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2007 ICD-9-CM Volume 1 Diagnosis Codes Home > Congenital Anomalies 740-759 > Congenital Anomalies Of The Integument 757.* >

2007 ICD-9-CM Diagnosis 757.1

Ichthyosis congenita

 On October 1, 2008 the 2009 ICD-9-CM codes came into effect. Therefore, this code may be out of date.

The 2009 version of ICD-9-CM 757.1 can be accessed here.

  • Designation for several severe forms of ichthyosis, present at birth, that are characterized by hyperkeratotic scaling. Infants may be born encased in a collodion membrane which begins shedding within 24 hours. This is followed in about two weeks by persistent generalized scaling. The forms include bullous (HYPERKERATOSIS, EPIDERMOLYTIC), non-bullous (ICHTHYOSIS, LAMELLAR), wet type, and dry type.
  • 757.1 is a specific code that can be used to specify a diagnosis
  • 757.1 contains 25 index entries
  • View the ICD-9-CM Volume 1 757.* hierarchy

757.1 also known as:

  • Congenital ichthyosis
  • Harlequin fetus
  • Ichthyosiform erythroderma

Index entries containing 757.1:

Alligator skin disease (ichthyosis congenita) 757.1Carini's syndrome (ichthyosis congenita) 757.1
Collodion baby (ichthyosis congenita) 757.1
Disease, diseased - see also Syndrome
  • alligator skin (ichthyosis congenita) 757.1
  • fish skin 757.1
Erythema, erythematous (generalized) 695.9
  • ichthyosiforme congenitum 757.1
Erythroderma (see also Erythema) 695.9
  • ichthyosiform, congenital 757.1
Harlequin (fetus) 757.1Hyperkeratosis (see also Keratosis) 701.1
  • universalis congenita 757.1
Ichthyosis (congenita) 757.1
  • acquired 701.1
  • fetalis gravior 757.1
  • follicularis 757.1
  • hystrix 757.39
  • lamellar 757.1
  • lingual 528.6
  • palmaris and plantaris 757.39
  • simplex 757.1
  • vera 757.1
  • vulgaris 757.1
Keratoma 701.1
  • malignum congenitale 757.1
Netherton's syndrome (ichthyosiform erythroderma) 757.1
Seeligmann's syndrome (ichthyosis congenita) 757.1
Sjögren-Larsson syndrome (ichthyosis congenita) 757.1
Syndrome - see also Disease
  • Alligator baby (ichthyosis congenita) 757.1
  • Carini's (ichthyosis congenita) 757.1
  • Netherton's (ichthyosiform erythroderma) 757.1
  • Seeligmann's (ichthyosis congenita) 757.1
  • Sjögren-Larsson (ichthyosis congenita) 757.1