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2007 ICD-9-CM Volume 1 Diagnosis Codes Home > Congenital Anomalies 740-759 > Congenital Anomalies Of The Integument 757.* >

2007 ICD-9-CM Diagnosis 757.39

Other specified congenital anomalies of skin

This code may be outdated. View the most recent version of ICD-9-CM 757.39

  • Group of genetically determined disorders characterized by the blistering of skin and mucosae. There are four major forms: acquired, simple, junctional, and dystrophic. Each of the latter three has several varieties.
  • 757.39 is a specific code that can be used to specify a diagnosis
  • 757.39 contains 119 index entries
  • View the ICD-9-CM Volume 1 757.* hierarchy

757.39 also known as:

  • Accessory skin tags, congenital
  • Congenital scar
  • Epidermolysis bullosa
  • Keratoderma (congenital)

757.39 excludes:

Index entries containing 757.39:

Absence (organ or part) (complete or partial)
  • skin (congenital) 757.39
Acantholysis 701.8
  • bullosa 757.39
Acanthosis (acquired) (nigricans) 701.2
  • benign (congenital) 757.39
  • congenital 757.39
Accessory (congenital)
  • skin tags 757.39
Acrokeratosis verruciformis 757.39
Acropachyderma 757.39
Anomaly, anomalous (congenital) (unspecified type) 759.9
  • skin (appendage) 757.9
    • specified type NEC 757.39
  • specified type NEC
    • skin 757.39
Aplasia - see also Agenesis
  • skin (congenital) 757.39
Audry's syndrome (acropachyderma) 757.39
Bloom (-Machacek) (-Torre) syndrome 757.39
Brugsch's syndrome (acropachyderma) 757.39
Chalazoderma 757.39
Cicatrix (adherent) (contracted) (painful) (vicious) 709.2
  • congenital 757.39
Cockayne-Weber syndrome (epidermolysis bullosa) 757.39
Cutis - see also condition
  • verticis gyrata 757.39
Darier's disease (congenital) (keratosis follicularis) 757.39
  • due to vitamin A deficiency 264.8
  • meaning erythema annulare centrifugum 695.0
Dermatolysis (congenital) (exfoliativa) 757.39Disease, diseased - see also Syndrome
  • Darier's (congenital) (keratosis follicularis) 757.39
    • erythema annulare centrifugum 695.0
    • vitamin A deficiency 264.8
  • Goldscheider's (epidermolysis bullosa) 757.39
  • Gougerot-Hailey-Hailey (benign familial chronic pemphigus) 757.39
  • Hailey-Hailey (benign familial chronic pemphigus) 757.39
  • Köbner's (epidermolysis bullosa) 757.39
  • Marie-Bamberger (hypertrophic pulmonary osteoarthropathy) (secondary) 731.2
    • primary or idiopathic (acropachyderma) 757.39
  • Meleda 757.39
  • Mibelli's 757.39
  • Mljet (mal de Meleda) 757.39
  • White's (congenital) (keratosis follicularis) 757.39
Dyskeratosis (see also Keratosis) 701.1
  • bullosa hereditaria 757.39
  • congenital 757.39
  • follicularis 757.39
    • vitamin A deficiency 264.8
Elastoma 757.39
  • juvenile 757.39
  • Miescher's (elastosis perforans serpiginosa) 701.1
Epidermolysis
  • bullosa 757.39
Friedrich-Erb-Arnold syndrome (acropachyderma) 757.39
Goldscheider's disease (epidermolysis bullosa) 757.39
Goltz-Gorlin syndrome (dermal hypoplasia) 757.39
Gougerot-Hailey-Hailey disease (benign familial chronic pemphigus) 757.39
Gyrate scalp 757.39
Hailey-Hailey disease (benign familial chronic pemphigus) 757.39
Hydromphalus (congenital) (since birth) 757.39
Hyperkeratosis (see also Keratosis) 701.1
  • congenital 757.39
  • eccentrica 757.39
  • figurata centrifuga atrophica 757.39
