Specific code 2014 ICD-9-CM Diagnosis Code 341.1
Schilder's disease
  • Billable Code
  • ICD-9-CM 341.1 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 341.1 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Balo concentric sclerosis (disorder)
  • Balos concentric sclerosis
  • Schilders disease
Clinical Information
  • A rare central nervous system demyelinating condition affecting children and young adults. Pathologic findings include a large, sharply defined, asymmetric focus of myelin destruction that may involve an entire lobe or cerebral hemisphere. The clinical course tends to be progressive and includes dementia, cortical blindness, cortical deafness, spastic hemiplegia, and pseudobulbar palsy. Concentric sclerosis of balo is differentiated from diffuse cerebral sclerosis of schilder by the pathologic finding of alternating bands of destruction and preservation of myelin in concentric rings. Alpers' syndrome refers to a heterogeneous group of diseases that feature progressive cerebral deterioration and liver disease. (from Adams et al., Principles of Neurology, 6th ed, p914; dev neurosci 1991;13(4-5):267-73)
  • A rare congenital demyelinating disorder affecting the central nervous system. It is characterized by a demyelinating destructive lesion affecting an entire brain lobe or hemisphere. Signs and symptoms include dementia, cortical deafness and blindness, pseudobulbar palsy, and hemiplegia.
Applies To
  • Balo's concentric sclerosis
  • Encephalitis periaxialis:
    • concentrica [Balo's]
    • diffusa [Schilder's]
Convert to ICD-10-CM: 341.1 converts approximately to:
  • 2014 ICD-10-CM G37.0 Diffuse sclerosis of central nervous system
    Or:
  • 2014 ICD-10-CM G37.5 Concentric sclerosis [Balo] of central nervous system
ICD-9-CM Volume 2 Index entries containing back-references to 341.1:
  • Baló's disease or concentric sclerosis 341.1
  • Disease, diseased - see also Syndrome
    • Baló's 341.1
    • Flatau-Schilder 341.1
    • Schilder (-Flatau) 341.1
  • Encephalitis (bacterial) (chronic) (hemorrhagic) (idiopathic) (nonepidemic) (spurious) (subacute) 323.9
    • periaxialis (concentrica) (diffusa) 341.1
  • Encephalopathy (acute) 348.30
    • subcortical progressive (Schilder) 341.1
  • Flatau-Schilder disease 341.1
  • Schilder (-Flatau) disease 341.1
  • Sclerosis, sclerotic
    • Baló's (concentric) 341.1
    • concentric, Balo's 341.1
    • diffuse NEC 341.1
    • Schilder's 341.1
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 341.1 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.