Specific code 2015 ICD-9-CM Diagnosis Code 757.39
Other specified anomalies of skin
  • 2015
  • Billable Thru Sept 30/2015
  • Non-Billable On/After Oct 1/2015

  • ICD-9-CM 757.39 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 757.39 should only be used for claims with a date of service on or before September 30, 2015. For claims with a date of service on or after October 1, 2015, use an equivalent ICD-10-CM code (or codes).
Convert to ICD-10-CM: 757.39 converts approximately to:
  • 2015/16 ICD-10-CM Q81.9 Epidermolysis bullosa, unspecified
    Or:
  • 2015/16 ICD-10-CM Q82.8 Other specified congenital malformations of skin
Approximate Synonyms
  • Abnl gluteal crease
  • Abnormal gluteal crease
  • Accessory skin tag, congenital
  • Acquired epidermolysis bullosa
  • Acquired perforating pseudoxanthoma elasticum
  • Acquired pseudoxanthoma elasticum
  • Acral Darier's disease
  • Acroerythrokeratoderma
  • Acrokeratosis paraneoplastica of Bazex
  • Acrokeratosis verruciformis
  • Acrokeratosis verruciformis of Darier disease
  • Acrokeratosis verruciformis of Hopf
  • Acrokeratosis verruciforms
  • ACROKERATOSIS VERRUCIFORMS (disorder)
  • Acromegaloid phenotype with cutis verticis gyrata and corneal leukoma
  • Adult junctional epidermolysis bullosa
  • Aplasia cutis
  • Aplasia cutis congenita
  • Aplasia cutis congenita due to teratogenic drug
  • Aplasia cutis congenita due to underlying malformation
  • Aplasia cutis congenita following intra-uterine infection
  • Aplasia cutis congenita in association with epidermolysis bullosa
  • Aplasia cutis congenita secondary to malformation syndrome
  • Aplasia cutis in Chromosome 4 short-arm deletion syndrome
  • Aplasia cutis in Johanson-Blizzard syndrome
  • Aplasia cutis in Trisomy 13 syndrome
  • Aplasia of skin
  • Arteriovenous malformation of skin
  • Autosomal dominant epidermolysis bullosa simplex
  • Autosomal dominant mutilating keratoderma
  • Autosomal dominant pseudoxanthoma elasticum
  • Autosomal recessive pseudoxanthoma elasticum
  • Bloom syndrome
  • Brugsch's syndrome
  • Bullous eruption of hand
  • Cicatricial junctional epidermolysis bullosa
  • Circumscribed palmoplantar keratoderma
  • Congenital absence of skin on scalp
  • Congenital absence of skin on scalp with epidermal nevi
  • Congenital accessory skin tag
  • Congenital junctional epidermolysis bullosa
  • Congenital junctional epidermolysis bullosa-pyloric atresia syndrome
  • Congenital keratoderma
  • Congenital keratosis follicularis
  • Congenital keratosis pilaris
  • Congenital palmoplantar and perioral keratoderma of Olmsted
  • Congenital scar
  • Congenital skin contracture
  • Conjunctivitis associated with epidermolysis bullosa
  • Cutaneous lesion resulting from spinal dysraphism
  • Cutis verticis gyrata
  • Cutis verticis gyrata with acromegaloid phenotype
  • Darier disease
  • Dariers disease
  • Deoxyribonucleic acid instability syndrome
  • Diffuse palmoplantar keratoderma of Thost-Unna
  • Disorder of apocrine secretion
  • Dominant dystrophic epidermolysis bullosa
  • Dominant dystrophic epidermolysis bullosa with absence of skin
  • Dominant dystrophic epidermolysis bullosa, albopapular type
  • Dominant epidermolysis bullosa simplex, Weber-Cockayne type
  • Drug induced epidermolysis bullosa
  • Drug-induced epidermolysis bullosa acquisita
  • Drug-induced pseudoxanthoma elasticum
  • Dyskeratosis congenita
  • Dystrophic epidermolysis bullosa
  • Dystrophic epidermolysis bullosa inverse type
  • Emotional sweating affecting palms and soles
  • Epidermolysis bullosa
  • Epidermolysis bullosa acquisita, Brunsting-Perry type
  • Epidermolysis bullosa acquisita, bullous pemphigoid-like
  • Epidermolysis bullosa acquisita, cicatricial pemphigoid-like
