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2007 ICD-9-CM Volume 1 Diagnosis Codes Home > Diseases Of The Nervous System And Sense Organs 320-389 > Other Disorders Of The Central Nervous System 340-349 > Other Demyelinating Diseases Of Central Nervous System 341.* >

2007 ICD-9-CM Diagnosis 341.1

Schilder's disease

 On October 1, 2008 the 2009 ICD-9-CM codes came into effect. Therefore, this code may be out of date.

The 2009 version of ICD-9-CM 341.1 can be accessed here.

  • A rare central nervous system demyelinating condition affecting children and young adults. Pathologic findings include a large, sharply defined, asymmetric focus of myelin destruction that may involve an entire lobe or cerebral hemisphere. The clinical course tends to be progressive and includes dementia, cortical blindness, cortical deafness, spastic hemiplegia, and pseudobulbar palsy. Concentric sclerosis of Balo is differentiated from diffuse cerebral sclerosis of Schilder by the pathologic finding of alternating bands of destruction and preservation of myelin in concentric rings. Alpers' Syndrome refers to a heterogeneous group of diseases that feature progressive cerebral deterioration and liver disease. (From Adams et al., Principles of Neurology, 6th ed, p914; Dev Neurosci 1991;13(4-5):267-73)
  • 341.1 is a specific code that can be used to specify a diagnosis
  • 341.1 contains 13 index entries
  • View the ICD-9-CM Volume 1 341.* hierarchy

341.1 also known as:

  • Balo's concentric sclerosis
  • Encephalitis periaxialis:
    • concentrica [Balo's]
    • diffusa [Schilder's]

Index entries containing 341.1:

Baló's disease or concentric sclerosis 341.1
Disease, diseased - see also Syndrome
  • Baló's 341.1
  • Flatau-Schilder 341.1
  • Schilder (-Flatau) 341.1
Encephalitis (bacterial) (chronic) (hemorrhagic) (idiopathic) (nonepidemic) (spurious) (subacute) 323.9
  • periaxialis (concentrica) (diffusa) 341.1
Encephalopathy (acute) 348.30
  • subcortical progressive (Schilder) 341.1
Flatau-Schilder disease 341.1
Schilder (-Flatau) disease 341.1
Sclerosis, sclerotic
  • Baló's (concentric) 341.1
  • brain (general) (lobular) 341.9
    • diffuse 341.1
      • familial (chronic) (infantile) 330.0
      • infantile (chronic) (familial) 330.0
      • Pelizaeus-Merzbacher type 330.0
  • concentric, Balo's 341.1
  • diffuse NEC 341.1
  • Schilder's 341.1