemia 285.9
    • congenital (following fetal blood loss) 776.5
      • aplastic 284.01
      • due to isoimmunization NEC 773.2
      • Heinz-body 282.7
      • hereditary hemolytic NEC 282.9
      • nonspherocytic
      • pernicious 281.0
      • spherocytic (see also Spherocytosis) 282.0
    • hemolytic 283.9
      • acquired 283.9
        • with hemoglobinuria NEC 283.2
        • autoimmune (cold type) (idiopathic) (primary) (secondary) (symptomatic) (warm type) 283.0
        • due to
          • cold reactive antibodies 283.0
          • drug exposure 283.0
          • warm reactive antibodies 283.0
        • fragmentation 283.19
        • idiopathic (chronic) 283.9
        • infectious 283.19
        • non-autoimmune 283.10
        • toxic 283.19
        • traumatic cardiac 283.19
      • acute 283.9
        • due to enzyme deficiency NEC 282.3
        • fetus or newborn (see also Disease, hemolytic) 773.2
        • Lederer's (acquired infectious hemolytic anemia) 283.19
      • autoimmune (acquired) 283.0
      • chronic 282.9
      • cold type (secondary) (symptomatic) 283.0
      • congenital (spherocytic) (see also Spherocytosis) 282.0
        • nonspherocytic - see Anemia, hemolytic, nonspherocytic, congenital
      • drug-induced 283.0
      • due to
        • cardiac conditions 283.19
        • drugs 283.0
        • enzyme deficiency NEC 282.3
        • presence of shunt or other internal prosthetic device 283.19
        • thrombotic thrombocytopenic purpura 446.6
      • elliptocytotic (see also Elliptocytosis) 282.1
      • familial 282.9
      • hereditary 282.9
        • due to enzyme deficiency NEC 282.3
        • specified NEC 282.8
      • idiopathic (chronic) 283.9
      • infectious (acquired) 283.19
      • mechanical 283.19
      • microangiopathic 283.19
      • nonautoimmune 283.10
      • nonspherocytic
      • of or complicating pregnancy 648.2
      • resulting from presence of shunt or other internal prosthetic device 283.19
      • secondary 283.19
      • sickle-cell - see Disease, sickle-cell
      • Stransky-Regala type (Hb-E) (see also Disease, hemoglobin) 282.7
      • symptomatic 283.19
      • toxic (acquired) 283.19
      • uremic (adult) (child) 283.11
      • warm type (secondary) (symptomatic) 283.0
    • spherocytic (hereditary) (see also Spherocytosis) 282.0
  • Disease, diseased - see also Syndrome
    • Holla (see also Spherocytosis) 282.0
  • Holla disease (see also Spherocytosis) 282.0
  • Icteroanemia, hemolytic (acquired) 283.9
    • congenital (see also Spherocytosis) 282.0
  • Icterus (see also Jaundice) 782.4
    • hemolytic (acquired) 283.9
      • congenital (see also Spherocytosis) 282.0
  • Jaundice (yellow) 782.4
    • acholuric (familial) (splenomegalic) (see also Spherocytosis) 282.0
    • hemolytic (acquired) 283.9
      • congenital (see also Spherocytosis) 282.0
  • Minkowski-Chauffard syndrome (see also Spherocytosis) 282.0
  • Spherocytosis (congenital) (familial) (hereditary) 282.0
  • Syndrome - see also Disease
    • Minkowski-Chauffard (see also Spherocytosis) 282.0
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 282.0 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.