  • follicularis 757.39
Hypoplasia, hypoplasis 759.89
  • dermal, focal (Goltz) 757.39
  • focal dermal 757.39
  • skin 757.39
Ichthyosis (congenita) 757.1
  • hystrix 757.39
  • palmaris and plantaris 757.39
Keratoderma, keratodermia (congenital) (palmaris et plantaris) (symmetrical) 757.39Keratolysis exfoliativa (congenital) 757.39
  • acquired 695.89
  • neonatorum 757.39
Keratoma 701.1
  • congenital 757.39
  • palmaris et plantaris hereditarium 757.39
Keratosis 701.1
  • congenital (any type) 757.39
  • follicularis 757.39
    • acquired 701.1
    • congenital (acneiformis) (Siemens') 757.39
    • spinulosa (decalvans) 757.39
    • vitamin A deficiency 264.8
  • nigricans 701.2
    • congenital 757.39
  • palmaris et plantaris (symmetrical) 757.39
  • pilaris 757.39
  • suprafollicularis 757.39
  • vegetans 757.39
Köbner's disease (epidermolysis bullosa) 757.39
Lichen 697.9
  • pilaris 757.39
  • spinulosus 757.39
Mal
  • de Meleda 757.39
Marie-Bamberger disease or syndrome (hypertrophic) (pulmonary) (secondary) 731.2
  • idiopathic (acropachyderma) 757.39
  • primary (acropachyderma) 757.39
Megalia, cutis et ossium 757.39
Mibelli's disease 757.39
Mljet disease (mal de Meleda) 757.39
Osteoarthropathy (see also Osteoarthrosis) 715.9
  • chronic idiopathic hypertrophic 757.39
  • familial idiopathic 757.39
  • idiopathic hypertrophic 757.39
Osteosis
  • acromegaloid 757.39
Pachydermatocele (congenital) 757.39Pachydermoperiostosis
  • primary idiopathic 757.39
Pachyperiosteodermia
  • primary or idiopathic 757.39
Pachyperiostosis
  • primary or idiopathic 757.39
Particolored infant 757.39
Pemphigus 694.4
  • benign 694.5
    • chronic familial 757.39
  • congenital, traumatic 757.39
Pityriasis 696.5Porokeratosis 757.39
  • disseminated superficial actinic (DSAP) 692.75
Pseudoxanthoma elasticum 757.39
Psorospermosis 136.4
  • follicularis (vegetans) 757.39
Roy (-Jutras) syndrome (acropachyderma) 757.39
Sauriderma 757.39
Scar, scarring (see also Cicatrix) 709.2
  • congenital 757.39
Siemens' syndrome
  • keratosis follicularis spinulosa (decalvans) 757.39
Syndrome - see also Disease
  • Audry's (acropachyderma) 757.39
  • Bloom (-Machacek) (-Torre) 757.39
  • Brugsch's (acropachyderma) 757.39
  • Cockayne-Weber (epidermolysis bullosa) 757.39
  • FDH (focal dermal hypoplasia) 757.39
  • Friedrich-Erb-Arnold (acropachyderma) 757.39
  • Goltz-Gorlin (dermal hypoplasia) 757.39
  • Marie's (acromegaly) 253.0
    • primary or idiopathic (acropachyderma) 757.39
  • osteodermopathic hyperostosis 757.39
  • Proteus (dermal hypoplasia) 757.39
  • Roy (-Jutras) (acropachyderma) 757.39
  • Siemens'
    • keratosis follicularis spinulosa (decalvans) 757.39
  • Touraine-Solente-Golé (acropachyderma) 757.39
  • Uehlinger's (acropachyderma) 757.39
  • Weber-Cockayne (epidermolysis bullosa) 757.39
Tag (hypertrophied skin) (infected) 701.9
  • skin 701.9
    • accessory 757.39
    • congenital 757.39
Touraine-Solente-Golé syndrome (acropachyderma) 757.39
Tumor (M8000/1) - see also Neoplasm, by site, unspecified nature
  • White-Darier 757.39
Tylosis 700
  • palmaris et plantaris 757.39
Uehlinger's syndrome (acropachyderma) 757.39
Urticaria 708.9
  • perstans hemorrhagica 757.39
Weber-Cockayne syndrome (epidermolysis bullosa) 757.39
White's disease (congenital) (keratosis follicularis) 757.39
Xeroderma (congenital) 757.39