  • Epidermolysis bullosa acquisita, classical acral type
  • Epidermolysis bullosa acquisita, oral mucosal involvement
  • Epidermolysis bullosa dystrophica
  • Epidermolysis bullosa letalis
  • Epidermolysis bullosa pruriginosa
  • Epidermolysis bullosa simplex
  • Epidermolysis bullosa simplex of the hands AND/OR feet
  • Epidermolysis bullosa simplex with hypodontia
  • Epidermolysis bullosa simplex with mottled pigmentation
  • Epidermolysis bullosa simplex with neuromuscular disease
  • Epidermolysis bullosa simplex, Ogna type
  • Epidermolysis simplex superficialis
  • Epidermolytic palmoplantar keratoderma of Vorner
  • Erythrokeratoderma
  • Erythrokeratoderma progressiva of Gottron
  • Familial benign pemphigus
  • Familial dyskeratotic comedones
  • Flegels disease
  • Flexural Darier's disease
  • Focal dermal hypoplasia
  • Generalized dystrophic epidermolysis bullosa
  • Generalized epidermolysis bullosa simplex
  • Generalized junctional epidermolysis bullosa
  • Generalized recessive dystrophic epidermolysis bullosa mitis
  • Generalized recessive non-mutilating dystrophic epidermolysis bullosa
  • Giant porokeratosis
  • Goltz Gorlin syndrome
  • Goltz syndrome
  • Goltz-Gorlin (dermal hypoplasia) syndrome
  • Gronblad-Strandberg syndrome
  • Hailey disease
  • Hailey Hailey disease
  • Hereditary acantholytic dermatosis
  • Hereditary benign acanthosis nigricans
  • Hereditary benign acanthosis nigricans with insulin resistance
  • Hereditary diffuse palmoplantar keratoderma
  • Hereditary erythrokeratolysis
  • Hereditary follicular keratoses
  • Hereditary palmoplantar keratoderma
  • Howel Evans syndrome
  • Howel-Evans' syndrome
  • Hyperkeratosis lenticularis perstans
  • Hypertrophic Darier's disease
  • Hypotrichosis with keratosis pilaris and lentiginosis
  • Hystrix ichthyosis with deafness
  • Ichthyosis hystrix
  • Ichthyosis hystrix gravior of Rheydt
  • Ichthyosis hystrix of Curth-Macklin
  • Inherited disorder of keratinization
  • Inherited epidermolysis bullosa
  • Inherited pseudoxanthoma elasticum
  • Inverse junctional epidermolysis bullosa
  • Junctional epidermolysis bullosa
  • Junctional epidermolysis bullosa gravis of Herlitz
  • Junctional epidermolysis bullosa mitis
  • Juvenile elastoma
  • Keratoderma areata
  • Keratoderma due to Dowling-Meara type epidermolysis bullosa simplex
  • Keratoderma plantare sulcata
  • Keratoderma with deafness
  • Keratoderma with mental retardation and spastic paraplegia
  • Keratoderma with pachyonychia congenita
  • Keratoderma with scleroatrophy of the extremities
  • Keratoderma, congenital
  • Keratolysis exfoliativa
  • Keratosis follicularis
  • Keratosis pilaris atrophicans
  • Keratosis pilaris decalvans
  • Keratosis pilaris with ichthyosis and deafness
  • Keratosis pilaris, congenital
  • Keratosis rubra pilaris
  • Lethal autosomal recessive epidermolysis bullosa simplex
  • Lichen spinulosus
  • Linear porokeratosis
  • Linear/nevoid/zosteriform Darier's disease
  • Livedo telangiectatica
  • Localized dystrophic epidermolysis bullosa
  • Localized junctional epidermolysis bullosa
  • Localized recessive dystrophic epidermolysis bullosa
  • Lymphedematous keratoderma
  • Maleformatio ectodermalis generalisata of Bafverstedt
  • Mutilating keratoderma
  • Nail dystrophy due to Darier's disease
  • Nevus lipomatosus cutaneous superficialis
  • Pachydermoperiostosis - familial
  • Palmar pitting due to Darier's disease
  • Palmoplantar keratoderma transgrediens
  • Palmoplantar keratoderma with leukoplakia
  • Papuloverrucous palmoplantar keratoderma of Jakac-Wolf
  • Porcupine man
  • Porokeratosis
  • Porokeratosis (skin condition)
  • Porokeratosis of Mantoux
  • Porokeratosis of Mibelli
