Specific code 2014 ICD-9-CM Diagnosis Code 334.8
Other spinocerebellar diseases
  • Billable Code
  • Short description: Spinocerebellar dis NEC.
  • ICD-9-CM 334.8 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 334.8 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Ataxia telangiectasia syndrome
  • Ataxia-telangiectasia syndrome
  • Azorean disease, type II
  • Bailey-Cushing syndrome
  • Corticostriatal spinal degeneration
  • Corticostriatal-spinal degeneration
  • Dentatorubral-pallidoluysian atrophy
  • Dentatorubral-pallidoluysian atrophy (DRPLA)
  • Dentatorubropallidoluysian degeneration (disorder)
  • Jervis' syndrome
  • Spinocerebellar ataxia, Type 1
  • Spinocerebellar ataxia, type 1 (disorder)
  • Spinocerebellar ataxia, Type 2
  • Spinocerebellar ataxia, type 2 (disorder)
  • Spinocerebellar ataxia, Type 3
  • Spinocerebellar ataxia, type 3 (disorder)
  • Spinocerebellar ataxia, Type 4
  • Spinocerebellar ataxia, type 4 (disorder)
  • Spinocerebellar ataxia, Type 5
  • Spinocerebellar ataxia, type 5 (disorder)
  • Spinocerebellar ataxia, Type 6
  • Spinocerebellar ataxia, type 6 (disorder)
  • Spinocerebellar ataxia, Type 7
  • Spinocerebellar ataxia, type 7 (disorder)
Clinical Information
  • Inherited disease characterized by onset in early childhood of progressive cerebellar ataxia, oculocutaneous telangiectasis, and severe sinopulmonary infections.
  • Rare hereditary disease characterized by extreme sensitivity to ionizing radiation or radiomimetic drugs because of a defect in dna repair. At heterozygosity is estimated to occur in more than 2% of the United States Population; heterozygotes exhibit increased radiation sensitivity and are at increased risk for several types of cancer. The normal version of the gene that is defective in at appears to activate the p53-dependent response to dna damage.
Applies To
  • Ataxia-telangiectasia [Louis-Bar syndrome]
  • Corticostriatal-spinal degeneration
Convert to ICD-10-CM: 334.8 converts approximately to:
  • 2014 ICD-10-CM G11.3 Cerebellar ataxia with defective DNA repair
    Or:
  • 2014 ICD-10-CM G11.8 Other hereditary ataxias
ICD-9-CM Volume 2 Index entries containing back-references to 334.8:
  • Ataxia, ataxy, ataxic 781.3
    • telangiectasia 334.8
  • Ataxia-telangiectasia 334.8
  • Azorean disease (of the nervous system) 334.8
  • Boder-Sedgwick syndrome (ataxia-telangiectasia) 334.8
  • Degeneration, degenerative
    • corticostriatal-spinal 334.8
  • Disease, diseased - see also Syndrome
    • Azorean (of the nervous system) 334.8
    • Machado-Joseph 334.8
    • spinocerebellar 334.9
      • specified NEC 334.8
  • Hemiatrophy 799.89
    • cerebellar 334.8
  • Louis-Bar syndrome (ataxia-telangiectasia) 334.8
  • Machado-Joseph disease 334.8
  • Syndrome - see also Disease
    • ataxia-telangiectasia 334.8
    • Boder-Sedgwick (ataxia-telangiectasia) 334.8
    • Louis-Bar (ataxia-telangiectasia) 334.8
  • Telangiectasia, telangiectasis (verrucous) 448.9
    • ataxic (cerebellar) 334.8
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 334.8 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.