Specific code 2014 ICD-9-CM Diagnosis Code 356.1
Peroneal muscular atrophy
  • Billable Code
  • Short description: Peroneal muscle atrophy.
  • ICD-9-CM 356.1 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 356.1 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Charcot Marie Tooth disease
  • Charcot Marie Tooth disease type 1
  • Charcot Marie Tooth disease, Type 1
  • Charcot Marie Tooth disease, Type 2
  • Charcot Marie Tooth disease, Type 3
  • Charcot Marie Tooth disease, Type 4
  • Charcot-Marie-Tooth disease
  • Charcot-Marie-Tooth disease type 4 (disorder)
  • Charcot-Marie-Tooth disease, type 3 (disorder)
  • Charcot-Marie-Tooth disease, type I
  • Charcot-Marie-Tooth disease, type II (disorder)
Clinical Information
  • A hereditary motor and sensory neuropathy transmitted most often as an autosomal dominant trait and characterized by progressive distal wasting and loss of reflexes in the muscles of the legs (and occasionally involving the arms). Onset is usually in the second to fourth decade of life. This condition has been divided into two subtypes, hereditary motor and sensory neuropathy (hmsn) types i and ii. Hmsn i is associated with abnormal nerve conduction velocities and nerve hypertrophy, features not seen in hmsn ii. (Adams et al., Principles of Neurology, 6th ed, p1343)
  • A progressive hereditary disorder that causes nerve damage
  • An inherited degenerative disorder involving the peripheral nerves. It is caused by mutations in the genes that are responsible for the production of proteins necessary for the function and structure of the peripheral nerves. It is characterized by muscle atrophy and weakness in the feet, legs, hands, and arms and loss of sensation in the limbs.
  • Charcot-marie-tooth disease (cmt) is a group of genetic nerve disorders. It is named after the three doctors who first identified it. In the United States, cmt affects about 1 in 3,300 people. Cmt affects your peripheral nerves. Peripheral nerves carry movement and sensation signals between the brain and spinal cord and the rest of the body. Symptoms usually start around the teen years. Foot problems such as high arches or hammertoes can be early symptoms. As cmt progresses, your lower legs may weaken. Later, your hands may also become weak. There is no cure. The disease can be so mild you don't realize you have it or severe enough to make you weak. Many people with cmt lead active lives and have a normal life span. Physical therapy, occupational therapy, braces and other devices and sometimes surgery can help you cope. genetics home reference
  • Group of peripheral nervous system hereditary disorders with varying course, symptoms, neuropathology, and genetics, but generally involving gradual loss of nerve conduction, distal wasting, deformity, and disability.
Applies To
  • Charcot-Marie-Tooth disease
  • Neuropathic muscular atrophy
Convert to ICD-10-CM: 356.1 converts approximately to:
  • 2014 ICD-10-CM G60.0 Hereditary motor and sensory neuropathy
ICD-9-CM Volume 2 Index entries containing back-references to 356.1:
  • Atrophy, atrophic
    • Charcôt-Marie-Tooth 356.1
  • Charcôt-Marie-Tooth disease, paralysis, or syndrome 356.1
  • Disease, diseased - see also Syndrome
    • Charcôt-Marie-Tooth 356.1
  • Dystrophy, dystrophia 783.9
  • Marie-Charcôt-Tooth neuropathic atrophy, muscle 356.1
  • Neuropathy, neuropathic (see also Disorder, nerve) 355.9
    • hypertrophic
      • Charcôt-Marie-Tooth 356.1
      • Déjérine-Sottas 356.0
      • interstitial 356.9
      • Refsum 356.3
  • Paralysis, paralytic (complete) (incomplete) 344.9
    • Charcôt-Marie-Tooth type 356.1
  • Syndrome - see also Disease
    • Charcôt-Marie-Tooth 356.1
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 356.1 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.