  • Porokeratosis of Mibelli, linear unilateral type
  • Porokeratosis of Mibelli, plaque type
  • Porokeratosis of Mibelli, superficial disseminated type
  • Pretibial epidermolysis bullosa
  • Progressive junctional epidermolysis bullosa
  • Progressive palmoplantar keratoderma of Greither
  • Progressive recessive dystrophic epidermolysis bullosa
  • Proteus syndrome
  • Pseudoxanthoma elasticum
  • Recessive dystrophic epidermolysis bullosa
  • Relapsing linear acantholytic dermatosis
  • Sacral dimple
  • Scar, congenital
  • Symmetrical keratoderma
  • Xeroderma in genetic syndrome
Clinical Information
  • Inherited chronic noninflammatory skin disease manifested by vesicles, large bullae (blisters), and skin erosions which often result from trauma
757.39 Excludes
Applies To
  • Accessory skin tags, congenital
  • Congenital scar
  • Epidermolysis bullosa
  • Keratoderma (congenital)
ICD-9-CM Volume 2 Index entries containing back-references to 757.39:
  • Absence (organ or part) (complete or partial)
    • skin (congenital) 757.39
  • Acantholysis 701.8
    • bullosa 757.39
  • Acanthosis (acquired) (nigricans) 701.2
    • benign (congenital) 757.39
    • congenital 757.39
  • Accessory (congenital)
    • skin tags 757.39
  • Acrokeratosis verruciformis 757.39
  • Acropachyderma 757.39
  • Anomaly, anomalous (congenital) (unspecified type) 759.9
    • skin (appendage) 757.9
      • specified type NEC 757.39
  • Aplasia - see also Agenesis
    • skin (congenital) 757.39
  • Audry's syndrome (acropachyderma) 757.39
  • Bloom (-Machacek) (-Torre) syndrome 757.39
  • Brugsch's syndrome (acropachyderma) 757.39
  • Chalazoderma 757.39
  • Cicatrix (adherent) (contracted) (painful) (vicious) 709.2
    • congenital 757.39
  • Cockayne-Weber syndrome (epidermolysis bullosa) 757.39
  • Cutis - see also condition
    • verticis gyrata 757.39
  • Darier's disease (congenital) (keratosis follicularis) 757.39
    • due to vitamin A deficiency 264.8
    • meaning erythema annulare centrifugum 695.0
  • Dermatolysis (congenital) (exfoliativa) 757.39
  • Disease, diseased - see also Syndrome
    • Darier's (congenital) (keratosis follicularis) 757.39
      • erythema annulare centrifugum 695.0
      • vitamin A deficiency 264.8
    • Goldscheider's (epidermolysis bullosa) 757.39
    • Gougerot-Hailey-Hailey (benign familial chronic pemphigus) 757.39
    • Hailey-Hailey (benign familial chronic pemphigus) 757.39
    • Köbner's (epidermolysis bullosa) 757.39
    • Marie-Bamberger (hypertrophic pulmonary osteoarthropathy) (secondary) 731.2
      • primary or idiopathic (acropachyderma) 757.39
      • pulmonary (hypertrophic osteoarthropathy) 731.2
    • Meleda 757.39
    • Mibelli's 757.39
    • Mljet (mal de Meleda) 757.39
    • White's (congenital) (keratosis follicularis) 757.39
  • Dyskeratosis (see also Keratosis) 701.1
    • bullosa hereditaria 757.39
    • congenital 757.39
    • follicularis 757.39
      • vitamin A deficiency 264.8
  • Elastoma 757.39
    • juvenile 757.39
    • Miescher's (elastosis perforans serpiginosa) 701.1
  • Epidermolysis
    • bullosa 757.39
  • Friedrich-Erb-Arnold syndrome (acropachyderma) 757.39
  • Goldscheider's disease (epidermolysis bullosa) 757.39
  • Goltz-Gorlin syndrome (dermal hypoplasia) 757.39
  • Gougerot-Hailey-Hailey disease (benign familial chronic pemphigus) 757.39
  • Gyrate scalp 757.39
  • Hailey-Hailey disease (benign familial chronic pemphigus) 757.39
  • Hydromphalus (congenital) (since birth) 757.39
  • Hyperkeratosis (see also Keratosis) 701.1
    • congenital 757.39
    • eccentrica 757.39
    • figurata centrifuga atrophica 757.39
    • follicularis 757.39
  • Hypoplasia, hypoplasis 759.89
    • dermal, focal (Goltz) 757.39
    • focal dermal 757.39
    • skin 757.39
