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2008 ICD-9-CM Volume 1 Diagnosis Codes Home > Diseases Of The Nervous System And Sense Organs 320-389 > Disorders Of The Peripheral Nervous System 350-359 > Hereditary And Idiopathic Peripheral Neuropathy 356.* >

2008 ICD-9-CM Diagnosis 356.1

Peroneal muscular atrophy

  • A group of slowly progressive inherited disorders affecting motor and sensory peripheral nerves. Subtypes include HMSNs I-VII. HMSN I and II both refer to CHARCOT-MARIE-TOOTH DISEASE. HMSN III refers to hypertrophic neuropathy of infancy, HMSN IV refers to REFSUM DISEASE, HMSN V refers to a condition marked by a hereditary motor and sensory neuropathy associated with spastic paraplegia (see SPASTIC PARAPLEGIA, HEREDITARY). HMSN VI refers to HMSN associated with an inherited optic atrophy (OPTIC ATROPHIES, HEREDITARY), and HMSN VII refers to HMSN associated with retinitis pigmentosa. (From Adams et al., Principles of Neurology, 6th ed, p1343)
  • A hereditary motor and sensory neuropathy transmitted most often as an autosomal dominant trait and characterized by progressive distal wasting and loss of reflexes in the muscles of the legs (and occasionally involving the arms). Onset is usually in the second to fourth decade of life. This condition has been divided into two subtypes, hereditary motor and sensory neuropathy (HMSN) types I and II. HMSN I is associated with abnormal nerve conduction velocities and nerve hypertrophy, features not seen in HMSN II. (Adams et al., Principles of Neurology, 6th ed, p1343)
  • 356.1 is a specific code that can be used to specify a diagnosis
  • 356.1 contains 11 index entries
  • View the ICD-9-CM Volume 1 356.* hierarchy

356.1 also known as:

  • Charcot-Marie-Tooth disease
  • Neuropathic muscular atrophy


Index entries containing 356.1:

Atrophy, atrophic
  • Charcôt-Marie-Tooth 356.1
  • muscle, muscular 728.2
    • neuritic 356.1
    • neuropathic (peroneal) (progressive) 356.1
    • peroneal 356.1
Charcôt-Marie-Tooth disease, paralysis, or syndrome 356.1
Disease, diseased - see also Syndrome
  • Charcôt-Marie-Tooth 356.1
Dystrophy, dystrophia 783.9
  • muscular 359.1
    • progressive (hereditary) 359.1
      • Charcôt-Marie-Tooth 356.1
Marie-Charcôt-Tooth neuropathic atrophy, muscle 356.1
Neuropathy, neuropathic (see also Disorder, nerve) 355.9
  • hypertrophic
    • Charcôt-Marie-Tooth 356.1
Paralysis, paralytic (complete) (incomplete) 344.9
  • Charcôt-Marie-Tooth type 356.1
Syndrome - see also Disease
  • Charcôt-Marie-Tooth 356.1