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2008 ICD-9-CM Volume 1 Diagnosis Codes Home > Diseases Of The Nervous System And Sense Organs 320-389 > Disorders Of The Peripheral Nervous System 350-359 > Muscular Dystrophies And Other Myopathies 359.* >

2008 ICD-9-CM Diagnosis 359.0

Congenital hereditary muscular dystrophy

 On October 1, 2008 the 2009 ICD-9-CM codes came into effect. Therefore, this code may be out of date.

The 2009 version of ICD-9-CM 359.0 can be accessed here.

  • A group of inherited congenital myopathic conditions characterized clinically by weakness, hypotonia, and prominent hypoplasia of proximal muscles including the face. Muscle biopsy reveals large numbers of rod-shaped structures beneath the muscle fiber plasma membrane. This disorder is genetically heterogeneous and may occasionally present in adults. (Adams et al., Principles of Neurology, 6th ed, p1453)
  • An inherited congenital myopathic condition characterized by weakness and hypotonia in infancy and delayed motor development. Muscle biopsy reveals a condensation of myofibrils and myofibrillar material in the central portion of each muscle fiber. (Adams et al., Principles of Neurology, 6th ed, p1452)
  • 359.0 is a specific code that can be used to specify a diagnosis
  • 359.0 contains 11 index entries
  • View the ICD-9-CM Volume 1 359.* hierarchy

359.0 also known as:

  • Benign congenital myopathy
  • Central core disease
  • Centronuclear myopathy
  • Myotubular myopathy
  • Nemaline body disease

359.0 excludes:

  • arthrogryposis multiplex congenita (754.89)


Index entries containing 359.0:

Disease, diseased - see also Syndrome
  • central core 359.0
  • nemaline body 359.0
Dystrophy, dystrophia 783.9
  • muscular 359.1
    • congenital (hereditary) 359.0
Hypotonia, hypotonicity, hypotony 781.3
  • infantile muscular (benign) 359.0
Myopathy 359.9
  • benign, congenital 359.0
  • central core 359.0
  • centronuclear 359.0
  • congenital (benign) 359.0
  • myotubular 359.0
  • nemaline 359.0
  • rod body 359.0