2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Diseases Of The Nervous System And Sense Organs 320-389 > Hereditary And Degenerative Diseases Of The Central Nervous System 330-338 > Other Extrapyramidal Disease And Abnormal Movement Disorders 333.* > 2006 ICD-9-CM Diagnosis 333.4 Huntington's chorea View the most recent version of ICD-9-CM 333.4 A familial disorder inherited as an autosomal dominant trait and characterized by the onset of progressive CHOREA and DEMENTIA in the fourth or fifth decade of life. Common initial manifestations include paranoia; poor impulse control; DEPRESSION; HALLUCINATIONS; and DELUSIONS. Eventually intellectual impairment; loss of fine motor control; ATHETOSIS; and diffuse chorea involving axial and limb musculature develops, leading to a vegetative state within 10-15 years of disease onset. The juvenile variant has a more fulminant course including SEIZURES; ATAXIA; dementia; and chorea. KEGG_ID: hsa05040 333.4 is a specific code that can be used to specify a diagnosis 333.4 contains 9 index entries View the ICD-9-CM Volume 1 333.* hierarchy  Index entries containing 333.4: Chorea (gravis) (minor) (spasmodic) 333.5 chronic 333.4 hereditary 333.4 Huntington's 333.4 progressive 333.4 chronic 333.4 hereditary 333.4 Disease, diseased - see also Syndrome Huntington's 333.4 Huntington's chorea 333.4 disease 333.4