Specific code 2013 ICD-9-CM Diagnosis Code 277.85
Disorders of fatty acid oxidation
  • Short description: Disorders acid oxidation.
  • ICD-9-CM 277.85 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 277.85 should only be used for claims with a date of service on or before September 30, 2015. For claims with a date of service on or after October 1, 2015, use an equivalent ICD-10-CM code (or codes).
  • You are viewing the 2013 version of ICD-9-CM 277.85.
  • More recent version(s) of ICD-9-CM 277.85: 2014 2015.
Convert to ICD-10-CM: 277.85 converts approximately to:
  • 2015/16 ICD-10-CM E71.310 Long chain/very long chain acyl CoA dehydrogenase deficiency
    Or:
  • 2015/16 ICD-10-CM E71.311 Medium chain acyl CoA dehydrogenase deficiency
    Or:
  • 2015/16 ICD-10-CM E71.312 Short chain acyl CoA dehydrogenase deficiency
    Or:
  • 2015/16 ICD-10-CM E71.313 Glutaric aciduria type II
    Or:
  • 2015/16 ICD-10-CM E71.314 Muscle carnitine palmitoyltransferase deficiency
    Or:
  • 2015/16 ICD-10-CM E71.318 Other disorders of fatty-acid oxidation
Approximate Synonyms
  • 2-methylbutyrylglycinuria
  • Acyl-CoA dehydrogenase deficiency
  • Carnitine palmitoyl transferase deficiency
  • Carnitine palmitoyl transferase, type 1 deficiency
  • Carnitine palmitoyl transferase, type 2 deficiency
  • Carnitine palmitoyltransferase deficiency
  • Carnitine palmitoyltransferase deficiency type 1
  • Carnitine palmitoyltransferase deficiency type 2
  • Carnitine palmitoyltransferase I deficiency
  • Carnitine palmitoyltransferase II deficiency
  • Deficiency of butyryl-CoA dehydrogenase
  • Deficiency, trifunctional protein
  • Disorder of fatty acid metabolism
  • Disorder of ketone metabolism
  • Fatty acid oxidation disorder
  • Fatty acid oxidation disorder, LCHADD
  • Fatty acid oxidation disorder, MADD
  • Fatty acid oxidation disorder, SCADD
  • Fatty acid oxidation disorder, VLCADD
  • Glutaric acidemia type 2
  • Glutaric aciduria, type 2
  • Ketone metabolism disorder
  • Long chain 3-hydroxyacyl-coa dehydrogenase deficiency
  • Long chain acyl-CoA dehydrogenase deficiency
  • Long chain fatty acid transport deficiency
  • Long-chain fatty acid transport deficiency
  • Medium chain acyl-coa dehydrogenase deficiency
  • Medium-chain acyl-coenzyme A dehydrogenase deficiency
  • Mitochondrial trifunctional protein deficiency
  • Short chain acyl-coa dehydrogenase deficiency
  • Trifunctional protein deficiency
  • Very long chain acyl-coa dehydrogenase deficiency
277.85 Excludes
  • primary carnitine deficiency (277.81)
Applies To
  • Carnitine palmitoyltransferase deficiencies (CPT1, CPT2)
  • Glutaric aciduria type II (type IIA, IIB, IIC)
  • Long chain 3-hydroxyacyl CoA dehydrogenase deficiency (LCHAD)
  • Long chain/very long chain acyl CoA dehydrogenase deficiency (LCAD, VLCAD)
  • Medium chain acyl CoA dehydrogenase deficiency (MCAD)
  • Short chain acyl CoA dehydrogenase deficiency (SCAD)
ICD-9-CM Volume 2 Index entries containing back-references to 277.85:
  • Aciduria 791.9
    • glutaric
      • type I 270.7
      • type II (type IIA, IIB, IIC) 277.85
      • type III 277.86
  • Deficiency, deficient
    • carnitine 277.81
      • due to
      • iatrogenic 277.83
      • palmitoyltransferase (CPT1, CPT2) 277.85
      • palmityl transferase (CPT1, CPT2) 277.85
      • primary 277.81
      • secondary 277.84
    • long chain 3-hydroxyacyl CoA dehydrogenase (LCHAD) 277.85
    • long chain/very long chain acyl CoA dehydrogenase (LCAD, VLCAD) 277.85
    • medium chain acyl CoA dehydrogenase (MCAD) 277.85
    • short chain acyl CoA dehydrogenase (SCAD) 277.85
  • Disorder - see also Disease
    • fatty acid oxidation 277.85
    • oxidation, fatty acid 277.85
  • LCAD (long chain/very long chain acyl CoA dehydrogenase deficiency, VLCAD) 277.85
  • LCHAD (long chain 3-hydroxyacyl CoA dehydrogenase deficiency) 277.85
  • MCAD (medium chain acyl CoA dehydrogenase deficiency) 277.85
  • Short, shortening, shortness
    • chain acyl CoA dehydrogenase deficiency (SCAD) 277.85
  • VLCAD (long chain/very long chain acyl CoA dehydrogenase deficiency, LCAD) 277.85
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 277.85 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2013 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.