- disorders affecting amino acid metabolism; majority of these disorders are inherited and present in the neonatal period with metabolic disturbances (for example, acidosis) and neurologic manifestations; present at birth, although they may not become symptomatic until later in life.
270 Disorders of amino-acid transport and metabolism convert 270 to ICD-10
270.0 Disturbances of amino-acid transport convert 270.0 to ICD-10
270.1 Phenylketonuria [PKU] convert 270.1 to ICD-10
270.2 Other disturbances of aromatic amino-acid metabolism convert 270.2 to ICD-10
270.3 Disturbances of branched-chain amino-acid metabolism convert 270.3 to ICD-10
270.4 Disturbances of sulphur-bearing amino-acid metabolism convert 270.4 to ICD-10
270.5 Disturbances of histidine metabolism convert 270.5 to ICD-10
270.6 Disorders of urea cycle metabolism convert 270.6 to ICD-10
270.7 Other disturbances of straight-chain amino-acid metabolism convert 270.7 to ICD-10
270.8 Other specified disorders of amino-acid metabolism convert 270.8 to ICD-10
270.9 Unspecified disorder of amino-acid metabolism convert 270.9 to ICD-10