Specific code 2011 ICD-9-CM Diagnosis Code 277.87
Disorders of mitochondrial metabolism
  • Short description: Dis mitochondrial metab.
  • ICD-9-CM 277.87 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 277.87 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
  • You are viewing the 2011 version of ICD-9-CM 277.87.
  • More recent version(s) of ICD-9-CM 277.87: 2012 2013 2014.
Disease Synonyms
  • Bilat Kearns-Sayre syndrome
  • Bilateral Kearns-Sayre syndrome
  • Defect, mitochondrial metabolism
  • Disorder of mitochondrial respiratory chain complexes
  • Juvenile myopathy, encephalopathy, lactic acidosis AND stroke
  • Kearns sayre syndrome
  • Kearns-Sayre syndrome
  • Kearns-Sayre syndrome, both eyes
  • L Kearns-Sayre syndrome
  • Left Kearns-Sayre syndrome
  • Mitochondrial disorder, respiratory chain
  • Mitochondrial encephalopathy, lactic acidosis, and stroke like episodes
  • Mitochondrial encephalopathy, lactic acidosis, stroke
  • Mitochondrial metabolism defect
  • Mitochondrial metabolism disorder
  • Mitochondrial mutation
  • Mitochondrial myopathy
  • Mitochondrial respiratory chain disorder
  • Myoclonus epilepsy AND ragged red fibers
  • Myoclonus epilepsy and ragged red fibers syndrome
  • Myopathy, mitochondrial
  • Neurogenic muscle weakness, ataxia and retinitis pigmentosa
  • Pearson's syndrome
  • R Kearns-Sayre syndrome
  • Right Kearns-Sayre syndrome
277.87 Excludes
  • disorders of pyruvate metabolism (271.8)
  • Leber's optic atrophy (377.16)
  • Leigh's subacute necrotizing encephalopathy (330.8)
  • Reye's syndrome (331.81)
Applies To
  • Kearns-Sayre syndrome
  • Mitochondrial Encephalopathy, Lactic Acidosis and Stroke-like episodes (MELAS syndrome)
  • Mitochondrial Neurogastrointestinal Encephalopathy syndrome (MNGIE)
  • Myoclonus with Epilepsy and with Ragged Red Fibers (MERRF syndrome)
  • Neuropathy, Ataxia and Retinitis Pigmentosa (NARP syndrome)
Use Additional
  • Use additional code for associated conditions
Convert to ICD-10-CM: 277.87 converts approximately to:
  • 2014 ICD-10-CM E88.40 Mitochondrial metabolism disorder, unspecified
    Or:
  • 2014 ICD-10-CM E88.41 MELAS syndrome
    Or:
  • 2014 ICD-10-CM E88.42 MERRF syndrome
    Or:
  • 2014 ICD-10-CM E88.49 Other mitochondrial metabolism disorders
    Or:
  • 2014 ICD-10-CM H49.819 Kearns-Sayre syndrome, unspecified eye
ICD-9-CM Volume 2 Index entries containing back-references to 277.87:
  • Disorder - see also Disease
    • mitochondrial metabolism 277.87
  • Fukuhara syndrome 277.87
  • Kearns-Sayre syndrome 277.87
  • MELAS syndrome (mitochondrial encephalopathy, lactic acidosis and stroke-like episodes) 277.87
  • MERRF syndrome (myoclonus with epilepsy and with ragged red fibers) 277.87
  • Mitochondrial encephalopathy, lactic acidosis and stroke-like episodes (MELAS syndrome) 277.87
  • Mitochondrial neurogastrointestinal encephalopathy syndrome (MNGIE) 277.87
  • Myoclonus (familial essential) (multifocal) (simplex) 333.2
    • with epilepsy and with ragged red fibers (MERRF syndrome) 277.87
  • NARP (ataxia and retinitis pigmentosa syndrome) 277.87
  • Neuropathy, neuropathic (see also Disorder, nerve) 355.9
    • ataxia and retinitis pigmentosa (NARP syndrome) 277.87
  • Syndrome - see also Disease
    • Fukuhara 277.87
    • Kearns-Sayre 277.87
    • MELAS (mitochondrial encephalopathy, lactic acidosis and stroke-like episodes) 277.87
    • MERRF (myoclonus with epilepsy and with ragged red fibers) 277.87
    • mitochondrial neurogastrointestinal encephalopathy (MNGIE) 277.87
    • MNGIE (mitochondrial neurogastrointestinal encephalopathy) 277.87
    • NARP (neuropathy, ataxia and retinitis pigmentosa) 277.87
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 277.87 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2011 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.