  • Ichthyosis (congenita) 757.1
    • hystrix 757.39
    • palmaris and plantaris 757.39
  • Keratoderma, keratodermia (congenital) (palmaris et plantaris) (symmetrical) 757.39
    • eccentrica 757.39
    • tylodes, progressive 701.1
  • Keratolysis exfoliativa (congenital) 757.39
    • neonatorum 757.39
  • Keratoma 701.1
    • congenital 757.39
    • palmaris et plantaris hereditarium 757.39
  • Keratosis 701.1
    • congenital (any type) 757.39
    • follicularis 757.39
      • acquired 701.1
      • congenital (acneiformis) (Siemens') 757.39
      • spinulosa (decalvans) 757.39
      • vitamin A deficiency 264.8
    • nigricans 701.2
      • congenital 757.39
    • palmaris et plantaris (symmetrical) 757.39
    • pilaris 757.39
    • suprafollicularis 757.39
    • vegetans 757.39
  • Köbner's disease (epidermolysis bullosa) 757.39
  • Lichen 697.9
    • pilaris 757.39
    • spinulosus 757.39
  • Mal
    • de Meleda 757.39
  • Marie-Bamberger disease or syndrome (hypertrophic) (pulmonary) (secondary) 731.2
    • idiopathic (acropachyderma) 757.39
    • primary (acropachyderma) 757.39
  • Megalia, cutis et ossium 757.39
  • Mibelli's disease 757.39
  • Mljet disease (mal de Meleda) 757.39
  • Osteoarthropathy (see also Osteoarthrosis) 715.9
    • chronic idiopathic hypertrophic 757.39
    • familial idiopathic 757.39
    • idiopathic hypertrophic 757.39
  • Osteosis
    • acromegaloid 757.39
  • Pachydermatocele (congenital) 757.39
  • Pachydermoperiostosis
    • primary idiopathic 757.39
  • Pachyperiosteodermia
    • primary or idiopathic 757.39
  • Pachyperiostosis
    • primary or idiopathic 757.39
  • Particolored infant 757.39
  • Pemphigus 694.4
    • benign 694.5
      • chronic familial 757.39
    • congenital, traumatic 757.39
  • Pityriasis 696.5
  • Porokeratosis 757.39
    • disseminated superficial actinic (DSAP) 692.75
  • Pseudoxanthoma elasticum 757.39
  • Psorospermosis 136.4
    • follicularis (vegetans) 757.39
  • Roy (-Jutras) syndrome (acropachyderma) 757.39
  • Sauriderma 757.39
  • Scar, scarring (see also Cicatrix) 709.2
    • congenital 757.39
  • Siemens' syndrome
    • keratosis follicularis spinulosa (decalvans) 757.39
  • Syndrome - see also Disease
    • Audry's (acropachyderma) 757.39
    • Bloom (-Machacek) (-Torre) 757.39
    • Brugsch's (acropachyderma) 757.39
    • Cockayne-Weber (epidermolysis bullosa) 757.39
    • FDH (focal dermal hypoplasia) 757.39
    • Friedrich-Erb-Arnold (acropachyderma) 757.39
    • Goltz-Gorlin (dermal hypoplasia) 757.39
    • Marie's (acromegaly) 253.0
      • primary or idiopathic (acropachyderma) 757.39
      • secondary (hypertrophic pulmonary osteoarthropathy) 731.2
    • osteodermopathic hyperostosis 757.39
    • Proteus (dermal hypoplasia) 757.39
    • Roy (-Jutras) (acropachyderma) 757.39
    • Siemens'
      • ectodermal dysplasia 757.31
      • keratosis follicularis spinulosa (decalvans) 757.39
    • Touraine-Solente-Golé (acropachyderma) 757.39
    • Uehlinger's (acropachyderma) 757.39
    • Weber-Cockayne (epidermolysis bullosa) 757.39
  • Tag (hypertrophied skin) (infected) 701.9
  • Touraine-Solente-Golé syndrome (acropachyderma) 757.39
  • Tumor (M8000/1) - see also Neoplasm, by site, unspecified nature
    • White-Darier 757.39
  • Tylosis 700
    • palmaris et plantaris 757.39
  • Uehlinger's syndrome (acropachyderma) 757.39
  • Urticaria 708.9
    • perstans hemorrhagica 757.39
  • Weber-Cockayne syndrome (epidermolysis bullosa) 757.39
  • White's disease (congenital) (keratosis follicularis) 757.39
  • Xeroderma (congenital) 757.39
    • vitamin A deficiency 264.8
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 757.39 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2015 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.