Home > 2013 ICD-9-CM Diagnosis Codes > Endocrine, Nutritional And Metabolic Diseases, And Immunity Disorders 240-279 > Other Metabolic Disorders And Immunity Disorders 270-279 > Disorders of amino-acid transport and metabolism 270-
2013 ICD-9-CM Diagnosis Code 270.8
Other specified disorders of amino-acid metabolism
- ICD-9-CM 270.8 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
270.8 Alternative Terminology
- 5-oxoprolinase deficiency
- Abnormal amino acid sequence
- Alaninemia
- Aminomethyltransferase deficiency
- Aromatic amino acid decarboxylase deficiency
- Beta-hydroxyisobutyryl-coa deacylase deficiency
- Biotin- ligase deficiency
- Carnosinuria
- Cobalamin d disease
- D-2 glutaric aciduria
- Disorder of amino acid and organic acid metabolism
- Disorder of aromatic amino acid metabolism
- Disorder of beta and omega amino acid metabolism
- Disorder of catecholamine synthesis
- Disorder of creatine synthesis
- Disorder of isoleucine metabolism
- Disorder of lysine and hydroxylysine metabolism
- Disorder of phenylalanine metabolism
- Disorder of proline and/or hydroxyproline metabolism
- Disorder of propionate and/or methylmalonate metabolism
- Disorder of tetrahydrobiopterin metabolism
- Disorder of the gamma-glutamyl cycle
- Disorder of valine metabolism
- Dopamine beta-hydroxylase deficiency
- Ethanolaminosis
- Familial renal iminoglycinuria
- Gamma-glutamyltransferase deficiency
- Glucoaminophosphaturia syndrome
- Glucoaminophosphaturia syndrome with rickets
- Glutamate formiminotransferase deficiency
- Glutamate-cysteine ligase deficiency
- Glutaric aciduria
- Glutathione synthase deficiency with 5-oxoprolinuria
- Glutathionemia
- Glycoprolinuria
- Hyper-beta-alaninemia
- Hyperdicarboxylicaminoaciduria and hyperprolinemia
- Hyperhydroxyprolinemia
- Hyperprolinemia
- Iminoacidopathy
- Iminoglycinuria
- Inborn error of glutathione metabolism
- Lowe syndrome
- Lysinuric protein intolerance
- Ornithine oxo-acid aminotransferase deficiency
- Proline dehydrogenase deficiency
- Prolinuria
- Propionyl-coa carboxylase deficiency pcca complementation group
- Propionyl-coa carboxylase deficiency pccbc complementation group
- Sarcosine dehydrogenase deficiency
- Succinyl-coa acetoacetate transferase deficiency
Applies To
- Alaninemia
- Ethanolaminuria
- Glycoprolinuria
- Hydroxyprolinemia
- Hyperprolinemia
- Iminoacidopathy
- Prolinemia
- Prolinuria
- Sarcosinemia
Convert 270.8 to ICD-10-CM 

ICD-9-CM Volume 2 Index entries containing back-references to 270.8:
- Alaninemia 270.8
- Disorder - see also Disease
amino acid (metabolic) (see also Disturbance, metabolism, amino acid) 270.9

albinism 270.2

alkaptonuria 270.2

argininosuccinicaciduria 270.6

beta-amino-isobutyricaciduria 277.2

cystathioninuria 270.4

cystinosis 270.0

cystinuria 270.0

glycinuria 270.0

homocystinuria 270.4

imidazole 270.5

maple syrup (urine) disease 270.3

neonatal, transitory 775.89

oasthouse urine disease 270.2

ochronosis 270.2

phenylketonuria 270.1

phenylpyruvic oligophrenia 270.1

purine NEC 277.2

pyrimidine NEC 277.2

renal transport NEC 270.0

specified type NEC 270.8
transport NEC 270.0


renal 270.0

xanthinuria 277.2
metabolism NEC 277.9

with
alkaptonuria 270.2

amino acid (see also Disorder, amino acid) 270.9


specified type NEC 270.8

ammonia 270.6

arginine 270.6

argininosuccinic acid 270.6

basal 794.7

bilirubin 277.4

calcium 275.40

carbohydrate 271.9


specified type NEC 271.8

cholesterol 272.9

citrulline 270.6

copper 275.1

corticosteroid 255.2

cystine storage 270.0

cystinuria 270.0

fat 272.9

fatty acid oxidation 277.85

following
fructosemia 271.2

fructosuria 271.2

fucosidosis 271.8

galactose-1-phosphate uridyl transferase 271.1

glutamine 270.7

glycine 270.7

glycogen storage NEC 271.0


hepatorenal 271.0

hemochromatosis (see also Hemochromatosis) 275.03

in labor and delivery 669.0

iron 275.09

lactose 271.3

lipid 272.9

lipoprotein - see also Hyperlipemia

deficiency (familial) 272.5

lysine 270.7

magnesium 275.2

mannosidosis 271.8

mineral 275.9


specified type NEC 275.8

mitochondrial 277.87

mucopolysaccharide 277.5

nitrogen 270.9

ornithine 270.6

oxalosis 271.8

pentosuria 271.8

phenylketonuria 270.1

phosphate 275.3

phosphorus 275.3

plasma protein 273.9


specified type NEC 273.8

porphyrin 277.1

purine 277.2

pyrimidine 277.2

serine 270.7

sodium 276.9

specified type NEC 277.89

steroid 255.2

threonine 270.7

urea cycle 270.6

xylose 271.8
- Disturbance - see also Disease
metabolism (acquired) (congenital) (see also Disorder, metabolism) 277.9

with
amino acid (see also Disorder, amino acid) 270.9

ammonia 270.6

arginine 270.6

argininosuccinic acid 270.6

carbohydrate NEC 271.9

cholesterol 272.9

citrulline 270.6

cystathionine 270.4

fat 272.9

following
general 277.9

glutamine 270.7

glycine 270.7

histidine 270.5

homocystine 270.4

in labor or delivery 669.0

iron 275.09

isoleucine 270.3

leucine 270.3

lipoid 272.9


specified type NEC 272.8

lysine 270.7

methionine 270.4

neonatal, transitory 775.9


specified type NEC 775.89

nitrogen 788.99

ornithine 270.6

phosphate 275.3

phosphatides 272.7

serine 270.7

sodium NEC 276.9

threonine 270.7

tryptophan 270.2

tyrosine 270.2

urea cycle 270.6

valine 270.3
- Dystrophy, dystrophia 783.9

oculocerebrorenal 270.8
- Ethanolaminuria 270.8
- Glycoprolinuria 270.8
- Hydroxyprolinemia 270.8
- Hydroxyprolinuria 270.8
- Hyperprolinemia 270.8
- Hypersarcosinemia 270.8
- Iminoacidopathy 270.8
- Iminoglycinuria, familial 270.8
- Lowe (-Terrey-MacLachlan) syndrome (oculocerebrorenal dystrophy) 270.8
- Prolinemia 270.8
- Prolinuria 270.8
- Sarcosinemia 270.8
- Syndrome - see also Disease
fish odor 270.8
Lowe's (oculocerebrorenal dystrophy) 270.8
Lowe-Terrey-MacLachlan (oculocerebrorenal dystrophy) 270.8
- Trimethylaminuria 270.8
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 270.8 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2013 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.
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