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2007 ICD-9-CM Volume 1 Diagnosis Codes Home > Diseases Of The Nervous System And Sense Organs 320-389 > Hereditary And Degenerative Diseases Of The Central Nervous System 330-338 > Spinocerebellar Disease 334.* >

2007 ICD-9-CM Diagnosis 334.2

Primary cerebellar degeneration

This code may be outdated. View the most recent version of ICD-9-CM 334.2

  • A condition marked by progressive CEREBELLAR ATAXIA combined with MYOCLONUS usually presenting in the third decade of life or later. Additional clinical features may include generalized and focal SEIZURES, spasticity, and DYSKINESIAS. Autosomal recessive and autosomal dominant patterns of inheritance have been reported. Pathologically, the dentate nucleus and brachium conjunctivum of the CEREBELLUM are atrophic, with variable involvement of the spinal cord, cerebellar cortex, and basal ganglia. (From Joynt, Clinical Neurology, 1991, Ch37, pp60-1)
  • 334.2 is a specific code that can be used to specify a diagnosis
  • 334.2 contains 20 index entries
  • View the ICD-9-CM Volume 1 334.* hierarchy

334.2 also known as:

  • Cerebellar ataxia:
    • Marie's
    • Sanger-Brown
  • Dyssynergia cerebellaris myoclonica
  • Primary cerebellar degeneration:
    • NOS
    • hereditary
    • sporadic

Index entries containing 334.2:

Ataxia, ataxy, ataxic 781.3
  • cerebellar 334.3
    • hereditary (Marie's) 334.2
  • family, familial 334.2
    • cerebral (Marie's) 334.2
    • spinal (Friedreich's) 334.0
  • hereditary NEC 334.2
  • heredofamilial (Marie's) 334.2
  • Marie's (cerebellar) (heredofamilial) 334.2
  • Sanger-Brown's 334.2
Degeneration, degenerative
  • cerebellar NEC 334.9
    • primary (hereditary) (sporadic) 334.2
  • cortical (cerebellar) (parenchymatous) 334.2
Disease, diseased - see also Syndrome
  • Hunt's
    • dyssynergia cerebellaris myoclonica 334.2
Dyssynergia
  • cerebellaris myoclonica 334.2
Hunt's
  • syndrome (herpetic geniculate ganglionitis) 053.11
    • dyssynergia cerebellaris myoclonica 334.2
Marie's
  • cerebellar ataxia 334.2
Ramsay Hunt syndrome (herpetic geniculate ganglionitis) 053.11
  • meaning dyssynergia cerebellaris myoclonica 334.2
Sanger-Brown's ataxia 334.2
Sclerosis, sclerotic
  • brain (general) (lobular) 341.9
    • hereditary 334.2
  • hereditary
    • cerebellar 334.2
Syndrome - see also Disease
  • Hunt's (herpetic geniculate ganglionitis) 053.11
    • dyssynergia cerebellaris myoclonica 334.2
  • Ramsay Hunt's
    • dyssynergia cerebellaris myoclonica 334.2