Specific code 2014 ICD-9-CM Diagnosis Code 751.3
Hirschsprung's disease and other congenital functional disorders of colon
  • Billable Code
  • Short description: Hirschsprung's disease.
  • ICD-9-CM 751.3 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 751.3 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Aganglionosis of Auerbach's plexus
  • Aganglionosis of colon
  • Congenital dilatation of colon
  • Congenital functional disorder of colon
  • Congenital functional disorders of the colon
  • Congenital macrocolon, not aganglionic
  • Congenital megacolon
  • Hirschsprungs disease
  • Hirschsprung's disease
  • Hirschsprung's disease and allied congenital conditions
  • Hyperganglionosis
  • Idiopathic congenital megacolon
  • Lethal white syndrome of foals
  • Long segment Hirschsprung's disease
  • Macrocolon
  • Megacolon, congenital
  • Short segment Hirschsprung's disease
  • Small intestinal dysmotility
  • Small left colon syndrome
  • Total colonic aganglionosis
  • Total intestinal aganglionosis
Clinical Information
  • Abnormally large or dilated colon due to congenital absence of myenteric ganglion cells in a distal segment of the large bowel; resultant loss of motor function in this segment causes massive hypertrophic dilatation of the normal proximal colon; condition appears soon after birth; called also hirschsprung's disease, aganglionic megacolon and pelvirectal achalasia.
Applies To
  • Aganglionosis
  • Congenital dilation of colon
  • Congenital megacolon
  • Macrocolon
Convert to ICD-10-CM: 751.3 converts approximately to:
  • 2014 ICD-10-CM Q43.1 Hirschsprung's disease
ICD-9-CM Volume 2 Index entries containing back-references to 751.3:
  • Achalasia 530.0
    • pelvirectal 751.3
  • Aganglionosis (bowel) (colon) 751.3
  • Dilatation
    • colon 564.7
      • congenital 751.3
      • due to mechanical obstruction 560.89
      • psychogenic 306.4
  • Disease, diseased - see also Syndrome
    • Hirschsprung's (congenital megacolon) 751.3
    • Myà's (congenital dilation, colon) 751.3
    • Ruysch's (Hirschsprung's disease) 751.3
  • Disorder - see also Disease
  • Excess, excessive, excessively
    • large
      • colon 564.7
        • congenital 751.3
      • fetus or infant 766.0
        • with obstructed labor 660.1
        • affecting management of pregnancy 656.6
        • causing disproportion 653.5
      • newborn (weight of 4500 grams or more) 766.0
      • organ or site, congenital NEC - see Anomaly, specified type NEC
  • Giant
    • colon (congenital) 751.3
  • Hirschsprung's disease or megacolon (congenital) 751.3
  • Hypertrophy, hypertrophic
  • Macrocolon (congenital) 751.3
  • Macrosigmoid 564.7
    • congenital 751.3
  • Megacolon (acquired) (functional) (not Hirschsprung's disease) 564.7
    • aganglionic 751.3
    • congenital, congenitum 751.3
    • Hirschsprung's (disease) 751.3
  • Megasigmoid 564.7
    • congenital 751.3
  • Myà's disease (congenital dilation, colon) 751.3
  • Ruysch's disease (Hirschsprung's disease) 751.3
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 751.3 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.